title: [Multifocal malignant transformation of extreme fibromatosis with pulmonary involvement].
abstract: We report on the case of a 40-year old patient with extreme neurofibromatosis with severe kyphoskoliosis and deformation of the thorax. The patient died from malignant transformation which occurred multifocally with extensive pulmonary metastases. The well-known thoracic manifestations of neurofibromatosis are reviewed.
authors.affiliation: Klinik für Innere Medizin, Städtisches Klinikum Dessau.
authors.forename: B
authors.initials: B
authors.lastname: Hummel
authors.forename: H J
authors.initials: HJ
authors.lastname: Schumann
authors.forename: B
authors.initials: B
authors.lastname: Hofmann
authors.forename: S
authors.initials: S
authors.lastname: Baumgärtel
authors.forename: W
authors.initials: W
authors.lastname: Rosahl
authors.forename: J
authors.initials: J
authors.lastname: Schreiber
mesh_terms: D000328:Adult; D002471:Cell Transformation, Neoplastic; D017809:Fatal Outcome; D006801:Humans; D007738:Kyphosis / Q000150:complications / Q000000981:diagnostic imaging; D008175:Lung Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000556:secondary*; D008297:Male; D017253:Neurofibromatoses / Q000000981:diagnostic imaging* / Q000473:pathology; D012600:Scoliosis / Q000150:complications / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed