title: [Gardner syndrome. Maxillofacial management of an extremely advanced form].
abstract: Gardner's syndrome is a very rare hereditary disease resulting from an embryo genesis disorder involving all three ectodermal, mesodermal and endodermal layers. Generally non-digestive tract signs disclose the syndrome. Underlying silent digestive anomalies should be investigated. Endodermal anomalies may have a fundamental effect on prognosis. Manifestations in our case were severe, with ectodermal and mesodermal anomalies occurring late. Maxillofacial management was required because of the critical esthetic and functional implications.
authors.affiliation: Service de chirurgie maxillo-faciale, Hôpital Roger-Salengro, CHRU Lille.
authors.forename: B
authors.initials: B
authors.lastname: Ruhin
authors.forename: P F
authors.initials: PF
authors.lastname: Gentile
authors.forename: C
authors.initials: C
authors.lastname: Rose
authors.forename: A
authors.initials: A
authors.lastname: Leclercq
authors.forename: J
authors.initials: J
authors.lastname: Ferri
mesh_terms: D000328:Adult; D001859:Bone Neoplasms / Q000601:surgery*; D004475:Ectoderm / Q000473:pathology; D004707:Endoderm / Q000473:pathology; D004954:Esthetics; D005147:Facial Bones / Q000601:surgery*; D005736:Gardner Syndrome / Q000601:surgery*; D006801:Humans; D008297:Male; D008339:Mandibular Neoplasms / Q000601:surgery*; D008648:Mesoderm / Q000473:pathology; D010016:Osteoma / Q000601:surgery*; D011379:Prognosis