Rhombencephalosynapsis: cerebellar embryogenesis.
We describe two infants in whom rhombencephalosynapsis was diagnosed with MR imaging in vivo. In contrast to Dandy-Walker malformation, the vermian maldevelopment in this anomaly is characterized by an absence of the anterior vermis and a deficiency of the posterior vermis. The cerebellar hemispheres are fused. In an attempt to identify the pathogenesis of these anatomic manifestations, we question the traditional concept of the embryologic development of the cerebellar primordium.
Utsunomiya
H
H
Department of Diagnostic Radiology, Fukuoka University Hospital, Japan.
Takano
K
K
Ogasawara
T
T
Hashimoto
T
T
Fukushima
T
T
Okazaki
M
M
D001921:Brain / Q000473:pathology; D002531:Cerebellum / Q000002:abnormalities* / Q000196:embryology* / Q000473:pathology; D002675:Child, Preschool; D005314:Embryonic and Fetal Development / Q000502:physiology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male