[Congenital dyserythropoietic anemia morphologically type I with a positive HEMPAS phenomenon].
A patient with clinical and morphological anaemia of type I is described. Surprisingly, the Ham's test yield positive with 2 of 20 compatible serum. Only other such case is recorded in the literature. We revised the literature and comment the unclassified cases reported.
Bergua Burgués
J M
JM
Servicio de Hematología y Hemoterapia, Hospital San Pedro de Alcántara, Cácres.
Navarro
D
D
González
J
J
Doblaré
E
E
D000742:Anemia, Dyserythropoietic, Congenital / Q000097:blood* / Q000145:classification / Q000473:pathology; D001788:Blood Grouping and Crossmatching; D001853:Bone Marrow / Q000473:pathology; D002467:Cell Nucleus / Q000648:ultrastructure; D002648:Child; D004900:Erythroblasts / Q000648:ultrastructure; D005260:Female; D006801:Humans; D015388:Organelles / Q000648:ultrastructure
Anemia diseritropoyética congénita morfológicamente de tipo I con fenómeno de HEMPAS positivo.