[Temporal fibrous dysplasia with labyrinthine involvement. Apropos of a case and review of the literature].
Craniofacial fibrous dysplasia manifests clinically with dysmorphic syndrome, ophtalmologic or otologic signs. We report a case of temporal polyostotic fibrous dysplasia with vertigo and sensorineural hearing loss. Sensorineural hearing loss, with no cholesteatoma associated, as described in our case is rarely described. We review the literature concerning main clinical, diagnostic and therapeutic aspects of this disease.
Service ORL, CHU, Caen.
S
S
Moreau
N
N
Bourdon
M
M
Goullet de Rugy
A
A
Bequignon
E
E
Babin
A
A
Valdazo
D000368:Aged; D005146:Facial Asymmetry / Q000209:etiology; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000150:complications* / Q000175:diagnosis; D034381:Hearing Loss / Q000209:etiology; D006801:Humans; D007759:Labyrinth Diseases / Q000209:etiology; D008279:Magnetic Resonance Imaging; D013701:Temporal Bone; D014057:Tomography, X-Ray Computed