Anomalous origin of all coronary arteries from the pulmonary trunk.
The origin of both coronary arteries from the pulmonary artery is a rare cardiac malformation. We report a baby who presented with an echocardiographically diagnosed perimembranous ventricular septal defect and normal left ventricular (LV) function. Later on the boy developed failure to thrive and increasing tachypnea. At the age of 5 weeks the ECG showed that LV strain and echocardiographic LV function had worsened (FS 18%). Echocardiography and heart catheterization showed that all coronary arteries originated from the pulmonary trunk. Intraoperative inspection revealed a single ostium for the right and left coronary artery in the nonfacing sinus of the pulmonary trunk. A tube was constructed connecting the coronary artery to the ascending aorta. Coronary perfusion was sufficient and the sinus rhythm was restored. However, in the early postoperative period there was a sudden deterioration of cardiac output followed by cardiac arrest. Reanimation was not successful.
Heusch
A
A
Department of Pediatric Cardiology, Heinrich-Heine-Universität, Düsseldorf, Germany.
Quagebeur
J
J
Paulus
A
A
Krogmann
O N
ON
Bourgeois
M
M
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000503:physiopathology; D001783:Blood Flow Velocity; D006328:Cardiac Catheterization; D017023:Coronary Angiography; D003330:Coronary Vessel Anomalies / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D018618:Echocardiography, Doppler, Color; D017809:Fatal Outcome; D006323:Heart Arrest / Q000209:etiology; D006333:Heart Failure; D006345:Heart Septal Defects, Ventricular / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D013318:Stroke Volume