title: Recurrence of desmoid tumor in a multivisceral transplant patient with Gardner's syndrome.
abstract: BACKGROUND
  Desmoid tumors are locally invasive fibromatous tumors, which, in patients with Gardner's syndrome, usually occur in the abdominal wall or intra-abdominally. After excision, they tend to recur, often leading to multiple bowel resections.
  
  
  METHODS
  This is a report of the clinical course of a patient with Gardner's syndrome and desmoid tumor who had multiple enterectomies and gradually developed short-gut syndrome. He required prolonged parenteral nutrition, which damaged the liver. The patient underwent a multivisceral transplantation as a life-saving procedure.
  
  
  RESULTS
  After the transplant, the desmoid tumor recurred in the thoracic wall twice and was successfully resected. It also recurred in the abdominal cavity, compressing the intestinal loops; the tumor was excised uneventfully, leaving the graft intact. The recurrent tumors were all of recipient origin.
  
  
  CONCLUSIONS
  Intestinal and multivisceral transplantation could be considered in patients with short-gut syndrome caused by recurrent desmoid tumor. In the case of posttransplant tumor recurrence, resection is the only option recommended.
authors.affiliation: Department of Surgery, University of Miami School of Medicine, Florida, USA.
authors.forename: E P
authors.initials: EP
authors.lastname: Misiakos
authors.forename: A
authors.initials: A
authors.lastname: Pinna
authors.forename: T
authors.initials: T
authors.lastname: Kato
authors.forename: M G
authors.initials: MG
authors.lastname: Rodriguez
authors.forename: A
authors.initials: A
authors.lastname: Francavilla
authors.forename: V
authors.initials: V
authors.lastname: Mazzaferro
authors.forename: P
authors.initials: P
authors.lastname: Ruiz
authors.forename: J D
authors.initials: JD
authors.lastname: Reith
authors.forename: A G
authors.initials: AG
authors.lastname: Tzakis
mesh_terms: D000328:Adult; D005736:Gardner Syndrome / Q000601:surgery*; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000000981:diagnostic imaging* / Q000601:surgery; D012086:Reoperation; D014057:Tomography, X-Ray Computed; D014781:Viscera / Q000637:transplantation*