The near complete tracheal ring deformity.
Congenital complete and near-complete tracheal rings are extremely rare tracheal deformities. There are fewer than 100 cases of congenital complete tracheal rings, and only four cases of near-complete described in the literature. Long-segment occurrences of these anomalies are usually incompatible with life. We describe the presentation of the long-segment near complete tracheal ring deformity and long-segment anterior fusion of cartilage rings (cartilage sleeve deformity) in a living infant. The literature is reviewed, and the embryology, presentation, and management of these extremely rare anomalies are discussed.
Faust
R A
RA
Department of Otolaryngology-Head and Neck Surgery, Mayo, Minneapolis, MN 55455, USA.
Stroh
B
B
Rimell
F
F
D005260:Female; D006801:Humans; D007223:Infant; D007442:Intubation, Intratracheal; D014132:Trachea / Q000002:abnormalities*; D014135:Tracheal Stenosis / Q000151:congenital / Q000196:embryology / Q000628:therapy; D014139:Tracheostomy