[Porphyria cutanea tarda is the most common type of porphyria. Medical control is a team work].
Porphyria cutanea tarda (PCT) is probably the most common of the porphyrias. The development of skin fragility and blisters are the symptoms that generally bring the patient to the notice of the dermatologist. During the past decade the disease has been recognised as being of heterogeneous aetiology, and a pathogenetic classification has been proposed. The significance of subtyping for the choice of management strategy is currently appreciated, as is the need of close monitoring owing to the risk of the common PCT-associated liver conditions. Preferably the PCT patient should be managed by a dermatologist and a hepatologist working in concert and supported by a specialised porphyria laboratory. The use of a structured management protocol should be considered.
Harper
P
P
Porfyricentrum Sverige.
Thunell
S
S
Hultcrantz
R
R
Ros
A M
AM
Wennersten
G
G
D003937:Diagnosis, Differential; D006801:Humans; D008107:Liver Diseases / Q000175:diagnosis; D010347:Patient Care Planning; D010348:Patient Care Team; D017119:Porphyria Cutanea Tarda / Q000175:diagnosis / Q000235:genetics / Q000628:therapy; D012871:Skin Diseases / Q000175:diagnosis; D014575:Uroporphyrinogen Decarboxylase / Q000737:chemistry / Q000235:genetics / Q000378:metabolism
D014575:Uroporphyrinogen Decarboxylase