title: Hemangioblastoma of the internal acoustic canal in a patient with von Hippel-Lindau disease: a case report and review of the literature.
abstract: We report a case of von Hippel-Lindau disease in a 55-year-old woman who presented with an intracanalicular hemangioblastoma and discuss the otologic manifestations of this disease. A review of the literature revealed no previous reports of this entity originating in the internal acoustic canal.
authors.affiliation: Department of Otolaryngology-Head and Neck Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA.
authors.forename: V A
authors.initials: VA
authors.lastname: Resto
authors.forename: L R
authors.initials: LR
authors.lastname: Lustig
mesh_terms: D004424:Ear Canal; D004428:Ear Neoplasms / Q000209:etiology* / Q000601:surgery; D005260:Female; D018325:Hemangioblastoma / Q000209:etiology* / Q000601:surgery; D006801:Humans; D008875:Middle Aged; D006623:von Hippel-Lindau Disease / Q000150:complications*