Right heart failure as the dominant clinical picture in a case of primary amyloidosis affecting the pulmonary vasculature.
A 91-year-old female patient died of right heart failure and pulmonary hypertension. The autopsy revealed multi-organ vascular amyloidosis and pulmonary alveolar septal amyloidosis with no evidence of parenchymal myocardial amyloid deposition. This is a rare example of cor pulmonale secondary to pulmonary amyloidosis.
Chapman
A D
AD
Department of Pathology, Aberdeen Royal Infirmary, Foresterhill. a.d.chapman@abdn.ac.uk
Brown
P A
PA
Kerr
K M
KM
D000368:Aged; D000369:Aged, 80 and over; D000686:Amyloidosis / Q000150:complications* / Q000473:pathology*; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications*; D011660:Pulmonary Heart Disease / Q000209:etiology* / Q000473:pathology; D018497:Ventricular Dysfunction, Right / Q000473:pathology*