Esophageal variceal bleeding caused by hypoplasia of the portal vein in a patient with the Klippel-Trenaunay syndrome.
The case of a patient affected by Klippel-Trenaunay syndrome presenting with esophageal variceal bleeding caused by hypoplasia of the vena porta is reported. Hemostasis was achieved by performing a proximal spleno-renal shunt. We discuss the likely association of this mesodermal development abnormality and vascular disorders of the portal vein.
Bataller
R
R
Liver Unit, Hospital Clínic i Provincial, University of Barcelona, Spain.
Sans
M
M
Escorsell
A
A
Elizalde
J I
JI
Bosch
J
J
Rodés
J
J
D000328:Adult; D004932:Esophageal and Gastric Varices / Q000209:etiology*; D006471:Gastrointestinal Hemorrhage / Q000209:etiology* / Q000601:surgery; D006488:Hemostasis, Surgical; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications* / Q000473:pathology; D008297:Male; D011169:Portal Vein / Q000473:pathology*; D013164:Splenorenal Shunt, Surgical