[Waldman's disease. Primary intestinal lymphangiectasis].
BACKGROUND
Primary intestinal lymphangiectasias are often associated with lymphoedema.


METHODS
The diagnosis was performed at 4 months when Maxime presented with lymphoedema, diarrhea, hypoprotidemia and hypolipemia. Duodenum biopsies revealed intestinal lymphangiectasias. An hyperprotidic and low fat diet, medium chain triglyceride-supplemented and an elastic contention allowed a decline of the oedemas.


CONCLUSIONS
We report one case of Waldman's disease. It shows very well the typical circumstances of diagnosis in this disease and the two types of oedema (lymphoedema and hypoprotidic oedema).
Misery
L
L
Clinique Dermatologique, Hôpital Edouard-Herriot, Lyon.
Lachaux
A
A
Chambon
M
M
Faure
M
M
Claudy
A
A
D004044:Dietary Proteins / Q000008:administration & dosage; D006801:Humans; D007223:Infant; D008201:Lymphangiectasis, Intestinal / Q000150:complications* / Q000178:diet therapy; D008209:Lymphedema / Q000150:complications* / Q000178:diet therapy; D008297:Male
D004044:Dietary Proteins
Maladie de Waldman. Lymphangiectasies intestinales primitives.