Pregnancy and delivery in Ehlers-Danlos syndrome type V.
Ehlers-Danlos syndrome (EDS) is a hereditary dysplasia of connective tissue with an abnormal collagen synthesis. It is characterized by hyperelasticity and fragility of the skin, joint hyperlaxity and fragility of the blood vessels. We describe the problems reported during pregnancy and delivery in women with EDS. Our patient had a type V syndrome. Accurate monitoring during the course of pregnancy is necessary. We believe cesarean section more appropriate than vaginal delivery in order to avoid the risks related to the rupture of the pelvic and perineal vessels which may be difficult to suture.
Bruno
P A
PA
Department of Obstetrics and Gynecology, University of Naples Federico II, Italy.
Napolitano
V
V
Votino
F
F
Di Mauro
P
P
Nappi
C
C
D000328:Adult; D002585:Cesarean Section; D036861:Delivery, Obstetric / Q000379:methods*; D004535:Ehlers-Danlos Syndrome / Q000503:physiopathology; D005260:Female; D006470:Hemorrhage / Q000517:prevention & control; D006801:Humans; D008297:Male; D007744:Obstetric Labor Complications / Q000517:prevention & control*; D011247:Pregnancy; D011248:Pregnancy Complications / Q000503:physiopathology; D011256:Pregnancy Outcome; D018566:Pregnancy, High-Risk; D012421:Rupture / Q000517:prevention & control