title: Familial pulmonary hypoplasia: plain film appearances with histopathological correlation.
abstract: Familial pulmonary hypoplasia is a rare cause of bilateral pulmonary hypoplasia. We describe the plain film appearances and correlate these with the histopathological findings in an infant who survived 5 weeks. In this case, improved technology prolonged survival, allowing the radiological appearance of the primitive lung architecture to become more clearly defined.
authors.affiliation: Department of Radiology, Great Ormond Street Hospital for Children NHS Trust, Great Ormond Street, London WC1 3JH, UK.
authors.forename: R A
authors.initials: RA
authors.lastname: Green
authors.forename: D G
authors.initials: DG
authors.lastname: Shaw
authors.forename: S G
authors.initials: SG
authors.lastname: Haworth
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008168:Lung / Q000002:abnormalities* / Q000000981:diagnostic imaging; D008171:Lung Diseases / Q000000981:diagnostic imaging* / Q000235:genetics / Q000473:pathology*; D013902:Radiography, Thoracic