[A case of asplenia in a sickle cell homozygote SS patient].
One case of total splenic atrophy is reported in a patient with SS homozygous sickle-cell disease presenting no related malformation, thus recalling the IVEMARK syndrome. An abdominal echography and computed tomography are indispensable in order to confirm the absence of the anatomic spleen; this makes for a better follow-up of sickle-cell disease.
N'Zi
K P
KP
Service de radiologie, C.H.U. de Treichville, Abidjan, Côte d'Ivoire.
N'Dri
K
K
Ouattara
D N
DN
Kone
T
T
Diabate
A S
AS
Gbazi
G C
GC
Djedje
A T
AT
D000293:Adolescent; D000755:Anemia, Sickle Cell / Q000000981:diagnostic imaging / Q000235:genetics / Q000473:pathology*; D006720:Homozygote; D006801:Humans; D013154:Spleen / Q000002:abnormalities*; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography
Un cas d'asplénie chez un drépanocytaire homozygote SS.