Unilateral total and contralateral partial pulmonary agenesis associated with total anomalous pulmonary venous drainage.
A term newborn presented with total right and partial left lung agenesis associated with total anomalous obstructed left pulmonary venous drainage. This unique association with a dramatic prognosis is thought to be due to a developmental insult early in the embryonic formation of the lung and its supporting vasculature.
Finci
V
V
Division of Clinical Pathology, Department of Pathology, University Hospital of Geneva, Geneva, Switzerland.
Beghetti
M
M
Kalangos
A
A
Brundler
M A
MA
D000015:Abnormalities, Multiple; D004322:Drainage; D004452:Echocardiography; D017809:Fatal Outcome; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000000981:diagnostic imaging; D006801:Humans; D007231:Infant, Newborn; D008168:Lung / Q000002:abnormalities*; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery