Recent developments in the management of Peutz-Jeghers syndrome in childhood.
A combined surgical and endoscopic approach for managing extensive polyposis in a child with Peutz-Jeghers syndrome (PJS) is presented. Application of this technique offers the following advantages over conventional surgical practice -- 1) an accurate assessment can be made of the extent of intestinal polyposis; 2) small polyps can be easily removed endoscopically; 3) endoscopy can direct the operating surgeon to selected enterotomy sites for open excision of larger polyps and 4) multiple laparotomy, extensive intestinal resection(s) and the potential threat of short-gut syndrome in PJS patients may be avoided.
Keshtgar
A S
AS
Department of Paediatric Surgery, Royal Liverpool Children's Hospital (Alder Hey), UK.
Losty
P D
PD
Lloyd
D A
DA
Morris
A I
AI
Pierro
A
A
D000293:Adolescent; D004564:Electrocoagulation; D004724:Endoscopy / Q000379:methods*; D005260:Female; D006801:Humans; D007417:Intestinal Polyps / Q000601:surgery*; D010580:Peutz-Jeghers Syndrome / Q000601:surgery*