[The current state of substitution treatment in congenital emphysema due to alpha-1-antitrypsin deficiency. The report of the National Registry].
Miravitlles
M
M
Servei de Pneumologia, Hospital Vall d'Hebron, Barcelona.
Vidal
R
R
Barros-Tizón
J C
JC
Bustamante
A
A
España
P P
PP
Casas
F
F
Martínez
M T
MT
Escudero
C
C
Jardí
R
R
D000328:Adult; D000368:Aged; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D010641:Phenotype; D011013:Pneumonectomy; D011656:Pulmonary Emphysema / Q000151:congenital* / Q000235:genetics / Q000628:therapy*; D012042:Registries / Q000706:statistics & numerical data*; D012907:Smoking / Q000009:adverse effects; D013030:Spain; D000515:alpha 1-Antitrypsin / Q000627:therapeutic use; D019896:alpha 1-Antitrypsin Deficiency / Q000151:congenital* / Q000235:genetics / Q000628:therapy*
D000515:alpha 1-Antitrypsin
Estado actual del tratamiento sustitutivo en el enfisema congénito por déficit de alfa-1-antitripsina. Informe del Registro Nacional.