title: Heart/single-lung transplant for a "failed Fontan" with pulmonary A-V malformation.
abstract: Pulmonary arteriovenous malformation can occur in patients with functional single ventricle after a cavopulmonary connection. There is no effective medical treatment for this complication. Pulmonary arteriovenous malformations may regress over time after heart transplantation, but may be a source of significant perioperative morbidity. We report the case of a woman with single ventricle, ventricular dysfunction, and bilateral pulmonary arteriovenous malformations who had successful treatment of both cardiac and pulmonary failure with en bloc heart and right lung transplantation.
authors.affiliation: Department of Anesthesiology, University of Pennsylvania School of Medicine, Philadelphia, USA.
authors.forename: A R
authors.initials: AR
authors.lastname: Mott
authors.forename: T L
authors.initials: TL
authors.lastname: Spray
authors.forename: N D
authors.initials: ND
authors.lastname: Bridges
mesh_terms: D000328:Adult; D001165:Arteriovenous Malformations / Q000150:complications / Q000601:surgery*; D005260:Female; D018729:Fontan Procedure; D006330:Heart Defects, Congenital / Q000150:complications / Q000601:surgery*; D016041:Heart-Lung Transplantation; D006801:Humans; D008168:Lung / Q000098:blood supply*; D012086:Reoperation; D017211:Treatment Failure