Simultaneous repair of cardiovascular disorders and pectus deformity in a patient with Sprintzen-Goldberg syndrome: A case report.
We report a 12-year-old girl with Sprintzen-Goldberg syndrome (SGS) who was complicated with annuloaortic ectasia with aortic regurgitation, mitral valve prolapse with mitral regurgitation, and a severe pectus excavatum. In this patient, aortic root replacement, mitral valve replacement, and sternal elevation were simultaneously performed, and a version of Ravitch's procedure that was technically modified to support the sternum was used for sternal elevation. This modified sternal elevation technique gave excellent operative exposure, and maintained chest wall stability after the operation.
Aoyagi
S
S
Department of Surgery, Kurume University School of Medicine, 67 Asahi-machi, Kurume 830-0011.
Fukunaga
S
S
Arinaga
K
K
Chihara
S
S
Yokose
S
S
Sakashita
H
H
Tobinaga
S
S
Akashi
H
H
Kawara
T
T
D001014:Aortic Aneurysm / Q000601:surgery; D001018:Aortic Diseases / Q000601:surgery; D001022:Aortic Valve Insufficiency / Q000601:surgery; D019917:Blood Vessel Prosthesis Implantation; D002648:Child; D004108:Dilatation, Pathologic / Q000601:surgery; D005260:Female; D005660:Funnel Chest / Q000601:surgery*; D006331:Heart Diseases / Q000601:surgery*; D006349:Heart Valve Diseases / Q000601:surgery*; D019918:Heart Valve Prosthesis Implantation; D006801:Humans; D008382:Marfan Syndrome / Q000601:surgery*; D008944:Mitral Valve Insufficiency / Q000601:surgery; D008945:Mitral Valve Prolapse / Q000601:surgery; D012850:Sinus of Valsalva / Q000601:surgery; D013249:Sternum / Q000601:surgery