Immune-deficient bronchiectasis associated with X-linked lymphoproliferative disease.
Bronchiectasis may occur with various congenital and acquired immunodeficiency diseases. The association of bronchiectasis and the X-linked lymphoproliferative disease (XLP), also known as Duncan's disease is unknown. We describe the case of a 39-year-old man with XLP, the oldest surviving, who developed chronic bronchiectasis with hemoptysis and required a pneumonectomy to control his symptoms.
Mehta
V K
VK
Division of Cardiothoracic Surgery, University of Illinois at Chicago, 60612, USA.
Massad
M G
MG
Tripathi
S P
SP
Koshy
M
M
Geha
A S
AS
D000328:Adult; D001987:Bronchiectasis / Q000235:genetics* / Q000276:immunology / Q000601:surgery; D006469:Hemoptysis / Q000235:genetics / Q000276:immunology / Q000601:surgery; D004854:Herpesvirus 4, Human / Q000276:immunology; D006801:Humans; D008232:Lymphoproliferative Disorders / Q000235:genetics* / Q000276:immunology / Q000601:surgery; D008297:Male; D011013:Pneumonectomy; D014057:Tomography, X-Ray Computed