title: Esophageal atresia: primary repair of a rare long gap variant involving distal pouch mobilization.
abstract: This report describes a rare type IIIb variant of long gap pure esophageal atresia treated with delayed primary repair. Preoperative imaging showed a distal pouch with a unusually long tapering end, and a 5-vertebral body gap. Delayed exploration with mobilization of the distal pouch allowed for successful primary repair without the need of myotomy. The characteristic radiological appearance of this rare variant enables its preoperative recognition and warrants attempting primary repair with a good expectation of success.
authors.affiliation: Department of Surgery, Queen's University, Kingston, Ontario, Canada.
authors.forename: P
authors.initials: P
authors.lastname: Davison
authors.forename: D
authors.initials: D
authors.lastname: Poenaru
authors.forename: I
authors.initials: I
authors.lastname: Kamal
mesh_terms: D000328:Adult; D000714:Anastomosis, Surgical; D004933:Esophageal Atresia / Q000000981:diagnostic imaging / Q000601:surgery*; D005260:Female; D005315:Fetal Diseases / Q000000981:diagnostic imaging; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D007234:Infant, Premature; D007235:Infant, Premature, Diseases / Q000601:surgery; D011247:Pregnancy; D011859:Radiography; D016216:Ultrasonography, Prenatal