Ritual relieved axial dystonia triggered by gaze-evoked amaurosis.
A woman with chronic posttraumatic axial lateropulsion cervical dystonia ("belly dancer's head") found relief of her spontaneous dystonic spasms by the sequential performance of an elaborate motor ritual. During an episode of left optic papillitis caused by central retinal vein occlusion, gaze-evoked amaurosis of the left eye developed, preceded by achromatopsia, during left lateral gaze. Gaze-evoked amaurosis triggered axial dystonia, which was followed by her unique, stereotyped, dystonia-relieving ritual that simulated a slow dance. Visual symptoms improved progressively in 1 year. Eventually, she was unable to trigger her dystonia by eye movements. Spontaneous dystonia remained otherwise unchanged from before the episode of papillitis and was still relieved by her unique ritual.
Jacome
D E
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Department of Medicine, Franklin Medical Center, Greenfield, Massachusetts, USA.
D000368:Aged; D001766:Blindness / Q000209:etiology*; D004421:Dystonia / Q000209:etiology / Q000503:physiopathology* / Q000523:psychology; D005260:Female; D005403:Fixation, Ocular; D016489:Head Injuries, Closed / Q000150:complications; D006801:Humans; D009043:Motor Activity; D009334:Neck Muscles / Q000503:physiopathology*