title: [Atypical primary biliary cirrhosis or autoimmune cholangitis?].
abstract: The term autoimmune cholangitis is used for a disease with clinical and pathological features of primary biliary cirrhosis (PBC), lack of anti-mitochondrial antibodies (AMA), presence of anti-nuclear antibodies (ANA), and good response to immunosuppresive therapy. The current knowledge of this condition is limited and it is not established whether or not it is a different syndrome from the CBP. We report a 51-year-old woman with chronic cholestasis, histological features of PBC, negative AMA and positive peripheral fluorescent ANA pattern, without response to prednisone.
authors.affiliation: Unidad de Digestivo, Hospital de Sagunto, Valencia. jprimo@san.gva.es
authors.forename: J
authors.initials: J
authors.lastname: Primo
authors.forename: A
authors.initials: A
authors.lastname: Miralles
authors.forename: J
authors.initials: J
authors.lastname: Ferrando
authors.forename: A
authors.initials: A
authors.lastname: Albert
authors.forename: R
authors.initials: R
authors.lastname: Julve
authors.forename: A
authors.initials: A
authors.lastname: Gómez
authors.forename: L
authors.initials: L
authors.lastname: García
mesh_terms: D000974:Antibodies, Antinuclear / Q000032:analysis; D001323:Autoantibodies / Q000032:analysis; D001327:Autoimmune Diseases / Q000175:diagnosis*; D001706:Biopsy; D002761:Cholangitis / Q000175:diagnosis* / Q000276:immunology; D003937:Diagnosis, Differential; D005260:Female; D019084:Fluorescent Antibody Technique, Indirect; D006801:Humans; D008099:Liver / Q000473:pathology; D008105:Liver Cirrhosis, Biliary / Q000175:diagnosis*; D008875:Middle Aged; D008928:Mitochondria / Q000276:immunology
chemical_list: D000974:Antibodies, Antinuclear; D001323:Autoantibodies