[Congenital skin defect and fetus papyraceus. A case].
BACKGROUND
Congenital skin defect is an uncommon condition. The term of "congenital skin aplasia" should be avoided since the origin may not necessarily be congenital malformation. The scalp is involved in 80 p. 100 of the cases.


METHODS
We observed a congenital skin defect located exclusively on the trunk. The infant lacked wide areas of skin in symmetrical star-like configurations.


CONCLUSIONS
The notion of a twin expulsed after 4 months gestation suggested the diagnosis of congenital skin defect and fetus papyraceus or group V congenital skin aplasia in the Frieden classification as recalled. This diagnosis must not be overlooked as the prognosis is good. Closure with atrophic skin usually occurs within a few weeks. The etiopathogenesis remains obscure.
Reichert
S
S
Service de Dermatologie, Hôpital Fournier, Nancy.
Cocciale
M P
MP
Lemelle
J L
JL
Barbaud
A
A
Schmitt
M
M
Weber
M
M
Schmutz
J L
JL
D004200:Diseases in Twins; D005260:Female; D005313:Fetal Death; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D011379:Prognosis; D012868:Skin Abnormalities / Q000209:etiology / Q000473:pathology; D013909:Thorax