[Neurofibromatosis type 1 associated arteriopathy. Case report and literature review].
Reported is the case of a 36-year-old man with neurofibromatosis type 1 with lethal haemorrhage from rupture of the left common iliac artery. Histologically and immunohistochemically, no hints on angiodysplasia as a possible cause of bleeding were detected. Considering the literature and the histological findings in the area of rupture, a local weakness of the vascular wall caused by the neighbouring neurofibromatous proliferates was most probably the reason for bleeding.
Kunz
J
J
Institut für Pathologie, Klinikum "Ernst von Bergmann, Potsdam.
Maxeiner
H
H
D000328:Adult; D017809:Fatal Outcome; D006470:Hemorrhage / Q000150:complications / Q000473:pathology*; D006801:Humans; D007083:Iliac Artery / Q000473:pathology*; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications / Q000473:pathology*; D012422:Rupture, Spontaneous
Neurofibromatose-Typ 1-assoziierte Arteriopathie. Fallbericht und Literaturübersicht.