A case of rapidly fatal systemic capillary leak syndrome in a kidney transplant recipient.
Idiopathic Systemic Capillary Leak Syndrome (SCLS) is a rare entity characterised by idiopathic increasing of capillary permeability associated with recurrent attacks of hypovolaemic shock. We report the case of a 39-year-old man with a SCLS fourteen years after a cadaveric renal transplantation. The clinical evolution was rapidly fatal despite treatment with corticoids, aminophylline and terbutaline which are the most efficient drugs known to prevent attacks.
Crenier
L
L
Service de médecine interne, Université Libre de Bruxelles-Hôpital Erasme, Belgium.
Piagnerelli
M
M
Doutrelepont
J M
JM
De Pauw
L
L
Kinnaert
P
P
Vereerstraeten
P
P
Abramowicz
D
D
D000328:Adult; D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D001993:Bronchodilator Agents / Q000627:therapeutic use; D019559:Capillary Leak Syndrome / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D004359:Drug Therapy, Combination; D017809:Fatal Outcome; D006400:Hematocrit; D006801:Humans; D016030:Kidney Transplantation / Q000009:adverse effects*; D008297:Male; D011239:Prednisolone / Q000627:therapeutic use; D012769:Shock / Q000150:complications; D013726:Terbutaline / Q000627:therapeutic use; D013806:Theophylline / Q000627:therapeutic use; D013997:Time Factors; D014665:Vasodilator Agents / Q000627:therapeutic use
D000893:Anti-Inflammatory Agents; D001993:Bronchodilator Agents; D014665:Vasodilator Agents; D011239:Prednisolone; D013806:Theophylline; D013726:Terbutaline