title: [A case of preserved otoacoustic emissions in a child with unilateral idiopathic severe sensorineural hearing loss].
abstract: In this study there is presented a case of unilateral, idiopathic, severe sensorineural hearing loss in a child. The inner ear pathology has been confirmed by tonal and impedance audiometry, and brainstem evoked response audiometry. Simultaneously in the same ear normal otoacoustic emission (SOAE, TEOAE, DPOAE) has been recorded. MRI did not reveal any pathology in internal ear canal and cerebellopontine angle. The presented case suggests that there is a possibility of existence of the normal outer hair cell function with simultaneous inner ear cell disorder or first neuron pathology. Similar cases of idiopathic sensorineural hearing losses with preserved otoacoustic emissions in children were described by Katona (1993), Welz-Mueller (1993) and Konradsson (1996).
authors.affiliation: II Katedra i Klinika Laryngologii Slaskiej AM w Zabrzu.
authors.forename: G
authors.initials: G
authors.lastname: Namysłowski
authors.forename: K
authors.initials: K
authors.lastname: Morawski
authors.forename: G
authors.initials: G
authors.lastname: Trybalska
mesh_terms: D000158:Acoustic Impedance Tests; D000161:Acoustic Stimulation / Q000379:methods*; D001301:Audiometry, Pure-Tone; D002648:Child; D003051:Cochlea / Q000502:physiology*; D016057:Evoked Potentials, Auditory, Brain Stem; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis*; D006801:Humans; D017084:Otoacoustic Emissions, Spontaneous / Q000502:physiology*; D012720:Severity of Illness Index