[Porphyria cutanea tarda with severe clinical complications. A 20-year follow-up].
A patient with porphyria cutanea tarda developed distinctive sclerodermoid changes with extensive dystrophic calcification and ulcerations in the sclerotic areas. In addition to these skin complications, over the course of 20 years other internal problems also appeared, such as diabetes mellitus, fatty cirrhosis and ocular inflammation. These severe clinical complications were related to omission of treatment and the alcohol abuse.
Krajnc
I
I
Abt. für innere Medizin und Rheumatologie, Lehrhospital Maribor.
Rozman
B
B
Pahor
A
A
D000328:Adult; D002114:Calcinosis / Q000175:diagnosis / Q000209:etiology; D003306:Coproporphyrins / Q000097:blood; D018450:Disease Progression; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D017119:Porphyria Cutanea Tarda / Q000150:complications* / Q000175:diagnosis; D012535:Scalp / Q000473:pathology; D012867:Skin / Q000473:pathology; D012883:Skin Ulcer / Q000175:diagnosis / Q000209:etiology; D016312:Treatment Refusal; D014578:Uroporphyrins / Q000097:blood
D003306:Coproporphyrins; D014578:Uroporphyrins