[Melkersson-Rosenthal syndrome: clinical features and a suggested diagnostic grading system].
The case history of a patient with orofacial oedema is presented, together with the findings on extensive investigation. A diagnosis of Melkersson-Rosenthal syndrome (MRS) was made. This case demonstrated the difficulties in diagnosis in monosymptomatic cases, and the importance of further investigation (EMG). MRS is a rare condition with a triad of symptoms: orofacial oedema, facial palsy, and plicated or "scrotal" tongue. The pathogenesis is unknown. The vital prognosis is good. Treatment has not been specific. It relies on local (intra-lesional) and systemic steroids, and elective eyelid surgery. Clofamizine has proved an effective alternative treatment.
Kharoubi
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CHU IBN Rochd, Service O.R.L., Annaba, Algérie.
D000328:Adult; D006801:Humans; D008297:Male; D008556:Melkersson-Rosenthal Syndrome / Q000175:diagnosis*
Syndrome de Melkersson-Rosenthal: considérations cliniques et proposition d'un gradient diagnostique.