title: Glycogen storage disease and von Willebrand's disease implications for dental treatment: dental management of a pediatric patient.
abstract: Glycogen storage diseases (GSD) are metabolic disorders which impair the body's ability to store glucose and utilize it later, requiring patients to take multiple daily dietary supplementation with a high carbohydrate content. Patients undergoing this treatment modality are placed at increased risk for gross dental caries and other oral abnormalities. Additionally, GSD may prolong the patient's bleeding time, which may necessitate consultation with the treating physician. In the following case, our patient required a multidisciplinary approach to address not only her dental needs, but also to coordinate the management of both her GSD and an additional complication, von Willebrand's disease. This was best achieved in a hospital setting.
authors.affiliation: Restorative Dentistry Department, University of Mississippi School of Dentistry, Jackson 39216, USA.
authors.forename: T M
authors.initials: TM
authors.lastname: Dellinger
authors.forename: H M
authors.initials: HM
authors.lastname: Livingston
authors.forename: R
authors.initials: R
authors.lastname: Holder
authors.forename: C F
authors.initials: CF
authors.lastname: Streckfus
mesh_terms: D002675:Child, Preschool; D017742:Dental Care for Chronically Ill; D003731:Dental Caries / Q000209:etiology / Q000628:therapy; D003796:Dental Service, Hospital; D005260:Female; D006008:Glycogen Storage Disease / Q000150:complications; D006801:Humans; D014842:von Willebrand Diseases / Q000150:complications