[Rett syndrome as a hodogenesis disorder].
In the last few years, Rett syndrome is conceived as a peculiar form of neurodevelopmental post-migrational disorder affecting dendritogenesis. In this article the clinical pathochronic pattern of classical forms is reviewed and the recent neurobiological and genetic evidences suggesting possible future explanations of its nature and origin are discussed.
Narbona
J
J
Unidad de Neurología Pediátrica, Clínica Universitaria de Navarra, Facultad de Medicina, Universidad de Navarra, Pamplona, España.
D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D015518:Rett Syndrome / Q000175:diagnosis* / Q000235:genetics*