Anaesthetic management of patients with mucopolysaccharidosis IV presenting for major orthopaedic surgery.
Mucopolysaccharidosis IV, also known as Morquio-Brailsford syndrome, is an inherited autosomal recessive disorder of mucopolysaccharide metabolism leading to accumulation of keratan sulphate in the connective tissue of multiple organ systems. Based on a case report, the anaesthetic implications for the treatment of patients with MPS IV presenting for major orthopaedic surgery are discussed.
Department of Anaesthesiology, University Hospital Eppendorf, Hamburg, Germany.
H J
HJ
Bartz
L
L
Wiesner
F
F
Wappler
D000758:Anesthesia / Q000379:methods*; D002648:Child; D006801:Humans; D008297:Male; D009085:Mucopolysaccharidosis IV; D009985:Orthopedics