[Absence of right atrioventricular connection. Morphological and clinical presentation when the dominant ventricle is morphologically right].
Absent right atrioventricular connection, with the left atrium connected to a dominant left-sided morphologically right ventricle is a rare situation. We report five cases with these anatomical features, with emphasis on the morphological and clinical aspects. Although this combination of lesions is very uncommon, the sequential segmental analysis can easily provide an accurate description of the anomaly.
Cavalini
J F
JF
Instituto do Coração do Hospital das Clínicas, FMUSP.
Aiello
V D
VD
Ebaid
M
M
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D006325:Heart Atria / Q000002:abnormalities* / Q000601:surgery; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male