Pregnancy with aortic dissection in Ehler-Danlos syndrome. Staged replacement of the total aorta (10-year follow-up).
Pregnancy complicated by aortic dissection in patients with hereditary disorder of connective tissue presents interesting considerations including management of caesarean section with the unexpected need for cardiac surgery in emergency. Generalizations can be made on management principles with long-term follow-up requiring an aggressive individualized approach by a multidisciplinary team. A 33-year-old parturient presenting an aortic dissection at 37 weeks gestation required prompt diagnosis of Ehlers-Danlos syndrome in combination with correct surgical therapy resulted in the survival of both the mother and infant. During the 10-year follow-up, multiple complex dissection required transverse aortic arch and thoracoabdominal aortic replacement.
Babatasi
G
G
Department of Thoracic and Cardiovascular Surgery, University Hospital CHU Caen, Côte de Nacre, France.
Massetti
M
M
Bhoyroo
S
S
Khayat
A
A
D000328:Adult; D000784:Aortic Dissection / Q000209:etiology / Q000601:surgery*; D001011:Aorta / Q000601:surgery; D017544:Aortic Aneurysm, Abdominal / Q000209:etiology / Q000601:surgery; D017545:Aortic Aneurysm, Thoracic / Q000209:etiology / Q000601:surgery*; D019917:Blood Vessel Prosthesis Implantation; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000175:diagnosis; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000209:etiology / Q000601:surgery*; D011256:Pregnancy Outcome; D013997:Time Factors