[Osteomyelitis of the facial skull in Albers-Schönberg osteopetrosis].
Albers-Schönberg osteopetrosis, a rare heritable bone disease with autosomal dominant or recessive transmission, is generally characterised by diffuse sclerosis of the whole skeleton accompanied by pathological bone fragility and delayed physical development, profound intractable myelophthisic anaemia, neurological deficits, and osteomyelitis, especially of the jaws and the skull. The precise aetiology of the osteopetrosis is not clear. Therefore therapy is restricted to alleviation of symptoms. In this study the case of a patient suffering from the benign form of osteopetrosis is presented. Osteomyelitis of the skull was treated successfully 2 years after the removal of lower and upper jaw teeth by a combined multistage surgical and antibiotic approach.
Ozmen
Y
Y
Klinik und Poliklinik für Zahn-, Mund- und Kieferheilkunde, Universität Köln.
Klesper
B
B
Lenzen
J
J
D000038:Abscess / Q000175:diagnosis / Q000235:genetics / Q000601:surgery; D000328:Adult; D002869:Chromosome Aberrations / Q000235:genetics; D025063:Chromosome Disorders; D005147:Facial Bones / Q000473:pathology / Q000601:surgery; D006801:Humans; D008297:Male; D010019:Osteomyelitis / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D010022:Osteopetrosis / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D012086:Reoperation; D013524:Surgical Flaps; D014081:Tooth Extraction