Dermatofibrosarcoma protuberans in childhood.
Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumor with a possibly misleading presentation. It is rare in childhood. We report an 18-month-old child with an acquired atrophic plaque of the left ankle. Based on clinical findings, initial proposed diagnoses included localized scleroderma and localized lipoatrophy. At the age of 5 years the plaque had increased in size and become a purplish color. Several firm nodules were seen at its periphery. A diagnosis of DFSP was proposed and confirmed histologically. A large surgical resection was performed. This case illustrates that DFSP may occur in childhood, during which initial diagnosis is generally more difficult than in adulthood.
Bouyssou-Gauthier
M L
ML
Department of Dermatology, Centre Hospitalier Régional et Universitaire Dupuytren, Limoges,France.
Labrousse
F
F
Longis
B
B
Bedane
C
C
Bernard
P
P
Bonnetblanc
J M
JM
D000367:Age Factors; D000842:Ankle; D001706:Biopsy; D018223:Dermatofibrosarcoma / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000601:surgery