Peters' anomaly associated with protruding corneal pseudo staphyloma.
OBJECTIVE
To describe a new manifestation of Peters' anomaly.


METHODS
We managed four infants with an unusual form of Peters' anomaly. One eye of each patient had a thickened and scarred cornea, mimicking a corneal staphyloma, protruding anteriorly from the corneal plane. The other eye of each patient ranged from normal to having severe ocular anomalies. A corneal transplant was performed in each case.


RESULTS
Follow-up ranged from 1 to 3 years. Three eyes maintained graft clarity for at least 1 year. Each of these eyes developed vision. Two of these eyes developed glaucoma. The one eye with graft failure developed an inoperable retinal detachment. The histopathology of each corneal button showed changes consistent with Peters' anomaly.


CONCLUSIONS
These corneas demonstrated characteristics of both Peters' anomaly and congenital anterior staphyloma. Despite their severe anomalies, surgery successfully restored a more normal cosmetic appearance in all four eyes and vision in three eyes.
Zaidman
G W
GW
Westchester Medical Center, Our Lady of Mercy Hospital, New York Medical College, Department of Ophthalmology, Valhalla 10595, USA.
Juechter
K
K
D003315:Cornea / Q000002:abnormalities* / Q000473:pathology / Q000601:surgery; D003316:Corneal Diseases / Q000151:congenital / Q000473:pathology / Q000601:surgery; D003318:Corneal Opacity / Q000151:congenital* / Q000473:pathology / Q000601:surgery; D016039:Corneal Transplantation; D015785:Eye Diseases, Hereditary / Q000209:etiology* / Q000473:pathology / Q000601:surgery; D005260:Female; D005901:Glaucoma / Q000209:etiology; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D014785:Vision, Ocular