title: [Unusual site of an embryonal rhabdomyosarcoma of the mesenchymal hepatic pedicle].
abstract: Rhabdomyosarcoma (RMS) is the most common soft tissue sarcoma of children. Tumors arising in the extrahepatic biliary tree are extremely rare (less than 1% of cases). In this location, most are RMS of the botryoid type. We report a case of a 10-year-old child with embryonal RMS arising in the mesenchyma of the hepatic pedicle. Most tumor cells were large, round with abundant eosinophilic cytoplasm. A few cells were small round or spindle-shaped. Tumor cells showed positive immunostaining for muscle markers: desmin and sarcomeric actin. Electron microscopy revealed 2 types of cells: some were undifferentiated and others showed striated muscle differentiation features.
authors.affiliation: Anatomie et Cytologie Pathologiques, CHU de Bicêtre, Le Kremlin-Bicêtre.
authors.forename: S
authors.initials: S
authors.lastname: Ferlicot
authors.forename: J
authors.initials: J
authors.lastname: Quillard
authors.forename: C
authors.initials: C
authors.lastname: Chardot
authors.forename: B
authors.initials: B
authors.lastname: Caillou
authors.forename: O
authors.initials: O
authors.lastname: Oberlin
authors.forename: F
authors.initials: F
authors.lastname: Gauthier
authors.forename: M
authors.initials: M
authors.lastname: Fabre
mesh_terms: D000328:Adult; D003131:Combined Modality Therapy; D006801:Humans; D008113:Liver Neoplasms / Q000473:pathology* / Q000601:surgery / Q000648:ultrastructure; D008297:Male; D008648:Mesoderm; D018233:Rhabdomyosarcoma, Embryonal / Q000473:pathology* / Q000601:surgery / Q000648:ultrastructure