Dynamic left ventricular arterial pressure gradient and sick sinus syndrome with heterozygous Fabry's disease improved following implantation of a dual chamber pacemaker.
A 63-year-old woman with heterozygous Fabry's disease, sick sinus syndrome, sinus pauses, congestive heart failure, syncope, and a dynamic pressure gradient between the left ventricle and systemic arteries underwent implantation of a dual chamber (DDD) pacemaker. Following pacemaker implantation, the pressure gradient has been reduced and congestive heart failure controlled for the past 3 years.
Nakayama
Y
Y
Department of Cardiology, Ishikiriseiki Hospital, Osaka, Higashiosaka-City, Japan.
Tsumura
K
K
Yamashita
N
N
Yoshimaru
K
K
D001794:Blood Pressure / Q000502:physiology*; D004452:Echocardiography; D000795:Fabry Disease / Q000235:genetics* / Q000503:physiopathology / Q000628:therapy; D005260:Female; D005500:Follow-Up Studies; D006333:Heart Failure / Q000235:genetics / Q000503:physiopathology / Q000628:therapy; D006579:Heterozygote; D006801:Humans; D008875:Middle Aged; D010138:Pacemaker, Artificial; D012804:Sick Sinus Syndrome / Q000235:genetics* / Q000503:physiopathology / Q000628:therapy; D016277:Ventricular Function, Left / Q000502:physiology*