The spine in diastrophic dysplasia. The surgical arthrodesis of thoracic and lumbar deformities in 21 patients.
METHODS
Retrospective chart and radiographic film review.


OBJECTIVE
To discern the deformity problems in diastrophic dysplasia and to report our results in surgical treatment.


BACKGROUND
Due to the rarity of the problem, the literature is very scanty as to the indications for surgery or the best technique.


METHODS
Analysis of radiographic film for scoliosis, kyphosis, lordosis, and decompensation before surgery, after surgery, and at follow-up. Analysis of charts for complications and problems.


RESULTS
The most common deformity pattern was a double thoracic kyphosis (79 degrees/97 degrees) with a true kyphosis at the junction of the two scolioses (101 degrees). Combined anterior-posterior arthrodesis gave the best results.


CONCLUSIONS
Very severe deformity can occur in children with diastrophic dysplasia, even at a young age. Prompt anterior-posterior arthrodesis can prevent catastrophic deformity.
Matsuyama
Y
Y
Department of Orthopaedic Surgery, Nagoya University School of Medicine, Japan.
Winter
R B
RB
Lonstein
J E
JE
D000293:Adolescent; D000328:Adult; D001848:Bone Diseases, Developmental / Q000000981:diagnostic imaging / Q000601:surgery*; D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007738:Kyphosis / Q000000981:diagnostic imaging / Q000601:surgery; D008159:Lumbar Vertebrae / Q000002:abnormalities / Q000601:surgery; D011859:Radiography; D012600:Scoliosis / Q000000981:diagnostic imaging / Q000601:surgery; D013123:Spinal Fusion; D013904:Thoracic Vertebrae / Q000002:abnormalities / Q000601:surgery; D013997:Time Factors; D016896:Treatment Outcome