title: Intestinal leiomyosarcoma and gastroparesis associated with von Recklinghausen's disease.
abstract: The rare association between intestinal leiomyosarcoma, von Recklinghausen's disease (type-1 neurofibromatosis) and gastroparesis is described. A 20-year-old male, diagnosed 12 years earlier as having pelvic von Recklinghausen's disease, presented with nausea and vomiting. A gastric scintigraphy demonstrated an extremely slow gastric emptying time in the absence of obvious causes for gastroparesis. A small ileal leiomyosarcoma was later found and removed by surgery. The latter was followed by a marked improvement in the clinical condition of the patient.
authors.affiliation: Gastrointestinal Unit, Department of Clinical and Experimental Pathology, University of Udine Medical School, Udine, Italy.
authors.forename: V
authors.initials: V
authors.lastname: Bernardis
authors.forename: D
authors.initials: D
authors.lastname: Sorrentino
authors.forename: D
authors.initials: D
authors.lastname: Snidero
authors.forename: C
authors.initials: C
authors.lastname: Avellini
authors.forename: R
authors.initials: R
authors.lastname: Paduano
authors.forename: C A
authors.initials: CA
authors.lastname: Beltrami
authors.forename: F
authors.initials: F
authors.lastname: Digito
authors.forename: E
authors.initials: E
authors.lastname: Bartoli
mesh_terms: D000328:Adult; D018589:Gastroparesis / Q000209:etiology*; D006801:Humans; D007078:Ileal Neoplasms / Q000453:epidemiology*; D007890:Leiomyosarcoma / Q000453:epidemiology*; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000453:epidemiology*; D009456:Neurofibromatosis 1 / Q000453:epidemiology*; D010257:Paraneoplastic Syndromes / Q000209:etiology*