Rapid onset of pulmonary arteriovenous malformations after cavopulmonary anastomosis.
The reported incidence of pulmonary arteriovenous malformations after superior cavopulmonary anastamosis in patients with heterotaxia syndrome is 18%-21%. The manifestation is usually in young children and the onset is gradual. We report an unusual case of pulmonary arteriovenous malformations developing within 72 hours of bilateral superior cavopulmonary anastamosis (Kawashima procedure) in an adolescent with heterotaxia syndrome.
Institute of Cardiovascular Diseases, Madras Medical Mission, India.
U M
UM
Pandurangi
M J
MJ
Shah
R
R
Murali
K M
KM
Cherian
D000293:Adolescent; D000714:Anastomosis, Surgical / Q000009:adverse effects; D001165:Arteriovenous Malformations / Q000209:etiology*; D005260:Female; D006330:Heart Defects, Congenital / Q000601:surgery; D006801:Humans; D011183:Postoperative Complications; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery*; D011667:Pulmonary Veins / Q000002:abnormalities*; D014683:Vena Cava, Superior / Q000601:surgery*