[Respiratory failure in mitochondrial myopathy treated with noninvasive mechanical ventilation].
Young man suffering from mitochondrial myopathy was admitted to our Institute due to severe hypercapnic respiratory failure. Noninvasive mechanical ventilation (NWM) during sleep using nasal mask was instituted with positive results. Diurnal blood gases breathing air also ameliorated suggesting improvement of respiratory muscles function.
Kliniki Chorób Płuc Instytutu Gruźlicy i Chorób Płuc w Warszawie.
P
P
Bieleń
P
P
Sliwiński
D
D
Kamiński
J
J
Zieliński
D000328:Adult; D001707:Biopsy, Needle; D006801:Humans; D008297:Male; D017240:Mitochondrial Myopathies / Q000150:complications* / Q000473:pathology; D018482:Muscle, Skeletal / Q000473:pathology; D010092:Oximetry; D012121:Respiration, Artificial; D012131:Respiratory Insufficiency / Q000209:etiology* / Q000378:metabolism / Q000628:therapy*; D012132:Respiratory Muscles / Q000378:metabolism; D016896:Treatment Outcome
Niewydolność oddychania w przebiegu miopatii mitochondrialnej skutecznie leczona nieinwazyjnym wspomaganiem wentylacji.