title: Immune-deficient bronchiectasis associated with X-linked lymphoproliferative disease.
abstract: Bronchiectasis may occur with various congenital and acquired immunodeficiency diseases. The association of bronchiectasis and the X-linked lymphoproliferative disease (XLP), also known as Duncan's disease is unknown. We describe the case of a 39-year-old man with XLP, the oldest surviving, who developed chronic bronchiectasis with hemoptysis and required a pneumonectomy to control his symptoms.
authors.affiliation: Division of Cardiothoracic Surgery, University of Illinois at Chicago, 60612, USA.
authors.forename: V K
authors.initials: VK
authors.lastname: Mehta
authors.forename: M G
authors.initials: MG
authors.lastname: Massad
authors.forename: S P
authors.initials: SP
authors.lastname: Tripathi
authors.forename: M
authors.initials: M
authors.lastname: Koshy
authors.forename: A S
authors.initials: AS
authors.lastname: Geha
mesh_terms: D000328:Adult; D001987:Bronchiectasis / Q000235:genetics* / Q000276:immunology / Q000601:surgery; D006469:Hemoptysis / Q000235:genetics / Q000276:immunology / Q000601:surgery; D004854:Herpesvirus 4, Human / Q000276:immunology; D006801:Humans; D008232:Lymphoproliferative Disorders / Q000235:genetics* / Q000276:immunology / Q000601:surgery; D008297:Male; D011013:Pneumonectomy; D014057:Tomography, X-Ray Computed