title: Recent developments in the management of Peutz-Jeghers syndrome in childhood.
abstract: A combined surgical and endoscopic approach for managing extensive polyposis in a child with Peutz-Jeghers syndrome (PJS) is presented. Application of this technique offers the following advantages over conventional surgical practice -- 1) an accurate assessment can be made of the extent of intestinal polyposis; 2) small polyps can be easily removed endoscopically; 3) endoscopy can direct the operating surgeon to selected enterotomy sites for open excision of larger polyps and 4) multiple laparotomy, extensive intestinal resection(s) and the potential threat of short-gut syndrome in PJS patients may be avoided.
authors.affiliation: Department of Paediatric Surgery, Royal Liverpool Children's Hospital (Alder Hey), UK.
authors.forename: A S
authors.initials: AS
authors.lastname: Keshtgar
authors.forename: P D
authors.initials: PD
authors.lastname: Losty
authors.forename: D A
authors.initials: DA
authors.lastname: Lloyd
authors.forename: A I
authors.initials: AI
authors.lastname: Morris
authors.forename: A
authors.initials: A
authors.lastname: Pierro
mesh_terms: D000293:Adolescent; D004564:Electrocoagulation; D004724:Endoscopy / Q000379:methods*; D005260:Female; D006801:Humans; D007417:Intestinal Polyps / Q000601:surgery*; D010580:Peutz-Jeghers Syndrome / Q000601:surgery*