Fenestration of extracardiac fontan and reversal of protein-losing enteropathy: case report.
We describe a patient with protein-losing enteropathy who presented 6 months after undergoing a modified Fontan operation. After failing to respond to medical therapy, the Fontan tunnel was fenestrated by catheter intervention with immediate improvement and resolution of hypoproteinemia and enteric protein loss.
Lemes
V
V
Department of Pediatrics, Division of Pediatric Cardiology, The Johns Hopkins Hospital, 600 North Wolfe Street, Brady 5, Baltimore, MD 21287, USA.
Murphy
A M
AM
Osterman
F A
FA
Laschinger
J C
JC
Kan
J S
JS
D000792:Angiography; D006328:Cardiac Catheterization; D002675:Child, Preschool; D017548:Echocardiography, Transesophageal; D005500:Follow-Up Studies; D018729:Fontan Procedure / Q000009:adverse effects*; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D008297:Male; D011183:Postoperative Complications / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D011504:Protein-Losing Enteropathies / Q000209:etiology*; D011651:Pulmonary Artery / Q000000981:diagnostic imaging; D012086:Reoperation