title: Idiopathic retroperitoneal fibrosis presented as an abdominal mass and nephrotic syndrome.
abstract: We present a 30-year-old male patient who was initially diagnosed as minimal change nephrotic syndrome, 5 years later, the patient developed a localized form of idiopathic retroperitoneal fibrosis (IRF). An elevated ESR and concomitant nephrotic syndrome in the patient suggested the immunologic nature of IRF, IRF has been reported in association with collagen diseases and rarely with proliferative and nonproliferative glomerulopathies. To our knowledge, the association between minimal change lesion (MC) and IRF has not been reported. Furthermore, the fact that IRF presented itself as an abdominal mass and lacked systemic symptoms was also unusual.
authors.affiliation: Department of Internal Medicine and Pathology, Seoul National University-Hospital, Korea.
authors.forename: K H
authors.initials: KH
authors.lastname: Oh
authors.forename: C
authors.initials: C
authors.lastname: Ahn
authors.forename: J H
authors.initials: JH
authors.lastname: Park
authors.forename: J E
authors.initials: JE
authors.lastname: Oh
authors.forename: H J
authors.initials: HJ
authors.lastname: Chin
authors.forename: J S
authors.initials: JS
authors.lastname: Han
authors.forename: S
authors.initials: S
authors.lastname: Kim
authors.forename: J G
authors.initials: JG
authors.lastname: Chi
authors.forename: M H
authors.initials: MH
authors.lastname: Park
authors.forename: J S
authors.initials: JS
authors.lastname: Lee
mesh_terms: D000328:Adult; D006801:Humans; D008297:Male; D009404:Nephrotic Syndrome / Q000150:complications*; D012185:Retroperitoneal Fibrosis / Q000175:diagnosis* / Q000209:etiology