[Aggressive fibromatosis in childhood: retrospective analysis of four cases].
OBJECTIVE
Aggressive fibromatosis is a rare illness in children. We analyzed the records of four patients, taken from a total of 505, all of which had different types of tumours, over a period of ten years. In the four cases, three were male and one female. Their ages ranged from 0-7 years old. We also did a review of this pathology.


RESULTS
The illness may present itself a a painless mass found particularly in the pelvic area, knee, buttock and anterior mediastinum, respectively. Two of these cases presented lysis of osseous tissue shown in radiologic assays. The diagnosis was histological in every case. The only treatment was surgical in all of them. Two of the cases required only one intervention to achieve remission and up to now there has been no record of further illness. At the time of writing this paper the patients are alive after a follow-up period of thirty months.


CONCLUSIONS
Up to now, no other alternative forms of treatment have been convincing. Adjuvant radiation and chemotherapy are probably beneficial, but the precise indication for its use is not well defined.
Unidad de Hematooncología pediatrica, Hospital 12 de Octubre.
C
C
Garrido Colino
J
J
López Pérez
M E
ME
Palacios López
J L
JL
Vivanco Martínez
M J
MJ
Torres Valdivieso
C
C
Melero Moreno
J L
JL
Rodríguez Peralto
D001859:Bone Neoplasms / Q000175:diagnosis* / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D005260:Female; D018222:Desmoid Tumors / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D012189:Retrospective Studies; D014057:Tomography, X-Ray Computed