Cloverleaf skull anomaly with extreme orbitostenosis.
A neonate presented with cloverleaf skull anomaly and severe proptosis requiring urgent cranioplasty to attain eyelid closure. Despite this, she experienced exposure keratitis and corneal perforations. A ventriculoperitoneal shunt was performed subsequently to relieve hydrocephalus, but respiratory problems eventually led to her death at 6 months. This case highlights the complexity of the problems encountered in the cloverleaf skull anomaly, and a brief review discussing its management is included. Despite improvements in treatment of this condition, the overall prognosis remains poor.
O'Broin
E S
ES
Craniofacial Unit, Children's Hospital, Dublin, Ireland.
O'Keefe
M
M
Allcutt
D
D
Earley
M J
MJ
D000168:Acrocephalosyndactylia / Q000601:surgery*; D003398:Craniosynostoses / Q000601:surgery*; D005094:Exophthalmos / Q000601:surgery*; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D006849:Hydrocephalus / Q000601:surgery; D007231:Infant, Newborn; D009915:Orbit / Q000002:abnormalities / Q000601:surgery; D010347:Patient Care Planning; D017287:Ventriculoperitoneal Shunt