Unilateral absence of pulmonary artery and ventricular septal defect in an infant.
A 2-month-old boy was diagnosed as having a rare combination of absence of left pulmonary artery and ventricular septal defect. He underwent intracardiac repair at the age of 8 months. Reconstruction of the left pulmonary artery was impossible because it could not be visualized through a median sternotomy. Although his early postoperative course was uneventful, he needed ipsilateral pneumonectomy 3 months later because of unremitting hemoptysis. Hilar left pulmonary artery, which used to exist, was not found even by histologic examination.
Department of Cardiovascular Surgery, Japanese Red Cross Medical Center, Tokyo.
K
K
Imanaka
S
S
Shimizu
J
J
Matsumoto
K
K
Hashizume
K
K
Tsuchiya
T
T
Takemura
D001013:Aorta, Thoracic / Q000473:pathology; D016122:Brachiocephalic Trunk / Q000473:pathology; D003097:Collateral Circulation; D006345:Heart Septal Defects, Ventricular / Q000473:pathology* / Q000601:surgery; D006469:Hemoptysis / Q000601:surgery; D006801:Humans; D007223:Infant; D008168:Lung / Q000098:blood supply; D008297:Male; D011013:Pneumonectomy; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D013249:Sternum / Q000601:surgery; D013908:Thoracotomy