Ehlers-Danlos syndrome associated with multiple spinal meningeal cysts--case report.
A 40-year-old female with Ehlers-Danlos syndrome was admitted because of a large pelvic mass. Radiological examination revealed multiple spinal meningeal cysts. The first operation through a laminectomy revealed that the cysts originated from dilated dural sleeves containing nerve roots. Packing of dilated sleeves was inadequate. Finally the cysts were oversewed through a laparotomy. The cysts were reduced, but the postoperative course was complicated by poor wound healing and diffuse muscle atrophy. Ehlers-Danlos syndrome associated with spinal cysts may be best treated by endoscopic surgery.
Isono
M
M
Department of Neurosurgery, Oita Medical University.
Hori
S
S
Konishi
Y
Y
Kinjo
H
H
Kakisako
K
K
Hirose
R
R
Yoshida
T
T
D000328:Adult; D003560:Cysts / Q000150:complications* / Q000175:diagnosis / Q000601:surgery*; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000601:surgery; D005260:Female; D006801:Humans; D007796:Laminectomy; D008279:Magnetic Resonance Imaging; D008578:Meninges / Q000000981:diagnostic imaging / Q000473:pathology; D017699:Pelvic Pain / Q000209:etiology; D012086:Reoperation; D013118:Spinal Cord Diseases / Q000150:complications*; D013168:Spondylolisthesis / Q000150:complications; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome