Inflammatory pseudotumor of the liver in Kostmann's disease.
A case in which inflammatory pseudotumor of the liver (IPTL) seemed to complicate severe congenital neutropenia (Kostmann's disease) is reported. IPTL is a rare entity, especially in childhood. The exact etiology of this lesion is unknown, but it is generally regarded as a benign, reactive inflammatory condition. Based on 15 reported pediatric cases in the literature, the causes, diagnosis, and treatment of IPTL are discussed.
Hsiao
C C
CC
Department of Pediatric Hematology and Oncology, Chang Gung Children's Hospital, Kaohsiung, 123, Ta-Pei Road, Niao-Sung Hsiang, Kaohsiung, 833, Taiwan, Republic of China.
Chen
C L
CL
Eng
H L
HL
D002675:Child, Preschool; D005260:Female; D006104:Granuloma, Plasma Cell / Q000150:complications* / Q000473:pathology; D006801:Humans; D008099:Liver / Q000473:pathology; D008107:Liver Diseases / Q000150:complications* / Q000473:pathology; D009503:Neutropenia / Q000151:congenital*; D013577:Syndrome