title: Cochlear implantation in the deaf-blind.
abstract: OBJECTIVE
  This study aimed to examine the outcome and rehabilitation of cochlear implantation in a select group of individuals: the deaf-blind.
  
  
  METHODS
  The study design was a retrospective and prospective case evaluation of the deaf-blind implantees.
  
  
  METHODS
  The study was conducted at a national adult and pediatric cochlear implant center.
  
  
  METHODS
  A total of eight adult and two pediatric blind or visually impaired individuals undergoing cochlear implantation for severe or profound deafness participated. Evaluation of the history, etiology of blindness and deafness, and outcome of the cochlear implantation was examined.
  
  
  METHODS
  Cochlear implantation and subsequent rehabilitation were performed.
  
  
  METHODS
  Bamford-Kowal-Bench (BKB) sentence scores were measured.
  
  
  RESULTS
  Individually and as a group, these patients respond exceptionally well to cochlear implantation. The BKB scores are above the average for the sighted cochlear implantees. This raises the question of heterosensory substitution.
  
  
  CONCLUSIONS
  Cochlear implantation has a major role to play in the rehabilitation of certain deaf-blind individuals, and these patients may be among the most worthwhile to consider for implantation. The implant team must acquire additional rehabilitative skills, and the strength of the deaf-blind culture must be taken into consideration.
authors.affiliation: University Department of Otolaryngology-Head and Neck Surgery, Manchester Royal Infirmary, United Kingdom.
authors.forename: S R
authors.initials: SR
authors.lastname: Saeed
authors.forename: R T
authors.initials: RT
authors.lastname: Ramsden
authors.forename: P R
authors.initials: PR
authors.lastname: Axon
mesh_terms: D000293:Adolescent; D000328:Adult; D000368:Aged; D000369:Aged, 80 and over; D001766:Blindness / Q000150:complications* / Q000534:rehabilitation; D002648:Child; D019929:Cochlear Implantation; D003638:Deafness / Q000150:complications* / Q000534:rehabilitation / Q000601:surgery*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011446:Prospective Studies; D012189:Retrospective Studies; D016896:Treatment Outcome