Polyostotic fibrous dysplasia associated with intramuscular myxomas: Mazabraud's syndrome.
Mazabraud's syndrome, though uncommon, is reported increasingly frequently. It represents an entity readily recognisable radiologically on MR imaging. Awareness of the syndrome, particularly when the myxoma is solitary, can prevent misdiagnosis of intramuscular myxomas (especially when large) as malignant mesenchymal tumors containing myxoid tissue. We review the 34 cases previously reported in the literature and include a recent case from our center.
Cabral
C E
CE
Department of Radiology, Instituto Nacional de Câncer (INCA), Rio de Janeiro, Brazil.
Guedes
P
P
Fonseca
T
T
Rezende
J F
JF
Cruz Júnior
L C
LC
Smith
J
J
D000328:Adult; D003937:Diagnosis, Differential; D005269:Femur / Q000473:pathology; D005359:Fibrous Dysplasia, Polyostotic / Q000175:diagnosis / Q000473:pathology*; D005500:Follow-Up Studies; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D019042:Muscle Neoplasms / Q000175:diagnosis / Q000473:pathology*; D009232:Myxoma / Q000175:diagnosis / Q000473:pathology*; D019275:Radiopharmaceuticals; D012272:Ribs / Q000473:pathology; D012509:Sarcoma / Q000175:diagnosis; D013577:Syndrome; D013669:Technetium Tc 99m Medronate; D013848:Thigh / Q000473:pathology; D014057:Tomography, X-Ray Computed
D019275:Radiopharmaceuticals; D013669:Technetium Tc 99m Medronate