title: [Multifocal hemangioblastoma in a young woman with Hippel-Lindau syndrome].
abstract: A 25 years old female person suffered from v. Hippel-Lindau disease with three manifestations within the central nervous system (cerebellum, nerve root C1 and Medulla oblongata). Pancreatic cysts, a cyst and a tumour of the kidney were diagnosed as well. In a first operation, the large cerebella's tumour and the small haemangioblastoma of the nerve root C1 were removed via a suboccipital craniectomy. A few weeks later, after the patient had made a good recovery, the tumour at the craniocervical junction was removed through a far lateral approach. The postoperative course was without complications. The MRI control seven months after surgery was free of tumour and the young person was in a good clinical condition, without neurological deficit.
authors.affiliation: Neurochirurgische Abteilung, Akademisches Lehrkrankenhaus München-Bogenhausen, Technische Universität München.
authors.forename: H
authors.initials: H
authors.lastname: Gumprecht
authors.forename: C B
authors.initials: CB
authors.lastname: Lumenta
mesh_terms: D000328:Adult; D001932:Brain Neoplasms / Q000175:diagnosis / Q000235:genetics / Q000601:surgery*; D002528:Cerebellar Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D002531:Cerebellum / Q000473:pathology / Q000601:surgery; D003399:Craniotomy; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008526:Medulla Oblongata / Q000473:pathology / Q000601:surgery*; D010524:Peripheral Nervous System Neoplasms / Q000175:diagnosis / Q000235:genetics / Q000601:surgery*; D011183:Postoperative Complications / Q000175:diagnosis; D013126:Spinal Nerve Roots / Q000473:pathology / Q000601:surgery*; D006623:von Hippel-Lindau Disease / Q000175:diagnosis / Q000235:genetics / Q000601:surgery*
vernacular_title: Multifokales Hämangioblastom bei einer jungen Frau mit von Hippel-Lindau Syndrom.