Malignant peripheral nerve sheath tumour in the maxilla associated with von Recklinghausen's disease.
Malignant transformation of neurofibromatosis is one of the most serious complications of von Recklinghausen's disease (VRD). The most common associated malignancy is the malignant peripheral nerve sheath tumour (MPNST). Few cases of MPNST associated with VRD in the maxillary region have been reported. This report describes a rare case of MPNST in the maxilla and the aggressive nature of MPNST associated with VRD.
Muraki
Y
Y
First Department of Oral and Maxillofacial Surgery, Kyushu Dental College, 2-6-1 Manazuru, Kokurakita-ku, Kitakyushu 803.
Tateishi
A
A
Tominaga
K
K
Fukuda
J
J
Haneji
T
T
Iwata
Y
Y
D000328:Adult; D017809:Fatal Outcome; D006801:Humans; D008297:Male; D008441:Maxillary Neoplasms / Q000150:complications* / Q000473:pathology; D009361:Neoplasm Invasiveness; D009364:Neoplasm Recurrence, Local; D018317:Nerve Sheath Neoplasms / Q000209:etiology* / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000150:complications*