title: A patient-benefit evaluation of unilateral congenital conductive hearing loss presenting in adulthood: should it be repaired?
abstract: OBJECTIVE
  To evaluate subjective and objective outcomes of surgical therapy in congenital conductive hearing loss (HL) presenting in adulthood. The impact of hearing restoration on quality of life (QOL) for these patients may differ from those with acquired HL.
  
  
  METHODS
  Retrospective review of five patients treated surgically.
  
  
  METHODS
  Standard audiometry was completed. Patients completed a subjective questionnaire as well as subjective (open-set) questions. A seven-point Likert scale was used for closed-set responses with 1 representing the worst possible outcome and 7 being best.
  
  
  RESULTS
  The average four-frequency improvements in pure-tone average and air-bone gap were 18 dB (range, 7-29 dB) and 16 dB (range, 2-30 dB), respectively. An average score was obtained for each closed-set question. The highest-scoring items were for overall improvement of QOL (average score, 6), followed by perceived improvement in hearing (average score, 5.6). Other positive responses were improved ability to use the telephone (four of five patients) and improved localization of sound (four of five patients). Negative subjective responses included prolonged dysequilibrium in two of five, prolonged adjustment period in three, and dysgeusia in one patient.
  
  
  CONCLUSIONS
  Important components of outcome are likely to escape our review if only objective measures are used to evaluate surgical outcomes. These results suggest that improved hearing in this population provides specific improvements in lifestyle and is perceived as a significant improvement in overall QOL.
authors.affiliation: Department of Otolaryngology, SUNY Health Science Center, Brooklyn 11203, USA.
authors.forename: N M
authors.initials: NM
authors.lastname: Sperling
authors.forename: N
authors.initials: N
authors.lastname: Patel
mesh_terms: D000328:Adult; D001299:Audiometry; D005260:Female; D006314:Hearing Loss, Conductive / Q000151:congenital* / Q000523:psychology / Q000601:surgery*; D006801:Humans; D008019:Life Style; D008297:Male; D008875:Middle Aged; D017060:Patient Satisfaction; D011788:Quality of Life; D016896:Treatment Outcome