[Primary adrenal lymphoma with latent adrenal insufficiency: a case report and literature review].
We report a new case of primary adrenal lymphoma with latent adrenal insufficiency and long-term remission after hydrocortisone replacement therapy. We have analyzed 29 other cases described in the literature. This disease with poor prognosis can be revealed by an incidentally discovered, frequently bilateral, adrenal mass. Adrenal insufficiency may be latent and the diagnostic procedure should include both cortisol and ACTH determination with an additional ACTH stimulation test if appropriate. Early adrenal substitution can improve patient survival.
Maugendre
D
D
Service d'endocrinologie, Hôpital Sud, Rennes.
Derrien
C
C
Grulois
I
I
Simon
J P
JP
Guilhem
I
I
Poirier
J Y
JY
Le Prise
P Y
PY
Allannic
H
H
D000310:Adrenal Gland Neoplasms / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D000309:Adrenal Insufficiency / Q000209:etiology / Q000473:pathology*; D000368:Aged; D015914:Estrogen Replacement Therapy; D006801:Humans; D006854:Hydrocortisone / Q000627:therapeutic use; D008223:Lymphoma / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D008279:Magnetic Resonance Imaging; D008297:Male; D014057:Tomography, X-Ray Computed
D006854:Hydrocortisone