[Renal cell carcinoma in a 14-year-old girl with Von Hippel Lindau disease].
We report a new case of renal cancer in the context of Von Hippel Lindau (VHL) disease in a 14-year-old girl. To our knowledge, this is the youngest case reported in the literature. VHL disease is now well known and its prognosis is related to renal cancer, which occurs very early in the patient's life, requiring adequate surveillance of patients carrying the VHL gene to ensure early diagnosis of the cancer, screening of family members and treatment, preferably conservative when permitted by the size and number of tumours, in these patients who are predisposed to developing other renal tumours, in order to delay bilateral nephrectomy and the need for dialysis or even transplantation, to a maximum.
Tazi
K
K
Service d'Urologie, Hôpital Necker, Paris.
Chretien
Y
Y
Droz
D
D
Richard
S
S
Dufour
B
B
D000293:Adolescent; D002292:Carcinoma, Renal Cell / Q000209:etiology* / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000209:etiology* / Q000473:pathology; D009392:Nephrectomy; D011379:Prognosis; D006435:Renal Dialysis; D006623:von Hippel-Lindau Disease / Q000150:complications*