title: Atrioventricular septal defect with cor triatriatum: case report and review of the literature.
abstract: Atrioventricular septal defect with cor triatriatum is a rare combination, with only nine cases reported so far. Cor triatriatum, a potentially correctable cause of pulmonary arterial hypertension in atrioventricular septal defect patients, was missed in a few earlier case reports, leading to death and subsequent diagnosis at autopsy. We report the case of 3-year-old female child with this combination (partial atrioventricular septal defect with cor triatriatum) wherein the final diagnosis was made at cardiac catheterization. Successful surgical correction was performed.
authors.affiliation: Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: A K
authors.initials: AK
authors.lastname: Goel
authors.forename: A
authors.initials: A
authors.lastname: Saxena
authors.forename: S S
authors.initials: SS
authors.lastname: Kothari
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000601:surgery; D006328:Cardiac Catheterization; D002675:Child, Preschool; D003310:Cor Triatriatum / Q000175:diagnosis* / Q000601:surgery; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006343:Heart Septal Defects / Q000175:diagnosis* / Q000601:surgery; D006801:Humans