Nevoid basal cell carcinoma syndrome in a black child.
Nevoid basal cell carcinoma syndrome (NBCCS) is rare in black persons. We describe an 11-year-old black boy with NBCCS who presented with exotropia and a painful, expanding, cystic mass in the left posterior alveolar ridge. Further examination revealed odontogenic keratocysts with palmar and plantar pitting. Less than 5% of reported patients with NBCCS are black. To our knowledge, this is the first report of a black patient with NBCCS presenting with exotropia and an impacted molar displaced into the orbit by an odontogenic keratocyst.
Hall
J
J
Baylor College of Medicine, Texas, USA.
Johnston
K A
KA
McPhillips
J P
JP
Barnes
S D
SD
Elston
D M
DM
D001478:Basal Cell Nevus Syndrome / Q000175:diagnosis*; D044383:Black People; D002648:Child; D003937:Diagnosis, Differential; D005099:Exotropia / Q000175:diagnosis; D006801:Humans; D007571:Jaw Diseases / Q000150:complications / Q000175:diagnosis; D008297:Male; D008437:Maxilla; D008963:Molar; D009807:Odontogenic Cysts / Q000150:complications / Q000175:diagnosis; D009915:Orbit; D014095:Tooth, Impacted / Q000150:complications / Q000175:diagnosis