Gorham syndrome: anaesthetic management.
Gorham syndrome is a rare chronic disease of children and young adults, featuring massive osteolysis with pathological fractures and complicated by respiratory and neurological deficits. To date, 175 cases have been reported in the literature but information on anaesthetic management is sparse. We present a child with Gorham syndrome who underwent urgent surgical medullary decompression and who subsequently developed bilateral pleural effusions.
Szabo
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Department of Anaesthesiology, UCL St-Luc University Hospital, Av. Hippocrate 10, B-1200 Brussels, Belgium.
Habre
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D000768:Anesthesia, General / Q000379:methods*; D002648:Child; D006801:Humans; D008297:Male; D010015:Osteolysis, Essential / Q000473:pathology / Q000601:surgery*; D019990:Perioperative Care / Q000379:methods*; D010996:Pleural Effusion / Q000209:etiology*; D011183:Postoperative Complications / Q000209:etiology*; D011300:Preoperative Care / Q000592:standards