[Spindle-cell hemangioendothelioma with monomelic and multifocal form in a child].
BACKGROUND
Spindle-cell hemangioendothelioma is a soft tissue skin tumor recently identified histologically. It can occur at all ages but generally is seen in young adults. The lesion usually occurs as a subcutaneous mass involving the limbs.


METHODS
A particular case of spindle-cell hemangioendothelioma was observed in an 18-month-old child. The lesions progressed with a monomelic distribution on the upper limb. Histological diagnosis of spindle-cell hemangioendothelioma was achieved at the age of 6 years.


CONCLUSIONS
The age of the patient and the monomelic distribution is particular in this case of spindle-cell hemangioendothelioma, inciting a nosological discussion on this disease and other vascular tumors of childhood and the relationship of these types of lesions with Maffucci's syndrome. Although no anomalies have been detected to date, radiological surveillance is needed as cases of Maffucci's syndrome associated with spindle-cell hemangioendothelioma is described in the literature.
Bodemer
C
C
Service de Dermatologie, Groupe Hospitalier Necker-Enfants Malades, Paris.
Fraitag
S
S
Amoric
J C
JC
Benaceur
S
S
Brunelle
F
F
De Prost
Y
Y
D006225:Hand; D006390:Hemangioendothelioma / Q000473:pathology*; D006801:Humans; D007223:Infant; D008297:Male; D009361:Neoplasm Invasiveness; D011379:Prognosis; D012878:Skin Neoplasms / Q000473:pathology*