Parry-Romberg syndrome with contralateral and ipsilateral extremity involvement.
BACKGROUND
The Parry-Romberg syndrome is an acquired progressive hemifacial atrophy involving the subcutaneous tissues of the scalp and face. Involvement of the extremities is uncommon in this syndrome.


OBJECTIVE
A case of contralateral and ipsilateral extremity involvement in the Parry-Romberg syndrome is reported, and the difficulties in distinguishing this syndrome from linear scleroderma en coup de sabre are reviewed.


METHODS
A MEDLINE search for cases of Parry-Romberg syndrome with contralateral extremity involvement was performed and the cases reviewed.


RESULTS
Contralateral extremity involvement in the Parry-Romberg syndrome is rare.


CONCLUSIONS
This may be the first case reported in the English literature of Parry-Romberg syndrome with contralateral and ipsilateral extremity involvement.
Chapman
M S
MS
Section of Dermatology, Department of Medicine, Dartmouth-Hitchcock Medical Center, Lebanon, New Hampshire 03756, USA.
Peraza
J E
JE
Spencer
S K
SK
D000273:Adipose Tissue / Q000473:pathology; D005121:Extremities; D005150:Facial Hemiatrophy / Q000150:complications; D005260:Female; D006801:Humans; D008875:Middle Aged; D012535:Scalp / Q000473:pathology; D013577:Syndrome