Congenital cervicovaginal aplasia with septate uterus and functioning endometrium.
A 14-year-old adolescent girl presented with primary amenorrhea and uncontrolled pelvic pain. Evaluation using pelvic sonogram, magnetic resonance imaging, and laparoscopy confirmed the diagnosis of cervicovaginal aplasia with functioning endometrium and a vaginal fistulous tract. At age 19 years, hysterectomy and vaginoplasty allowed the patient to be free of pain and to have normal sexual function.
Badawy
S Z
SZ
Department of Obstetrics and Gynecology, SUNY Health Science Center, Syracuse, USA.
Prasad
M
M
Powers
C
C
Wojtowycz
A R
AR
D000293:Adolescent; D000568:Amenorrhea / Q000209:etiology; D002584:Cervix Uteri / Q000002:abnormalities* / Q000473:pathology; D004717:Endometrium / Q000473:pathology / Q000502:physiology*; D005260:Female; D006801:Humans; D007044:Hysterectomy; D017699:Pelvic Pain / Q000209:etiology; D014599:Uterus / Q000002:abnormalities* / Q000473:pathology; D014621:Vagina / Q000002:abnormalities* / Q000473:pathology / Q000601:surgery