title: Portal vein thrombosis after splenectomy for hereditary stomatocytosis in childhood.
abstract: Portal vein thrombosis is a rare but potentially lethal complication in children requiring splenectomy. We report on a 15-year-old boy with a dehydrated hereditary stomatocytosis, who underwent splenectomy and presented a postoperative partial portal vein thrombosis. With prompt heparin therapy, neither propagation of the thrombus nor further cavernous transformation in the following occurred 6 years.
  
  
  CONCLUSIONS
  Recent data suggest that hereditary stomatocytosis carries a high risk of thrombotic complications, especially after splenectomy. This procedure, the benefit of which is limited in this condition, should therefore be strongly avoided.
authors.affiliation: Unité d'Onco-Hematologie Pediatrique, Hopital des Enfants, Centre Hospitalier et Universitaire de Bordeaux, France. yves.perel@chu-aquitaine.fr
authors.forename: Y
authors.initials: Y
authors.lastname: Perel
authors.forename: D
authors.initials: D
authors.lastname: Dhermy
authors.forename: A
authors.initials: A
authors.lastname: Carrere
authors.forename: J F
authors.initials: JF
authors.lastname: Chateil
authors.forename: J M
authors.initials: JM
authors.lastname: Bondonny
authors.forename: M
authors.initials: M
authors.lastname: Micheau
authors.forename: R
authors.initials: R
authors.lastname: Barbier
mesh_terms: D000293:Adolescent; D000745:Anemia, Hemolytic, Congenital / Q000601:surgery*; D006801:Humans; D008297:Male; D011169:Portal Vein; D013156:Splenectomy / Q000009:adverse effects*; D013927:Thrombosis / Q000209:etiology*