Congenital short bowel syndrome associated with appendiceal agenesis and functional intestinal obstruction.
Congenital short bowel with functional intestinal obstruction and absence of appendix vermiformis is a very rare condition with poor prognosis. Seventeen cases of congenital short bowel have been reported previously in the literature. The etiology is unknown. In this report, a case of congenital short bowel, combined with functional intestinal obstruction, mal-rotation, and absence of the appendix vermiformis, is presented and the pathogenesis discussed.
Sarimurat
N
N
Department of Paediatric Surgery, Cerrahpasa Medical Faculty, University of Istanbul, Turkey.
Celayir
S
S
Elicevik
M
M
Dervisoglu
S
S
Yeker
D
D
D001065:Appendix / Q000002:abnormalities*; D002432:Cecum / Q000002:abnormalities; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007415:Intestinal Obstruction / Q000150:complications*; D012778:Short Bowel Syndrome / Q000150:complications / Q000151:congenital*