New-onset headache in an adolescent with MASS syndrome.
A 15-year-old girl with the "MASS" phenotype (meeting several of the minor criteria for Marfan syndrome) presents with a new onset low-pressure postural headache. Clinical features and magnetic resonance imaging suggested intracranial hypotension, which was confirmed with lumbar puncture. The pathophysiology and treatment of spontaneous intracranial hypotension are discussed.
Deputy
S R
SR
Department of Neurology, Louisiana State University, New Orleans, USA.
Tilton
A H
AH
D000293:Adolescent; D001018:Aortic Diseases / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D017217:Blood Patch, Epidural; D001847:Bone Diseases / Q000150:complications* / Q000175:diagnosis; D001921:Brain / Q000000981:diagnostic imaging / Q000473:pathology; D004108:Dilatation, Pathologic; D005260:Female; D006261:Headache / Q000150:complications* / Q000175:diagnosis* / Q000628:therapy; D006801:Humans; D019585:Intracranial Hypotension / Q000175:diagnosis / Q000188:drug therapy; D008279:Magnetic Resonance Imaging; D008945:Mitral Valve Prolapse / Q000150:complications* / Q000175:diagnosis; D009192:Myelography; D009216:Myopia / Q000150:complications* / Q000175:diagnosis; D011187:Posture; D012871:Skin Diseases / Q000150:complications* / Q000175:diagnosis; D013126:Spinal Nerve Roots / Q000000981:diagnostic imaging; D013129:Spinal Puncture; D013577:Syndrome; D014057:Tomography, X-Ray Computed