Spontaneous haemothorax: a cause of sudden death in von Recklinghausen's disease.
Vasculopathy is a relatively frequent but poorly recognised manifestation of von Recklinghausen's neurofibromatosis. One of its more dramatic presentations is as spontaneous haemothorax. Clinicians and pathologists should be aware of this syndrome as a cause of sudden death in patients with neurofibromatosis.
Griffiths
A P
AP
Department of Histopathology, Morriston Hospital NHS Trust, Swansea, UK.
White
J
J
Dawson
A
A
D003645:Death, Sudden / Q000209:etiology*; D005260:Female; D006491:Hemothorax / Q000209:etiology*; D006801:Humans; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000473:pathology