Anaesthetic implications of rigid spine syndrome.
The perioperative management of a 14-year-old girl, suffering from the muscular disorder rigid spine syndrome, is presented. The anaesthetic implications with regard to possible difficult intubation, cardiac involvement, malignant hyperthermia, neuromuscular blocking agents, and postoperative recovery are discussed.
Jorgensen
B G
BG
Department of Anaesthesia, Center of Head and Orthopaedics and Respiratory Center East, Copenhagen University Hospital, Righospitalet, Copenhagen, Denmark.
Laub
M
M
Knudsen
R H
RH
D000293:Adolescent; D000768:Anesthesia, General; D018685:Anesthetics, Inhalation / Q000008:administration & dosage; D018686:Anesthetics, Intravenous / Q000008:administration & dosage; D003286:Contracture / Q000503:physiopathology*; D005260:Female; D005283:Fentanyl / Q000008:administration & dosage; D006801:Humans; D007442:Intubation, Intratracheal; D007530:Isoflurane / Q000008:administration & dosage; D008439:Maxillary Diseases / Q000601:surgery; D018908:Muscle Weakness / Q000503:physiopathology*; D009133:Muscular Atrophy / Q000503:physiopathology*; D009609:Nitrous Oxide / Q000008:administration & dosage; D010100:Oxygen / Q000008:administration & dosage; D010159:Palate / Q000601:surgery; D010608:Pharyngeal Diseases / Q000601:surgery; D015742:Propofol / Q000008:administration & dosage; D012600:Scoliosis / Q000503:physiopathology*; D013122:Spinal Diseases / Q000503:physiopathology*; D013577:Syndrome
D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D007530:Isoflurane; D009609:Nitrous Oxide; D010100:Oxygen; D005283:Fentanyl; D015742:Propofol