Recurrence of desmoid tumor in a multivisceral transplant patient with Gardner's syndrome.
BACKGROUND
Desmoid tumors are locally invasive fibromatous tumors, which, in patients with Gardner's syndrome, usually occur in the abdominal wall or intra-abdominally. After excision, they tend to recur, often leading to multiple bowel resections.


METHODS
This is a report of the clinical course of a patient with Gardner's syndrome and desmoid tumor who had multiple enterectomies and gradually developed short-gut syndrome. He required prolonged parenteral nutrition, which damaged the liver. The patient underwent a multivisceral transplantation as a life-saving procedure.


RESULTS
After the transplant, the desmoid tumor recurred in the thoracic wall twice and was successfully resected. It also recurred in the abdominal cavity, compressing the intestinal loops; the tumor was excised uneventfully, leaving the graft intact. The recurrent tumors were all of recipient origin.


CONCLUSIONS
Intestinal and multivisceral transplantation could be considered in patients with short-gut syndrome caused by recurrent desmoid tumor. In the case of posttransplant tumor recurrence, resection is the only option recommended.
Misiakos
E P
EP
Department of Surgery, University of Miami School of Medicine, Florida, USA.
Pinna
A
A
Kato
T
T
Rodriguez
M G
MG
Francavilla
A
A
Mazzaferro
V
V
Ruiz
P
P
Reith
J D
JD
Tzakis
A G
AG
D000328:Adult; D005736:Gardner Syndrome / Q000601:surgery*; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000000981:diagnostic imaging* / Q000601:surgery; D012086:Reoperation; D014057:Tomography, X-Ray Computed; D014781:Viscera / Q000637:transplantation*