Congenital malignant rhabdoid tumor of the orbit.
Malignant rhabdoid tumor is a rare and highly malignant renal tumor of infancy. Extrarenal tumors involving the orbit have been reported, but never at birth. The authors describe a primary malignant rhabdoid tumor of the orbit in a neonate who had massive unilateral proptosis at birth. Clinical, radiographic, and histologic features of the tumor are discussed.
Stidham
D B
DB
Indiana University School of Medicine, Department of Ophthalmology, Indianapolis, USA. bstidham@eye.med.uth.tmc.edu
Burgett
R A
RA
Davis
M M
MM
Plager
D A
DA
D001706:Biopsy; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D005094:Exophthalmos / Q000473:pathology; D006801:Humans; D007223:Infant; D008297:Male; D009918:Orbital Neoplasms / Q000151:congenital* / Q000000981:diagnostic imaging / Q000473:pathology; D018335:Rhabdoid Tumor / Q000151:congenital* / Q000000981:diagnostic imaging / Q000473:pathology; D014057:Tomography, X-Ray Computed