Möbius syndrome with dental involvement: a case report and literature review.
The clinicopathological findings on a 17-year-old female with the Möbius/Moebius syndrome are reported. The signs and symptoms of this neuromuscular condition include congenital bilateral or unilateral palsies of the facial and abducens cranial nerves and a broad scope of multisystem abnormalities. A case of unilateral deficiencies of cranial nerves VI and VII, congenital ectrodactyly of toes, and multiple congenitally missing primary and permanent teeth is reported. A review of the literature reveals various ideas regarding the diversity of symptoms and the etiology of the syndrome. The purpose of this article is to report oral manifestations, such as congenitally missing teeth, associated with Möbius syndrome.
Rizos
M
M
Department of Orthodontics, Columbia University, New York, New York, USA.
Negrón
R J
RJ
Serman
N
N
D000010:Abducens Nerve / Q000503:physiopathology; D000293:Adolescent; D000539:Alveolar Process / Q000002:abnormalities; D000848:Anodontia / Q000473:pathology; D005146:Facial Asymmetry / Q000473:pathology; D005158:Facial Paralysis / Q000151:congenital / Q000473:pathology*; D005260:Female; D006801:Humans; D008312:Malocclusion, Angle Class II / Q000473:pathology; D010243:Paralysis / Q000151:congenital; D014034:Toes / Q000002:abnormalities; D014071:Tooth Abnormalities / Q000473:pathology*; D014094:Tooth, Deciduous / Q000002:abnormalities