Lymphangiectasia within angiomyolipoma in a tuberous sclerosis patient.
This is a presentation of a case of tuberous sclerosis with multifocal hamartomas in the retroperitoneum, both kidneys, and the liver. Lymphangiectasia and numerous ectatic lymphatic channels penetrating through the retroperitoneal angiomyolipoma were demonstrated by lymphography and computed tomography. The findings in our study may document the presence of degenerative change in the lymphatic system--not just in elastic vessels--an association which has not yet been reported in the radiological literature.
Cheung
Y C
YC
Department of Diagnostic Radiology, Chang Gung Medical Center at Linkou, Chang Gung Medical College, Chang Gung University, Taiwan. alex2143@ms33.hinet.net
Ng
S H
SH
Tan
C F
CF
Wong
H F
HF
Wan
Y L
YL
D000328:Adult; D018207:Angiomyolipoma / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000000981:diagnostic imaging; D008113:Liver Neoplasms / Q000000981:diagnostic imaging; D008200:Lymphangiectasis / Q000000981:diagnostic imaging* / Q000209:etiology*; D008220:Lymphography; D009378:Neoplasms, Multiple Primary / Q000000981:diagnostic imaging*; D012186:Retroperitoneal Neoplasms / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed; D014402:Tuberous Sclerosis / Q000150:complications*