Port-wine-stain (nevus flammeus), congenital Becker's nevus, café-au-lait-macule and lentigines: phakomatosis pigmentovascularis type Ia--a new combination.
A 16-year-old male had brown macules in a geographic pattern with increased terminal hair on the back and dusky red partially blanchable non progressing macules on his left thigh since birth. Clinical diagnoses of Becker's nevus and port-wine-stain were made and confirmed histopathologically. In addition, he had multiple lentigines on the face and trunk and a single café-au-lait-macule on his chest.
Joshi
A
A
Department of Dermatology, B.P. Koirala Institute of Health Sciences, Dharan, Nepal.
Garg
V K
VK
Agrawal
S
S
Agarwalla
A
A
Thakur
A
A
D000293:Adolescent; D019080:Cafe-au-Lait Spots / Q000473:pathology; D006801:Humans; D007911:Lentigo / Q000473:pathology; D008297:Male; D020752:Neurocutaneous Syndromes / Q000175:diagnosis / Q000473:pathology; D009508:Nevus, Pigmented / Q000473:pathology; D019339:Port-Wine Stain / Q000473:pathology