[State of bilateral opercular disorder and pseudobulbar paralysis of late onset in unilateral perisylvian dysplasia].
We come up the case of a six and a half year old girl suffering from right unilateral perisylvian cortical dysplasia who present left spastic hemiparesia, mirror movements and language disorder. She made her epileptic debut at the age of four and a half with myoclonic absences which responded to valproate treatment. At the age of five she began with biopercular status epilepticus shown as pseudobulbar palsy as diffusion of discharges from the dysplasia localization to the contralateral one. These episodes look places with variable duration from one hour to one month and finished after medical treatment or spontaneously. At the present a pseudobulbar palsy persistence and a bilateralization in the symptoms is observed.
Vaquerizo
J
J
Departamento y Cátedra de Pediatría, Hospital Materno-Infantil Universitario Infanta Cristina, UEX, Badajoz, España.
Díaz-García
C
C
D000927:Anticonvulsants / Q000627:therapeutic use; D002540:Cerebral Cortex / Q000002:abnormalities*; D002648:Child; D004569:Electroencephalography; D005260:Female; D007839:Functional Laterality; D006429:Hemiplegia / Q000209:etiology; D006801:Humans; D007806:Language Disorders / Q000209:etiology; D008279:Magnetic Resonance Imaging; D010243:Paralysis / Q000175:diagnosis / Q000209:etiology; D010507:Periodicity; D013226:Status Epilepticus / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D013577:Syndrome; D013997:Time Factors
D000927:Anticonvulsants
Estado de mal biopercular y parálisis pseudobulbar de debut tardío en la displasia perisilviana unilateral.