Large airway obstruction by a chronic dissecting aortic aneurysm in the Marfan syndrome.
We describe a patient with the Marfan syndrome who presented with an acute aortic dissection. She underwent composite graft replacement of the aortic root. She returned two years later with dyspnoea and stridor due to tracheal compression by a large chronic dissection of the thoracic aorta. Marfan patients are at risk of chronic dissection involving the remaining distal aorta and require regular noninvasive assessment following surgery.
Hargreaves
M R
MR
Cardiac Department, John Radeliffe Hospital, Headington, Oxford, UK.
Gilbert
T J
TJ
Pillai
R
R
Hart
G
G
D000328:Adult; D000402:Airway Obstruction / Q000209:etiology*; D000784:Aortic Dissection / Q000150:complications*; D017545:Aortic Aneurysm, Thoracic / Q000150:complications* / Q000601:surgery; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008382:Marfan Syndrome / Q000150:complications*; D012008:Recurrence