title: [Our experience in portal cavernomatosis in childhood: cross-sectional study and analysis of results].
abstract: A retrospective and transversal study of our patients with portal cavernomatosis is developed, with the aim of comparing the evolution and the present status of the patients that have undergone different therapeutical approaches. Between 1975 and 1995, 15 patients with portal cavernomatosis have been treated. Personal history, signs and symptoms at the moment of diagnosis, and treatment were analyzed. Now, the controls have been made by physical examination and ECO-Doppler of the espleno-portal system. In 6 cases the absence of bleeding made surgery unnecessary. In the 9 patients with digestive haemorrhage, it could be controlled pharmacologically, with a later surgical approach. Now, all non-operated and 6 operated patients show splenomegaly, without bleeding. The ECO-Doppler shows colateral flow, the splenomegaly in the non-operated and the surgical shunts and the hepatofugal circulation in the operated patients. Looking at our results, we believe that prophylactic surgery is not indicated. In those cases of digestive bleeding, surgery after the complete resolution of the acute disease shows good results at a short and long term.
authors.affiliation: Departamento de Cirugía Pediátrica, Hospital Infantil La Fe Valencia.
authors.forename: A
authors.initials: A
authors.lastname: López Saiz
authors.forename: J J
authors.initials: JJ
authors.lastname: Vila Carbó
authors.forename: M S
authors.initials: MS
authors.lastname: Fernández
authors.forename: D
authors.initials: D
authors.lastname: Muro
authors.forename: V
authors.initials: V
authors.lastname: Ibáñez
authors.forename: C
authors.initials: C
authors.lastname: Gutiérrez
authors.forename: A
authors.initials: A
authors.lastname: Roca
authors.forename: C
authors.initials: C
authors.lastname: García-Sala
mesh_terms: D002675:Child, Preschool; D003430:Cross-Sectional Studies; D005260:Female; D006392:Hemangioma, Cavernous / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011169:Portal Vein / Q000601:surgery*; D012189:Retrospective Studies; D012720:Severity of Illness Index; D019043:Vascular Neoplasms / Q000601:surgery*