[Pachydermoperiostosis with extramedullary hematopoiesis without myelofibrosis].
BACKGROUND
In three previous reports of primary hypertrophic osteoarthropathy, an associated extramedullary hematopoiesis was related to myelofibrosis.


METHODS
A 44-year-old male patient with primary hypertrophic osteoarthropathy diagnosed when he was 34-year-old was referred to our hospital with an abdominal mass fortuitously detected.


CONCLUSIONS
The present case is unique for the patient developed an extramedullary hematopoïesis without associated myelofibrosis. It suggests the possible intervention of growth factors common to the skin fibroblasts and the blood progenitor cells in the pathogenesis of primary osteoarthropathy.
Venencie
P Y
PY
Unité de Dermatologie, CHU Bicêtre, Le Kremlin Bicêtre.
Blanchet
P
P
Mallet
V
V
Chantome
A
A
Quillard
J
J
Croisille
L
L
Lavabre
C
C
Tchernia
G
G
Bouchard
P
P
Benoit
G
G
D000005:Abdomen; D000328:Adult; D006411:Hematopoiesis, Extramedullary; D006801:Humans; D008297:Male; D010004:Osteoarthropathy, Primary Hypertrophic / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D055728:Primary Myelofibrosis / Q000209:etiology*; D014057:Tomography, X-Ray Computed