Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease).
Sinus histiocytosis with massive lymphadenopathy (SHML) is a distinct clinicopathological entity described by Rosai and Dorfman and differentiated by other childhood histiocytoses by its distinct characteristics. This is a rare pathology and should be kept in mind for differential diagnosis of neck masses, especially in childhood. In this article a case with SHML is presented and clinical features of the disease given.
Unal
O F
OF
Department of Otolaryngology, Head & Neck Surgery, Hacettepe University Medical Faculty, Ankara, Turkey. ofunal@tr-net.net.tr
Köybaşi
S
S
Kaya
S
S
D003937:Diagnosis, Differential; D015618:Histiocytosis, Sinus / Q000175:diagnosis*; D006801:Humans; D007223:Infant; D008206:Lymphatic Diseases / Q000209:etiology*; D008297:Male; D009333:Neck