title: Fenestration of extracardiac fontan and reversal of protein-losing enteropathy: case report.
abstract: We describe a patient with protein-losing enteropathy who presented 6 months after undergoing a modified Fontan operation. After failing to respond to medical therapy, the Fontan tunnel was fenestrated by catheter intervention with immediate improvement and resolution of hypoproteinemia and enteric protein loss.
authors.affiliation: Department of Pediatrics, Division of Pediatric Cardiology, The Johns Hopkins Hospital, 600 North Wolfe Street, Brady 5, Baltimore, MD 21287, USA.
authors.forename: V
authors.initials: V
authors.lastname: Lemes
authors.forename: A M
authors.initials: AM
authors.lastname: Murphy
authors.forename: F A
authors.initials: FA
authors.lastname: Osterman
authors.forename: J C
authors.initials: JC
authors.lastname: Laschinger
authors.forename: J S
authors.initials: JS
authors.lastname: Kan
mesh_terms: D000792:Angiography; D006328:Cardiac Catheterization; D002675:Child, Preschool; D017548:Echocardiography, Transesophageal; D005500:Follow-Up Studies; D018729:Fontan Procedure / Q000009:adverse effects*; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D008297:Male; D011183:Postoperative Complications / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D011504:Protein-Losing Enteropathies / Q000209:etiology*; D011651:Pulmonary Artery / Q000000981:diagnostic imaging; D012086:Reoperation