title: [Lymphangioleiomyomatosis and tuberous sclerosis: a casual association or a causative one?].
abstract: Lymphangioleiomyomatosis (LAM) is a rare lung disease that mainly affects women of childbearing age. Pulmonary disease that is indistinguishable from LAM appears in 1% of patients with tuberous sclerosis (TS). At present we can not say whether we are looking at an association of two rare diseases or at a single disease with different clinical profiles. To date, open lung biopsy has been required for definitive diagnosis. We report the case of a women with TS and LAM in whom a diagnosis of pulmonary involvement was based on clinical signs and high resolution computerized tomography of the chest.
authors.affiliation: Servicio de Medicina Interna I, Hospital Clínico San Carlos, Universidad Complutense, Madrid.
authors.forename: R
authors.initials: R
authors.lastname: Lana
authors.forename: J M
authors.initials: JM
authors.lastname: Sánchez-Alarcos
authors.forename: R
authors.initials: R
authors.lastname: Martínez-Cruz
authors.forename: M
authors.initials: M
authors.lastname: Calle
authors.forename: J L
authors.initials: JL
authors.lastname: Alvarez-Sala
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D018192:Lymphangioleiomyomatosis / Q000150:complications* / Q000175:diagnosis; D014057:Tomography, X-Ray Computed; D014402:Tuberous Sclerosis / Q000150:complications* / Q000175:diagnosis
vernacular_title: Linfangioleiomiomatosis y esclerosis tuberosa: una asociación casual o causal?