Ocular staphyloma associated with facial clefting.
A staphyloma is an uncommon ocular lesion consisting of an attenuation in the sclera, which, along with the underlying uveal tissue, bulges to form a raised pigmented area on the eye. The scleral defect predisposes the globe to rupture under conditions of increased intraocular pressure, which might occur while retracting the eye during cranio-orbital surgery. We report a case of a staphyloma in a child with bilateral facial clefts. Before hypertelorism correction, she underwent scleral repair with a cadaveric graft. Her orbital repositioning was performed without incident 10 months later. The significance of a possible association between facial clefting and staphyloma is discussed.
Hardy
S P
SP
Division of Plastic Surgery, University of Wisconsin Medical School, Madison 53706, USA.
Lundergan
M
M
Morales
L
L
D002102:Cadaver; D002675:Child, Preschool; D019465:Craniofacial Abnormalities / Q000150:complications*; D005260:Female; D006801:Humans; D006972:Hypertelorism / Q000150:complications; D009915:Orbit / Q000601:surgery; D012086:Reoperation; D012590:Sclera / Q000637:transplantation; D015422:Scleral Diseases / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery; D014603:Uveal Diseases / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery