title: Cholesteatoma in a child with congenital ichthyosiform erythroderma.
abstract: A 7-year-old girl had non-bullous congenital ichthyosiform erythroderma (NBCIE) in treatment with retinoids. She also suffered continuous desquamation of the external ears, recurrent external otitis, chronic adenoiditis, tubaric dysfunction and intermittent episodes of otitis media and developed a cholesteatoma in her left ear. Chronic scaling disorders, such as NBCIE and other ichthyosis, can be entities at risk for the development of cholesteatoma in childhood.
authors.affiliation: Department of Pediatric Otolaryngology, Hospital del Niño Jesús, Madrid, Spain.
authors.forename: M
authors.initials: M
authors.lastname: Bartolomé
authors.forename: A
authors.initials: A
authors.lastname: Torrelo
authors.forename: E
authors.initials: E
authors.lastname: Molina
authors.forename: A
authors.initials: A
authors.lastname: Zambrano
mesh_terms: D002648:Child; D018424:Cholesteatoma, Middle Ear / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D005260:Female; D006801:Humans; D016113:Ichthyosiform Erythroderma, Congenital / Q000150:complications* / Q000175:diagnosis; D009336:Necrosis; D010032:Otitis Externa / Q000150:complications; D012008:Recurrence; D014057:Tomography, X-Ray Computed; D014432:Tympanic Membrane / Q000473:pathology / Q000601:surgery; D014433:Tympanoplasty