Identification of the newly discovered 58 kDa peroxisomal thiolase SCPx as the main thiolase involved in both pristanic acid and trihydroxycholestanoic acid oxidation: implications for peroxisomal beta-oxidation disorders.
Wanders
R J
RJ
University of Amsterdam, Academic Medical Centre, Department of Clinical Chemistry, The Netherlands.
Denis
S
S
van Berkel
E
E
Wouters
F
F
Wirtz
K W
KW
Seedorf
U
U
D000101:Acetyl-CoA C-Acetyltransferase / Q000378:metabolism*; D002352:Carrier Proteins / Q000378:metabolism*; D002777:Cholestanols / Q000378:metabolism*; D005227:Fatty Acids / Q000378:metabolism*; D006801:Humans; D008830:Microbodies / Q000201:enzymology*; D010084:Oxidation-Reduction; D018901:Peroxisomal Disorders / Q000201:enzymology*
D002352:Carrier Proteins; D002777:Cholestanols; D005227:Fatty Acids; C072087:sterol carrier proteins; C022069:3,7,12-trihydroxycholestan-26-oic acid; C002844:pristanic acid; D000101:Acetyl-CoA C-Acetyltransferase