title: Failure to control the airway in a patient with Hunter's syndrome.
abstract: Hunter's syndrome is due to recessively inherited mucopolysaccharide storage diseases. The anaesthetic complications in this syndrome are related to the organs involved in the disease, but pertain especially to upper airway obstruction problems. We report a patient with Hunter's syndrome who, while under general anaesthesia for a simple procedure (the introduction of bilateral grommets), suffered a fatal outcome.
authors.affiliation: Department of Anaesthesiology, Bnai Zion Medical Center, Haifa, Israel.
authors.forename: L
authors.initials: L
authors.lastname: Gaitini
authors.forename: M
authors.initials: M
authors.lastname: Fradis
authors.forename: S
authors.initials: S
authors.lastname: Vaida
authors.forename: G
authors.initials: G
authors.lastname: Collins
authors.forename: M
authors.initials: M
authors.lastname: Croitoru
authors.forename: M
authors.initials: M
authors.lastname: Somri
authors.forename: Z
authors.initials: Z
authors.lastname: Borochovitz
authors.forename: A
authors.initials: A
authors.lastname: Golz
mesh_terms: D000293:Adolescent; D000402:Airway Obstruction / Q000209:etiology*; D000768:Anesthesia, General; D017809:Fatal Outcome; D006801:Humans; D007431:Intraoperative Complications; D008297:Male; D008876:Middle Ear Ventilation; D016532:Mucopolysaccharidosis II / Q000601:surgery*