A review of the management of the hand in dystrophic epidermolysis bullosa.
The hand deformities associated with dystrophic epidermolysis bullosa lead to a mitten-like hand with significant loss of function. The pattern of their development is discussed. Although the digits can be released and divided surgically, the deformity is recurrent. This study provides a review of the literature on the management of the hand in this disease and a discussion of the role of therapy in maintaining hand function.
Mullett
F
F
Great Ormond Street Hospital Trust, London, England.
D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications*; D006225:Hand / Q000601:surgery; D006227:Hand Deformities, Acquired / Q000209:etiology / Q000628:therapy*; D006801:Humans; D026741:Physical Therapy Modalities / Q000379:methods; D013165:Splints