[Malignant transformation of Recklinghausen disease in the small intestine].
Neurofibromatosis is a relatively common genetic disorder of the peripheral and central nervous systems. Benign or malignant tumours may occur in different organs. Visceral tumours arising in the neural plexus of the intestinal wall may cause ulceration, bleeding, obstruction, perforation and palpable abdominal masses. In this paper a case of chronic anaemia due to a chronically bleeding intestinal neurofibroma is presented in a woman who had undergone intestinal resection. Histopathological analysis showed a neurofibroma with malignant transformation and a liver metastasis.
Khalil
M R
MR
Organkirurgisk afdeling, Sygehus Fyn, Middelfart.
D000368:Aged; D000740:Anemia / Q000175:diagnosis; D002471:Cell Transformation, Neoplastic / Q000473:pathology*; D003937:Diagnosis, Differential; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000175:diagnosis; D006801:Humans; D007580:Jejunal Neoplasms / Q000473:pathology*; D008113:Liver Neoplasms / Q000473:pathology / Q000556:secondary*; D009456:Neurofibromatosis 1 / Q000473:pathology*
Malign transformation af mb. Recklinghausen i tyndtarmen.