title: Dermatofibrosarcoma protuberans in childhood.
abstract: Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumor with a possibly misleading presentation. It is rare in childhood. We report an 18-month-old child with an acquired atrophic plaque of the left ankle. Based on clinical findings, initial proposed diagnoses included localized scleroderma and localized lipoatrophy. At the age of 5 years the plaque had increased in size and become a purplish color. Several firm nodules were seen at its periphery. A diagnosis of DFSP was proposed and confirmed histologically. A large surgical resection was performed. This case illustrates that DFSP may occur in childhood, during which initial diagnosis is generally more difficult than in adulthood.
authors.affiliation: Department of Dermatology, Centre Hospitalier Régional et Universitaire Dupuytren, Limoges,France.
authors.forename: M L
authors.initials: ML
authors.lastname: Bouyssou-Gauthier
authors.forename: F
authors.initials: F
authors.lastname: Labrousse
authors.forename: B
authors.initials: B
authors.lastname: Longis
authors.forename: C
authors.initials: C
authors.lastname: Bedane
authors.forename: P
authors.initials: P
authors.lastname: Bernard
authors.forename: J M
authors.initials: JM
authors.lastname: Bonnetblanc
mesh_terms: D000367:Age Factors; D000842:Ankle; D001706:Biopsy; D018223:Dermatofibrosarcoma / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000601:surgery