title: [A little known cause of chronic renal insufficiency in the adult: systemic tuberous sclerosis].
abstract: BACKGROUND
  Angiomyolipomas and renal cysts are commonly observed in patients with systemic tuberous sclerosis. Hemorrhagic complications related to the angiomyolipomas are well known.
  
  
  METHODS
  A 63-year old woman was hospitalized for severe chronic renal failure. Physical examination revealed skin manifestations of systemic tuberous sclerosis, which the patient had hidden to date. The radiographic work-up demonstrated complete disorganization of the renal parenchyma in both kidneys due to multiple cysts and angiomyolipomas.
  
  
  CONCLUSIONS
  Chronic renal failure can be the inaugural manifestation in low-grade cases of systemic tuberous sclerosis which may go undiagnosed for years allowing progressive destruction of the kidneys.
authors.affiliation: Service de Néphrologie, Centre Hospitalier Général, Ajaccio.
authors.forename: J M
authors.initials: JM
authors.lastname: Poux
authors.forename: A
authors.initials: A
authors.lastname: Tifoura
authors.forename: C
authors.initials: C
authors.lastname: Leroux-Robert
mesh_terms: D005260:Female; D006801:Humans; D007676:Kidney Failure, Chronic / Q000209:etiology*; D008875:Middle Aged; D014402:Tuberous Sclerosis / Q000150:complications*