Prune belly syndrome with penile and urethral agenesis: report of a case.
The authors report the case of an infant born with prune belly syndrome associated with penile and urethral agenesis. At 15 weeks' gestation, antenatal ultrasonography showed a fetal giant bladder, congenital hydronephrosis, and oligohydramnios, and at 17 weeks' gestation, a fetal vesicoamniotic shunt operation was performed. A boy was born at 33 weeks' gestation with prune belly syndrome, an anocutaneous fistula, and penile agenesis. A cystostomy and cut-back operation were performed immediately, showing urethral agenesis, no urethral opening, and left renal hypoplasia. Thereafter, his renal system began functioning normally, and a urinary tract infection resolved. The authors speculate that the prune belly syndrome in this patient was caused by penile and urethral agenesis.
Kuga
T
T
First Department of Surgery, Yamaguchi University School of Medicine, Ube, Japan.
Esato
K
K
Sase
M
M
Nakata
M
M
Kaneko
J
J
Inoue
T
T
D005315:Fetal Diseases / Q000601:surgery; D006801:Humans; D006869:Hydronephrosis / Q000150:complications / Q000209:etiology* / Q000601:surgery; D007231:Infant, Newborn; D008297:Male; D010413:Penis / Q000002:abnormalities*; D011535:Prune Belly Syndrome / Q000209:etiology* / Q000601:surgery; D014521:Urethra / Q000002:abnormalities*