title: Oral health implications in children with inborn errors of intermediary metabolism: a review.
abstract: Children with inborn errors of metabolism form an important group of children at risk of oral pathology. Their management includes dietary therapies which aim to promote normal growth and development but which are often highly cariogenic. It is important for paediatricians, dietitians and paediatric dentists to liaise closely in the management of these children. This paper reviews these disorders and the limited literature that exists on the oral health implications of those conditions that rely on dietary manipulation for their management, and presents suggestions for their dental care.
authors.affiliation: Victorian Clinical Genetics Service, Murdoch Institute, Royal Children's Hospital, Parkville, Melbourne, Victoria, Australia.
authors.forename: M A
authors.initials: MA
authors.lastname: Cleary
authors.forename: D E
authors.initials: DE
authors.lastname: Francis
authors.forename: N M
authors.initials: NM
authors.lastname: Kilpatrick
mesh_terms: D002648:Child; D002675:Child, Preschool; D003731:Dental Caries / Q000209:etiology / Q000517:prevention & control; D006801:Humans; D007223:Infant; D008661:Metabolism, Inborn Errors / Q000145:classification / Q000150:complications*; D009059:Mouth Diseases / Q000209:etiology* / Q000517:prevention & control; D009909:Oral Health; D014076:Tooth Diseases / Q000209:etiology* / Q000517:prevention & control