Acropathia ulcero-mutilans acquisita of the upper limbs.
We report an 80-year-old woman with a bilateral mutilating acro-osteolysis of the fingers progressing over a period of 3 years. As the patient refused nerve or muscle biopsies, our diagnosis of acropathia ulcero-mutilans acquisita or Bureau-Barrière syndrome, characterized by osteolysis, remains hypothetical. Sporadic sensory mutilating acropathy of the upper limbs is rare, and we discuss the differential diagnosis.
Vanhooteghem
O
O
Department of Dermatology and Venereology, University Hospital Saint-Pierre, 129 Boulevard de Waterloo, B-1000 Brussels, Belgium.
Lateur
N
N
Hautecoeur
P
P
Wiart
T
T
D000368:Aged; D000369:Aged, 80 and over; D003937:Diagnosis, Differential; D018450:Disease Progression; D005260:Female; D005385:Fingers; D005500:Follow-Up Studies; D006225:Hand / Q000000981:diagnostic imaging; D006801:Humans; D010015:Osteolysis, Essential / Q000175:diagnosis*; D011859:Radiography