Successful heart transplantation in a patient with Ivemark syndrome combined with situs inversus, single atrium and ventricle after total cavo-pulmonary connection.
Heart transplantation represents a valuable therapeutical option for patients with congenital heart disease and end-stage heart failure. We report the case of a young adult patient with a situs inversus and additional complex congenital malformations of the heart who underwent several prior palliative interventions, a biventricular repair being impossible. Orthotopic cardiac transplantation with several technical modifications was performed successfully at the age of 19 years.
Berdat
P A
PA
Clinic for Thoracic and Cardiovascular Surgery, University Hospital, Berne, Switzerland.
Mohacsi
P
P
Althaus
U
U
Carrel
T
T
D000015:Abnormalities, Multiple / Q000601:surgery; D000328:Adult; D018610:Heart Bypass, Right; D006330:Heart Defects, Congenital / Q000150:complications / Q000601:surgery*; D016027:Heart Transplantation; D006801:Humans; D010166:Palliative Care / Q000379:methods*; D012857:Situs Inversus / Q000150:complications*