Obstructed infracardiac total anomalous pulmonary venous connection in an adult.
Adult survival in patients with uncorrected obstructed infracardiac total anomalous pulmonary venous drainage has not been reported. A 17-year-old man who presented to us with features of severe pulmonary arterial hypertension was diagnosed to have obstructed pulmonary venous drainage to the hepatic vein. Presence of a large ventricular septal defect in this patient may have contributed favorably to survival.
Juneja
R
R
Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
Saxena
A
A
Kothari
S S
SS
Taneja
K
K
D000293:Adolescent; D000328:Adult; D003952:Diagnostic Imaging; D004541:Eisenmenger Complex / Q000175:diagnosis; D006345:Heart Septal Defects, Ventricular / Q000175:diagnosis; D006439:Hemodynamics / Q000502:physiology; D006503:Hepatic Veins / Q000002:abnormalities*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000151:congenital / Q000175:diagnosis; D008297:Male; D011379:Prognosis; D011667:Pulmonary Veins / Q000002:abnormalities*; D011668:Pulmonary Veno-Occlusive Disease / Q000151:congenital* / Q000175:diagnosis