[Multiple and unilateral angiofibromas of the face: forme fruste of Bourneville tuberous sclerosis].
BACKGROUND
Multiple facial angiofibromas are considered a characteristic and pathognomonic feature of tuberous sclerosis. In contrast, the observation of localized multiple angiofibromas limited to one side of the face is a uncommon.


METHODS
We cared for two patients with multiple clustered unilateral angiofibromas (although one patient also presented a few angiofibromas on the other side) without other features associated with the sclerosis tuberous complex.


CONCLUSIONS
The possibility that these patients presented an independent disorder or a minor form of tuberous sclerosis is discussed.
García Muret
M P
MP
Clínica Quirón, Barcelona, España.
Pujol
R M
RM
de Moragas
J M
JM
D018322:Angiofibroma / Q000175:diagnosis* / Q000473:pathology; D002648:Child; D005153:Facial Neoplasms / Q000175:diagnosis* / Q000473:pathology; D005260:Female; D006801:Humans; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis* / Q000473:pathology; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000473:pathology; D014402:Tuberous Sclerosis / Q000175:diagnosis*