title: Tracheal intubation in a child with trismus pseudocamptodactyly (Hecht) syndrome.
abstract: Tracheal intubation of a child with trismus pseudocamptodactyly (Hecht) syndrome is described. This disorder is characterized by progressive trismus and the need for repeated surgeries. Children intubated orally on a prior occasion may require an alternative approach subsequently due to progressive inability to open the mouth. An antegrade fiberoptic-guided nasotracheal technique initially was chosen due to extremely limited mouth opening. After this approach was unsuccessful, a retrograde guidewire-assisted fiberoptic intubation was performed. The manifestations of Hecht syndrome, as well as both techniques for tracheal intubation employed, are reviewed.
authors.affiliation: Department of Anesthesiology, Stanford University Medical Center, CA 94305, USA.
authors.forename: J
authors.initials: J
authors.lastname: Seavello
authors.forename: G B
authors.initials: GB
authors.lastname: Hammer
mesh_terms: D002648:Child; D019465:Craniofacial Abnormalities / Q000601:surgery*; D018450:Disease Progression; D005336:Fiber Optic Technology; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods; D008297:Male; D013577:Syndrome; D014313:Trismus / Q000601:surgery*