Progression of myelinated retinal nerve fibers.
OBJECTIVE
To present a case demonstrating progression of retinal nerve fiber myelin and to suggest that myelinated retinal nerve fibers be considered among the peripapillary choristomas.


METHODS
Case report. A 46-year-old woman demonstrated progression of myelinated retinal nerve fibers and associated retinal vascular anomalies.


RESULTS
Myelinated retinal nerve fibers can be progressive. We confirm earlier reports of vascular anomalies associated with retinal nerve fiber myelin and show that they can also be progressive.


CONCLUSIONS
The rarely progressive nature of myelinated retinal nerve fibers and the histopathologic studies published to date suggest that myelinated retinal nerve fibers represent a striking ophthalmoscopic feature resulting from ectopic oligodendrocytes; thus, the entity may be described as an oligodendrocytic choristoma.
Rosen
B
B
Centre for Ophthalmology and Visual Science, Lions Eye Institute, Perth, Western Australia, Australia. bradrosen@hotmail.com
Barry
C
C
Constable
I J
IJ
D002828:Choristoma / Q000473:pathology; D005260:Female; D005654:Fundus Oculi; D006801:Humans; D008875:Middle Aged; D009186:Myelin Sheath; D009412:Nerve Fibers / Q000473:pathology*; D009900:Optic Nerve / Q000473:pathology*; D012164:Retinal Diseases / Q000473:pathology*; D012171:Retinal Vessels / Q000473:pathology*