[Hypokalemic quadriplegia with distal tubular acidosis revealing a a case of primary Gougerot-Sjögren syndrome].
BACKGROUND
Primary Sjögren's syndrome is associated in 6 to 25% of cases with kidney involvement Most often it is a chronic interstitial nephritis, generally asymptomatic but sometimes responsible for distal tubular acidosis which can be complicated by severe hypokalemia.


METHODS
A 48-year-old woman had hypokalemic quadriplegia, distal renal tubular acidosis and chronic interstitial nephritis at kidney biopsy. Primary Sjögren's syndrome was diagnosed.


CONCLUSIONS
We discuss briefly the clinical, biological and immunological features of 18 similar cases reported in the literature.
Raynal
C
C
Service de Médecine Interne du Pr Vital Durand, Centre Hospitalier Lyon Sud, Pierre Bénite.
Durupt
S
S
Durieu
I
I
Boudray
C
C
Bouhour
F
F
Levrat
R
R
Vital Durand
D
D
D000141:Acidosis, Renal Tubular / Q000209:etiology*; D005260:Female; D006801:Humans; D007008:Hypokalemia / Q000209:etiology*; D008875:Middle Aged; D011782:Quadriplegia / Q000209:etiology*; D012859:Sjogren's Syndrome / Q000150:complications / Q000175:diagnosis*
Quadriparésie hypokaliémique avec acidose tubulaire distale révélatrice d'un syndrome de Gougerot-Sjögren primaire.