[Extra-adrenal retroperitoneal paraganglioma].
OBJECTIVE
To report a case of paraganglioma localized in the organ of Zuckerkandl and to discuss its diagnosis, treatment and outcome.


RESULTS
A 37-year-old female presented with a periumbilical mass and pain that radiated to the lumbar region for the past three months. Abdominal US and CT disclosed a well vascularized mass lying adjacent to the aorta, 1 cm from its bifurcation. At laparotomy, an 8 x 10 cm tumor was discovered at the aortic bifurcation that displaced the left ureter and included the inferior mesenteric artery. Pathological analysis of the surgical specimen revealed a paraganglioma.


CONCLUSIONS
Extra-adrenal paraganglioma should be taken into account in the differential diagnosis of retroperitoneal masses, particularly those adjoining the abdominal aorta.
Prieto Nieto
M I
MI
Departamento de Cirugía General, Hospital Universitario La Paz, Facultad de Medicina, Universidad Autónoma de Madrid, España.
Pérez Robledo
J P
JP
Hardisson
D
D
Palenzuela Fernández
J L
JL
Nistal Martín
M
M
D000328:Adult; D005260:Female; D006801:Humans; D010235:Paraganglioma / Q000473:pathology / Q000601:surgery; D012186:Retroperitoneal Neoplasms / Q000473:pathology / Q000601:surgery
Paraganglioma retroperitoneal extraadrenal.