Absent pulmonary valve syndrome with interrupted aortic arch.
A surgically treated case of absent pulmonary valve syndrome associated with type B interrupted aortic arch is presented. The presence of a restrictive ductus arteriosus promoted the development of a collateral circulation between ascending and descending thoracic aorta, allowing the child to remain clinically stable after birth.
Mignosa
C
C
Congenital Heart Disease Centre, and Department of Radiology, University Hospital of Wales, Cardiff, United Kingdom.
Wilson
D G
DG
Wood
A
A
Kirk
C R
CR
Musumeci
F
F
D001013:Aorta, Thoracic / Q000002:abnormalities*; D003097:Collateral Circulation / Q000502:physiology; D004374:Ductus Arteriosus, Patent / Q000473:pathology / Q000503:physiopathology; D006345:Heart Septal Defects, Ventricular / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities; D011664:Pulmonary Valve / Q000002:abnormalities*; D011665:Pulmonary Valve Insufficiency / Q000473:pathology; D011666:Pulmonary Valve Stenosis / Q000473:pathology; D013577:Syndrome