Retroperitoneal lymphangioleiomyomatosis: CT appearance.
Lymphangioleiomyomatosis is a rare disease involving the lung, lymphatic trunk and lymph nodes. Sometimes it appears in the retroperitoneum with or without subsequent development in the lungs. We present a 52-year-old woman with retroperitoneal location of the disease. We discuss the abdominal CT appearance, the cytologic and immunophenotypic features and a preoperative differential diagnosis is attempted.
Kehagias
D
D
Department of Radiology, University of Athens, Areteion Hospital, 76 Vas. Sophias Av., Athens 115 28, Greece.
Pafiti
A
A
Vaos
N
N
Samanidis
L
L
D000199:Actins / Q000032:analysis; D014408:Biomarkers, Tumor / Q000032:analysis; D003937:Diagnosis, Differential; D005169:Factor VIII / Q000032:analysis; D005260:Female; D006801:Humans; D016130:Immunophenotyping; D007889:Leiomyoma / Q000473:pathology; D018192:Lymphangioleiomyomatosis / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000473:pathology; D012186:Retroperitoneal Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed; D014594:Uterine Neoplasms / Q000473:pathology; D014746:Vimentin / Q000032:analysis
D000199:Actins; D014408:Biomarkers, Tumor; D014746:Vimentin; D005169:Factor VIII