From functional pulmonary atresia to right ventricular restriction. Long term follow up of Uhl's anomaly.
We report a 14 year old boy who presented as a neonate with functional pulmonary atresia due to Uhl's disease with emphasis on the later detection of restrictive right ventricular physiology.
Tumbarello
R
R
The Hospital for Sick Children and University of Toronto, Ontario, Canada.
Adatia
I
I
Yetman
A
A
Boutin
C
C
Izukawa
T
T
Freedom
R M
RM
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000150:complications / Q000473:pathology*; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D018633:Pulmonary Atresia / Q000209:etiology / Q000473:pathology*; D018497:Ventricular Dysfunction, Right / Q000209:etiology / Q000473:pathology*