[Behçet disease in children. 3 Tunisian cases and review of the literature].
OBJECTIVE
To describe epidemiological, clinical and evolutive features of ophthalmological involvment of Behçet disease in children in tunisian patients.


METHODS
In a retrospective study from 1990 to 1996, we collected three observations in children in 130 recorded cases of Behçet disease. Patients have been explored by a complete ophthalmologic staging and are treated and followed in our institution for theirs oculars problems.


RESULTS
The three children, all males, aged from 12 to 13 years, represented 2.3% of all the Behçet disease diagnosed during the same period. Oral and/or genital aphtosis are present in all 3 cases and cutaneous or articular involvement is seen in 2 patients. Ocular Behçet disease involvement, bilateral in all the cases, is dominated by uveitis (posterior in 3 patients or anterior in 2) complicated by macular edema in 3 cases and cataract or pseudo-trou in 1 case.


CONCLUSIONS
Behçet disease in children is characterized by the frequency of familial forms and articular involvement. The most characteristic ocular feature is represented by the posterior uveitis with a visual prognosis poor in short term. Specific criteria of Behçet disease is necessary for children for a early and best identification.
Mili-Boussen
I
I
Service d'ophtalmologie, Pr A. Ouertani, Hôpital Charles Nicolle, Tunis, Tunisie.
Kriaa
L
L
Anane
R
R
Marrakchi
I
I
Ouertani
A
A
D000293:Adolescent; D001528:Behcet Syndrome / Q000235:genetics / Q000473:pathology / Q000503:physiopathology*; D002648:Child; D006801:Humans; D008297:Male; D012189:Retrospective Studies; D014416:Tunisia
La maladie de Behçet de l'enfant. A propos de 3 observations tunisiennes et revue de la littérature.