Diagnosis and current management of penile agenesis.
Penile agenesis is a rare congenital anomaly in which early gender reassignment is recommended. In the past, multiple operations were carried out to form feminized external genitalia. The authors performed a definite genital reconstruction in a neonate using the posterior sagittal approach. Preoperatively, a magnetic resonance imaging (MRI) scan demonstrated erectile tissue, which was preserved and incorporated into the genital plasty. The operation included bilateral orchiectomy, urethral reconstruction, sigmoid vaginal replacement, and formation of the labia. The authors discuss the controversy around gender assessment. They emphasize the urethral hypotrophy to be a main challenge in this anomaly and conclude that immediate complete reconstruction is possible and should be performed in patients with this delicate condition.
Glüer
S
S
Department of Pediatric Surgery, Medizinische Hochschule Hannover, Germany.
Fuchs
J
J
Mildenberger
H
H
D000013:Congenital Abnormalities / Q000601:surgery; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D009919:Orchiectomy; D010413:Penis / Q000002:abnormalities*; D019651:Plastic Surgery Procedures; D014521:Urethra / Q000601:surgery; D014621:Vagina / Q000601:surgery