Unilateral absence of pulmonary artery and ventricular septal defect in an infant.
A 2-month-old boy was diagnosed as having a rare combination of absence of left pulmonary artery and ventricular septal defect. He underwent intracardiac repair at the age of 8 months. Reconstruction of the left pulmonary artery was impossible because it could not be visualized through a median sternotomy. Although his early postoperative course was uneventful, he needed ipsilateral pneumonectomy 3 months later because of unremitting hemoptysis. Hilar left pulmonary artery, which used to exist, was not found even by histologic examination.
Imanaka
K
K
Department of Cardiovascular Surgery, Japanese Red Cross Medical Center, Tokyo.
Shimizu
S
S
Matsumoto
J
J
Hashizume
K
K
Tsuchiya
K
K
Takemura
T
T
D001013:Aorta, Thoracic / Q000473:pathology; D016122:Brachiocephalic Trunk / Q000473:pathology; D003097:Collateral Circulation; D006345:Heart Septal Defects, Ventricular / Q000473:pathology* / Q000601:surgery; D006469:Hemoptysis / Q000601:surgery; D006801:Humans; D007223:Infant; D008168:Lung / Q000098:blood supply; D008297:Male; D011013:Pneumonectomy; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D013249:Sternum / Q000601:surgery; D013908:Thoracotomy