Anaesthetic management of children with type II and III Gaucher disease.
The anaesthetic management of two children with Gaucher disease is described. The cases were a girl aged 12 and a boy aged 4 who had undergone 13 and 3 anaesthetic interventions respectively for endoscopic, orthopaedic, general, otolaryngologic and dental surgical procedures over a total period of 11 years. Anaesthetic management of these patients can be achieved with various agents and techniques, but care is needed to identify preoperative end-organ dysfunction and prevent postoperative respiratory insufficiency. In particular, regional anaesthesia, when suitable, has certain advantages that have made it a worthwhile alternative to general anaesthesia.
Dell'Oste
C
C
Anesthesia and Resuscitation Service Burlo Garofolo Pediatric Institute, Trieste.
Vincenti
F
F
D000293:Adolescent; D000758:Anesthesia; D002648:Child; D002675:Child, Preschool; D005260:Female; D005776:Gaucher Disease / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011300:Preoperative Care