title: Cochlear implantation for symptomatic hereditary deafness.
abstract: Recently, the effectiveness of cochlear implantation for hereditary deafness has been reported. We performed cochlear implantation for two patients with symptomatic hereditary deafness. Deafness in one patient was thought to be a result of albinism-deafness syndrome and in the other patient, a result of chronic progressive external ophthalmoplegia syndrome. Since their speech perception abilities improved dramatically, we believe that cochlear implantation should be actively performed for these two syndromes.
authors.affiliation: Department of Otorhinolaryngology, Okayama University Medical School, Japan. nishizak@cc.okayama-u.ac.jp
authors.forename: K
authors.initials: K
authors.lastname: Nishizaki
authors.forename: K
authors.initials: K
authors.lastname: Fukushiama
authors.forename: Y
authors.initials: Y
authors.lastname: Oda
authors.forename: A
authors.initials: A
authors.lastname: Masuda
authors.forename: S
authors.initials: S
authors.lastname: Hayashi
authors.forename: N
authors.initials: N
authors.lastname: Nagayasu
authors.forename: T
authors.initials: T
authors.lastname: Yoshino
authors.forename: K
authors.initials: K
authors.lastname: Kashihara
authors.forename: K
authors.initials: K
authors.lastname: Takahashi
authors.forename: Y
authors.initials: Y
authors.lastname: Masuda
mesh_terms: D000328:Adult; D016115:Albinism, Oculocutaneous / Q000235:genetics; D019929:Cochlear Implantation; D003638:Deafness / Q000235:genetics* / Q000534:rehabilitation*; D006801:Humans; D008297:Male; D017246:Ophthalmoplegia, Chronic Progressive External / Q000235:genetics; D013577:Syndrome