Dyskeratosis congenita associated with Hodgkin's disease.
Dyskeratosis congenita is a rare, hereditary, multisystem disorder characterized by mucocutaneous changes, pancytopenia and increased incidence of malignancy. Different types of neoplasia have been reported in association with dyskeratosis congenita. We present a second case associated with Hodgkin's disease. Delayed appearance of dermatological signs and association with chronic hepatitis B are other unusual features of this case.
Baykal
C
C
Dermatology Department, Istanbul University, Istanbul Medical School.
Büyükbabani
N
N
Kavak
A
A
D000328:Adult; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D001707:Biopsy, Needle; D003131:Combined Modality Therapy; D019871:Dyskeratosis Congenita / Q000150:complications* / Q000175:diagnosis; D005500:Follow-Up Studies; D019694:Hepatitis B, Chronic / Q000150:complications* / Q000175:diagnosis; D006689:Hodgkin Disease / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008297:Male; D011878:Radiotherapy; D016896:Treatment Outcome