[Papillary edema and the POEMS syndrome].
POEMS syndrome is a multisystem disorder associated with plasma cell dyscrasia. Papilloedema is a feature of this syndrome with an incidence ranging from 33% to 84% in published reports. Its pathogenesis remains unclear. We present an observation that clearly demonstrates the difficulties to diagnose this affection. POEMS syndrome can be accepted as one of the various etiologies of papilloedema. Considering this observation and the recent publications, different pathological hypothesis are reviewed.
Gatinel
D
D
Service d'Ophtalmologie, Hôpital Avicenne, Bobigny, France.
Larroche
C
C
Fanjkuchen
F
F
Chaine
G
G
Guillevin
L
L
D003520:Cyclophosphamide / Q000627:therapeutic use; D003937:Diagnosis, Differential; D005260:Female; D005500:Follow-Up Studies; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D006965:Hyperplasia; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D015994:Incidence; D008875:Middle Aged; D016878:POEMS Syndrome / Q000150:complications / Q000175:diagnosis / Q000473:pathology* / Q000628:therapy; D010211:Papilledema / Q000209:etiology / Q000473:pathology*; D010950:Plasma Cells / Q000473:pathology; D010951:Plasma Exchange; D011241:Prednisone / Q000627:therapeutic use
D005938:Glucocorticoids; D007166:Immunosuppressive Agents; D003520:Cyclophosphamide; D011241:Prednisone
Oedème papillaire et syndrome POEMS.