Cholangiopathy and intrahepatic stones in sickle cell disease: coincidence or ischemic cholangiopathy?
Hepatic and bile duct involvement are common in sickle cell disease. This article reports the case of a young woman with cholangiopathy, homozygous sickle cell disease, and protracted anemia. We suggest that sickle cell disease was directly responsible for ischemic cholangiopathy through anoxia.
Hillaire
S
S
Service d'Hépatologie et INSERM U-481, Service d'Hépatologie Clinique, Service de Transfusion Sanguine, Service d'Anatomie et de Cytologie Pathologiques, Hôpital Beaujon, Clichy, France.
Gardin
C
C
Attar
A
A
Attassi
M
M
Terris
B
B
Belghiti
J
J
Degott
C
C
Erlinger
S
S
Valla
D
D
D000328:Adult; D000755:Anemia, Sickle Cell / Q000150:complications* / Q000235:genetics; D001652:Bile Ducts / Q000098:blood supply*; D001653:Bile Ducts, Intrahepatic / Q000000981:diagnostic imaging; D002758:Cholangiography; D002769:Cholelithiasis / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006720:Homozygote; D006801:Humans; D007511:Ischemia / Q000150:complications*