title: From functional pulmonary atresia to right ventricular restriction. Long term follow up of Uhl's anomaly.
abstract: We report a 14 year old boy who presented as a neonate with functional pulmonary atresia due to Uhl's disease with emphasis on the later detection of restrictive right ventricular physiology.
authors.affiliation: The Hospital for Sick Children and University of Toronto, Ontario, Canada.
authors.forename: R
authors.initials: R
authors.lastname: Tumbarello
authors.forename: I
authors.initials: I
authors.lastname: Adatia
authors.forename: A
authors.initials: A
authors.lastname: Yetman
authors.forename: C
authors.initials: C
authors.lastname: Boutin
authors.forename: T
authors.initials: T
authors.lastname: Izukawa
authors.forename: R M
authors.initials: RM
authors.lastname: Freedom
mesh_terms: D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000150:complications / Q000473:pathology*; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D018633:Pulmonary Atresia / Q000209:etiology / Q000473:pathology*; D018497:Ventricular Dysfunction, Right / Q000209:etiology / Q000473:pathology*