Chorioretinal vascular abnormalities associated with angioid streaks and pseudoxanthoma elasticum.
OBJECTIVE
To analyze the retinal and choroidal vascular abnormalities in eyes with angioid streaks (AS) associated with pseudoxanthoma elasticum (PXE).


METHODS
Color photographs and fluorescein angiograms of 54 eyes of 27 consecutive patients with AS and PXE were examined retrospectively.


RESULTS
Four (7%) of the 54 eyes had a major vascular abnormality at the level of the disc; this took the form of a large vascular loop corresponding to an arteriovenous communication between retina and choroid in 3 eyes (6%) and an anastomosis between 2 retinal arteries in 1 eye (2%).


CONCLUSIONS
Analysis of the vascular network in these eyes showed several vascular abnormalities, among which chorioretinal arteriovenous communications appear to be the most dramatic.
Secrétan
M
M
Department of Ophthalmology, Hôpital Jules Gonin, Lausanne, Switzerland.
Zografos
L
L
Guggisberg
D
D
Piguet
B
B
D000328:Adult; D000368:Aged; D000793:Angioid Streaks / Q000150:complications* / Q000473:pathology; D001159:Arterio-Arterial Fistula / Q000209:etiology* / Q000473:pathology; D001164:Arteriovenous Fistula / Q000209:etiology* / Q000473:pathology; D002829:Choroid / Q000098:blood supply*; D005260:Female; D005451:Fluorescein Angiography; D006801:Humans; D007208:Indocyanine Green; D008297:Male; D008875:Middle Aged; D009898:Optic Disk / Q000098:blood supply; D010781:Photography; D011561:Pseudoxanthoma Elasticum / Q000150:complications* / Q000473:pathology; D012171:Retinal Vessels / Q000002:abnormalities* / Q000473:pathology; D012189:Retrospective Studies
D007208:Indocyanine Green