Hamartoma of the mitral valve with blood cysts: a rare tumor detected by echocardiography.
A 16-year-old boy was submitted to a cardiac examination after an episode of faintness. A transthoracic echocardiogram was performed, which revealed a very mobile multicystic tumor attached to the mitral valve. A small solid mass adherent to the cysts was better defined by transesophageal echocardiography. The patient was submitted to cardiac surgery consisting of tumor resection and a mitral prosthesis implant. The surgery was successful. The tumor consisted of three bright red tense cysts with hematic content, each 1 to 2 cm in diameter. The cysts were coalescent and adherent to a solid mass attached to the posterior papillary muscle head. Histopathologic examination revealed a hamartoma with a cystic part composed of the proliferation of myofibroblast cells in a stroma with vessels, collagen, and elastin fibers. Valvular hamartoma with blood cysts is a very rare cardiac tumor both for its histopathology and its localization.
Serviço de Cardiologia do Hospital Fernando Fonseca, Lisboa, Portugal.
A
A
Abreu
A
A
Galrinho
E P
EP
Sá
S
S
Ramos
A P
AP
Martins
J
J
Fragata
R
R
Ferreira
D000293:Adolescent; D003560:Cysts / Q000000981:diagnostic imaging; D004452:Echocardiography; D017548:Echocardiography, Transesophageal; D006222:Hamartoma / Q000000981:diagnostic imaging*; D006338:Heart Neoplasms / Q000000981:diagnostic imaging; D006349:Heart Valve Diseases / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D008943:Mitral Valve