[Esophageal stenosis in epidermolysis bullosa hereditaria].
Benign esophageal strictures in the upper esophagus may be caused by systemic diseases. A rare reason for esophageal strictures are the mechanobullous disorders marked by blister formation following relatively minor trauma, e.g. epidermolysis bullosa. In this report we present a 63-year-old patient who had suffered from epidermolysis bullosa simplex since birth. The epicutaneous symptoms were no longer present but an esophageal stricture had developed. The stricture was treated by X-ray-controlled balloon dilation twice, with a functionally good result. We suggest managing a recurrence recidiv of stricture with balloon dilation to minimize trauma and prevent further lesions.
Kling
H
H
HNO-Klinik, Zentralkrankenhaus St. Jürgenstrasse, Bremen.
D002404:Catheterization; D016110:Epidermolysis Bullosa Simplex / Q000150:complications*; D004940:Esophageal Stenosis / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D004945:Esophagoscopy; D006801:Humans; D008297:Male; D008875:Middle Aged; D012008:Recurrence
Osophagusstenose bei Epidermolysis bullosa hereditaria.