Surgical ablation of a cardiac rhabdomyoma in an infant with tuberous sclerosis.
Cardiac rhabdomyoma is a rare tumor. Because of its rate of regression, mainly in the first year of life, conservative therapy is generally suggested when diagnosis occurs in infancy. We report surgical ablation of a rhabdomyoma in a 2-month-old boy in whom the tumor extended into the subaortic outflow tract. The tumor, which had a dual attachment to the aortic and mitral valves, was safely removed without any valvar damage. We suggest immediate surgical intervention for those rhabdomyomas which are life-threatening because of their size, location, or arrhythmogenicity.
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, Paris, France.
D
D
Henglein
N M
NM
Guirgis
G
G
Bloch
D006338:Heart Neoplasms / Q000209:etiology / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D012207:Rhabdomyoma / Q000209:etiology / Q000601:surgery*; D014402:Tuberous Sclerosis / Q000150:complications*