Absent pulmonary valve syndrome with interrupted aortic arch.
A surgically treated case of absent pulmonary valve syndrome associated with type B interrupted aortic arch is presented. The presence of a restrictive ductus arteriosus promoted the development of a collateral circulation between ascending and descending thoracic aorta, allowing the child to remain clinically stable after birth.
Congenital Heart Disease Centre, and Department of Radiology, University Hospital of Wales, Cardiff, United Kingdom.
C
C
Mignosa
D G
DG
Wilson
A
A
Wood
C R
CR
Kirk
F
F
Musumeci
D001013:Aorta, Thoracic / Q000002:abnormalities*; D003097:Collateral Circulation / Q000502:physiology; D004374:Ductus Arteriosus, Patent / Q000473:pathology / Q000503:physiopathology; D006345:Heart Septal Defects, Ventricular / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities; D011664:Pulmonary Valve / Q000002:abnormalities*; D011665:Pulmonary Valve Insufficiency / Q000473:pathology; D011666:Pulmonary Valve Stenosis / Q000473:pathology; D013577:Syndrome