Adult primitive neuroectodermal tumour. A case report and review of the literature.
A 19-year-old woman presented with left-sided sensorineural hearing loss. She was found to have a left cerebellopontine angle tumour, thought to be an acoustic neuroma on MRI, and was treated with radiosurgery. There was no evidence of tumour on MRI at 6 months. After 1 year, she was admitted with further neurological symptoms. Repeat MRI showed multiple craniospinal tumours. Biopsy of the cerebellar tumour revealed it to be a primitive neuroectodermal tumour (PNET). This is a rare tumour in this age group and its management is discussed.
Tripathy
L N
LN
Department of Neurosurgery, Royal Hallamshire Hospital, Sheffield, UK.
Forster
D M
DM
Timperley
W R
WR
D000328:Adult; D002528:Cerebellar Neoplasms / Q000175:diagnosis / Q000601:surgery*; D002530:Cerebellopontine Angle; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D018242:Neuroectodermal Tumors, Primitive / Q000175:diagnosis / Q000601:surgery*