Massive plexiform neurofibroma of the sympathetic trunk.
A case report of a massive plexiform neurofibroma of the sympathetic trunk is reported. Symptoms included dysphagia, shortness of breath and paraesthesia of the right hand. The nerve of origin and extent of the tumour were unusual. The tumour mass partially filled the right hemithorax, surrounded the right brachial plexus, extended to the base of skull and invaded the cervical vertebrae threatening to compromise the spinal cord. Surgical resection required combined cardiothoracic, neurosurgical and plastic and reconstructive surgical teams. Early outcome following surgery was excellent. This case illustrates the need for a combined surgical approach for such a lesion and we believe it is the first reported case of plexiform neurofibroma of the sympathetic trunk.
Oliver
D W
DW
Department of Plastic and Reconstructive Surgery, Addenbrooke's Hospital, Cambridge, UK.
Wells
F C
FC
Lamberty
B G
BG
Waters
A
A
D005260:Female; D006801:Humans; D008875:Middle Aged; D018318:Neurofibroma, Plexiform / Q000175:diagnosis / Q000601:surgery*; D019635:Neurosurgical Procedures / Q000379:methods*; D019651:Plastic Surgery Procedures / Q000379:methods; D013564:Sympathetic Nervous System / Q000473:pathology / Q000601:surgery*; D013899:Thoracic Neoplasms / Q000175:diagnosis / Q000601:surgery*; D013908:Thoracotomy / Q000379:methods; D016896:Treatment Outcome