[Multifocal malignant transformation of extreme fibromatosis with pulmonary involvement].
We report on the case of a 40-year old patient with extreme neurofibromatosis with severe kyphoskoliosis and deformation of the thorax. The patient died from malignant transformation which occurred multifocally with extensive pulmonary metastases. The well-known thoracic manifestations of neurofibromatosis are reviewed.
Hummel
B
B
Klinik für Innere Medizin, Städtisches Klinikum Dessau.
Schumann
H J
HJ
Hofmann
B
B
Baumgärtel
S
S
Rosahl
W
W
Schreiber
J
J
D000328:Adult; D002471:Cell Transformation, Neoplastic; D017809:Fatal Outcome; D006801:Humans; D007738:Kyphosis / Q000150:complications / Q000000981:diagnostic imaging; D008175:Lung Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000556:secondary*; D008297:Male; D017253:Neurofibromatoses / Q000000981:diagnostic imaging* / Q000473:pathology; D012600:Scoliosis / Q000150:complications / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed