Scoliosis secondary to cerebrocosto-mandibular syndrome. A case report with surgical management.
METHODS
A case report of scoliosis secondary to cerebrocosto-mandibular syndrome.


OBJECTIVE
To bring about awareness of the scoliosis and respiratory problems associated with this rare syndrome.


BACKGROUND
Of the approximately 50 cases of this syndrome previously reported, only 3 involved scoliosis, and only 1 of these required surgery (but the patient expired).


METHODS
A retrospective chart was made, and a radiologic review were done.


RESULTS
A successful surgical outcome was achieved, despite severe preoperative curvature (112 degrees scoliosis) and diminished pulmonary function (21% vital capacity).


CONCLUSIONS
This syndrome can be associated with progressive scoliosis but can be managed successfully with surgery.
D002648:Child; D019465:Craniofacial Abnormalities / Q000150:complications*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008607:Intellectual Disability / Q000150:complications; D008159:Lumbar Vertebrae / Q000000981:diagnostic imaging / Q000601:surgery; D008334:Mandible / Q000002:abnormalities*; D011859:Radiography; D012272:Ribs / Q000002:abnormalities*; D012600:Scoliosis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D013123:Spinal Fusion / Q000379:methods*; D013577:Syndrome; D013904:Thoracic Vertebrae / Q000000981:diagnostic imaging / Q000601:surgery