Bilateral proptosis: an unusual presentation of fibrous dysplasia.
Fibrous dysplasia is a benign, developmental bone disorder of unknown aetiology. With involvement of the facial bones, indications for surgical intervention include cosmetic deformity and/or progressive neurological dysfunction. We present the case of a 36-year-old female with bilateral orbital lesions whose initial presentation was that of progressive proptosis and visual loss. She underwent bilateral pterional craniotomies with gross total resection of her tumours. Review of the literature reveals several cases of unilateral orbital fibrous dysplasia. This appears to be the first reported case of distinct, bilateral orbital fibrous dysplasia.
Horgan
M A
MA
Division of Neurosurgery, Oregon Health Sciences University, Portland 97201, USA.
Delashaw
J B
JB
Dailey
R A
RA
D000328:Adult; D003399:Craniotomy / Q000379:methods; D005094:Exophthalmos / Q000209:etiology* / Q000601:surgery; D005147:Facial Bones; D005260:Female; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications*; D006801:Humans; D014057:Tomography, X-Ray Computed