title: [The current state of substitution treatment in congenital emphysema due to alpha-1-antitrypsin deficiency. The report of the National Registry].
authors.affiliation: Servei de Pneumologia, Hospital Vall d'Hebron, Barcelona.
authors.forename: M
authors.initials: M
authors.lastname: Miravitlles
authors.forename: R
authors.initials: R
authors.lastname: Vidal
authors.forename: J C
authors.initials: JC
authors.lastname: Barros-Tizón
authors.forename: A
authors.initials: A
authors.lastname: Bustamante
authors.forename: P P
authors.initials: PP
authors.lastname: España
authors.forename: F
authors.initials: F
authors.lastname: Casas
authors.forename: M T
authors.initials: MT
authors.lastname: Martínez
authors.forename: C
authors.initials: C
authors.lastname: Escudero
authors.forename: R
authors.initials: R
authors.lastname: Jardí
mesh_terms: D000328:Adult; D000368:Aged; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D010641:Phenotype; D011013:Pneumonectomy; D011656:Pulmonary Emphysema / Q000151:congenital* / Q000235:genetics / Q000628:therapy*; D012042:Registries / Q000706:statistics & numerical data*; D012907:Smoking / Q000009:adverse effects; D013030:Spain; D000515:alpha 1-Antitrypsin / Q000627:therapeutic use; D019896:alpha 1-Antitrypsin Deficiency / Q000151:congenital* / Q000235:genetics / Q000628:therapy*
chemical_list: D000515:alpha 1-Antitrypsin
vernacular_title: Estado actual del tratamiento sustitutivo en el enfisema congénito por déficit de alfa-1-antitripsina. Informe del Registro Nacional.