Tessier type VI-VII cleft combination associated with congenital bimaxillary fusion and anophthalmia.
Congenital intermaxillary fusion is a rare anomaly. Combination of the anomaly with any type of facial cleft is extremely rare. Death in a majority of these patients as a result of feeding and aspiration problems in early life may have caused the reports to be limited. In this article a 5-year-old patient, probably the first in the literature having Tessier type VI-VII facial cleft combination associated with bimaxillary fusion and anophthalmia on the right side, is presented. The patient has survived on fluid meal through a very small opening for 5 years. The features of the case are presented, and the time and method of the management of such a rare anomaly are discussed with a review of the literature.
Cek
D I
DI
Department of Plastic and Reconstructive Surgery, Vakif Gureba State Hospital, Istanbul, Turkey.
Güvenç
B H
BH
Uzunismail
A
A
Günay
Y
Y
D000015:Abnormalities, Multiple / Q000601:surgery; D000853:Anophthalmos / Q000150:complications / Q000601:surgery; D019465:Craniofacial Abnormalities / Q000601:surgery*; D005146:Facial Asymmetry / Q000209:etiology / Q000601:surgery*; D005147:Facial Bones / Q000002:abnormalities* / Q000601:surgery; D005260:Female; D006801:Humans; D007223:Infant; D007569:Jaw Abnormalities / Q000150:complications / Q000601:surgery*; D013704:Temporomandibular Joint / Q000503:physiopathology