Familial pulmonary hypoplasia: plain film appearances with histopathological correlation.
Familial pulmonary hypoplasia is a rare cause of bilateral pulmonary hypoplasia. We describe the plain film appearances and correlate these with the histopathological findings in an infant who survived 5 weeks. In this case, improved technology prolonged survival, allowing the radiological appearance of the primitive lung architecture to become more clearly defined.
Green
R A
RA
Department of Radiology, Great Ormond Street Hospital for Children NHS Trust, Great Ormond Street, London WC1 3JH, UK.
Shaw
D G
DG
Haworth
S G
SG
D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008168:Lung / Q000002:abnormalities* / Q000000981:diagnostic imaging; D008171:Lung Diseases / Q000000981:diagnostic imaging* / Q000235:genetics / Q000473:pathology*; D013902:Radiography, Thoracic