[Gardner syndrome. Maxillofacial management of an extremely advanced form].
Gardner's syndrome is a very rare hereditary disease resulting from an embryo genesis disorder involving all three ectodermal, mesodermal and endodermal layers. Generally non-digestive tract signs disclose the syndrome. Underlying silent digestive anomalies should be investigated. Endodermal anomalies may have a fundamental effect on prognosis. Manifestations in our case were severe, with ectodermal and mesodermal anomalies occurring late. Maxillofacial management was required because of the critical esthetic and functional implications.
Ruhin
B
B
Service de chirurgie maxillo-faciale, Hôpital Roger-Salengro, CHRU Lille.
Gentile
P F
PF
Rose
C
C
Leclercq
A
A
Ferri
J
J
D000328:Adult; D001859:Bone Neoplasms / Q000601:surgery*; D004475:Ectoderm / Q000473:pathology; D004707:Endoderm / Q000473:pathology; D004954:Esthetics; D005147:Facial Bones / Q000601:surgery*; D005736:Gardner Syndrome / Q000601:surgery*; D006801:Humans; D008297:Male; D008339:Mandibular Neoplasms / Q000601:surgery*; D008648:Mesoderm / Q000473:pathology; D010016:Osteoma / Q000601:surgery*; D011379:Prognosis