title: Spinal cord ganglioglioma in a child with neurofibromatosis type 2. Case report and literature review.
abstract: Gangliogliomas of the spinal cord are rare disease entities that occur in early childhood. Their occurrence in association with neurofibromatosis Type 2 (NF2) has not been described. The authors describe the unique case of a 2-year-old child with stigmata of NF2 who harbored a spinal cord ganglioglioma that presented as a rapidly growing, exophytic intramedullary mass lesion at the cervicomedullary junction. Treatment consisted of complete surgical resection. Histopathological analysis of the lesion demonstrated a mixed population of neoplastic cells, of both neuronal and glial lineage, that supported the diagnosis of ganglioglioma.
authors: Department of Neurological Surgery, Barrow Neurological Institute, and St. Joseph's Hospital and Medical Center, Phoenix, Arizona 85013, USA..
authors: P D
authors: PD
authors: Sawin
authors: N
authors: N
authors: Theodore
authors: H L
authors: HL
authors: Rekate
mesh_terms: D002675:Child, Preschool; D005260:Female; D018303:Ganglioglioma / Q000150:complications* / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D016518:Neurofibromatosis 2 / Q000150:complications*; D013120:Spinal Cord Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000473:pathology / Q000601:surgery