title: [Cystic fibrosis in adolescent patients].
abstract: Summary--An autopsy observation of mucoviscydosis in a female who died at the age of 17 with a prevalent affection of the bronchopulmonary system is reported. Pronounced cystic fibrosis with atrophy and lipomatosis of the pancreas was found. The cause of death was respiratory failure in spite of intensive antibacterial therapy. Bullous emphysema with frequent pneumothorax in adults with this disease considerably worsens the prognosis and requires urgent therapy which in this case was not conducted because of late hospitalization.
authors.affiliation: Research Institute of Pulmonology, Moscow.
authors.forename: A L
authors.initials: AL
authors.lastname: Cherniaev
authors.forename: M V
authors.initials: MV
authors.lastname: Samsonova
authors.forename: L A
authors.initials: LA
authors.lastname: Kronina
mesh_terms: D000293:Adolescent; D003550:Cystic Fibrosis / Q000473:pathology*; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008168:Lung / Q000473:pathology; D010179:Pancreas / Q000473:pathology
vernacular_title: Mukovistsidoz v iunosheskom vozraste.