An unusual type of combined aortic coarctation due to fibromuscular dysplasia.
A 3-year-old patient is described with an unusual form of co-arctation due to hypoplasia of the transverse arch and fibromuscular dysplasia involving a long segment of the thoracic aorta. Surgical repair required resection of the aorta from the distal transverse arch to the mid-descending thoracic aorta, and replacement with a 16-mm Dacron interposition graft. This case demonstrates the importance of preoperative evaluation of the entire aorta in the presence of co-arctation due to fibromuscular dysplasia.
Suarez
W A
WA
Department of Pediatrics, Medical College of Ohio, Toledo 43614-5809, USA.
Kurczynski
T W
TW
Bove
E L
EL
D001017:Aortic Coarctation / Q000209:etiology*; D019917:Blood Vessel Prosthesis Implantation; D002675:Child, Preschool; D005260:Female; D005352:Fibromuscular Dysplasia / Q000150:complications*; D006801:Humans