The syndrome of pericarditis, arthritis, and camptodactyly: an under-recognized cause of pericardial constriction in children?
The syndrome encompassing the combination of pericarditis, arthritis, and camptodactyly is a rarely described cause of pericardial constriction in children. It is likely that this association is being under-recognized. We report a new case in which the skeletal abnormalities were subtle. The syndrome should be included in the differential diagnosis of any child with persistent non-inflammatory pericardial effusion. A careful search at the bedside for the associated skeletal abnormalities should lead to the correct diagnosis. Pericardiectomy is the treatment of choice.
Buendía
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Instituto Nacional de Cardiología Ignacio Chávez, Mexico.
Attié
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Martínez-Lavín
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D001168:Arthritis / Q000150:complications*; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005384:Finger Joint / Q000503:physiopathology*; D006801:Humans; D008297:Male; D010494:Pericarditis, Constrictive / Q000150:complications*; D013577:Syndrome