Mitral stenosis obscuring the diagnosis of plexogenic pulmonary arteriopathy and familial pulmonary hypertension.
A patient who died after surgery for critical mitral stenosis was found to have underlying unrecognised plexogenic pulmonary arteriopathy and familial pulmonary hypertension. The importance of recognising familial pulmonary hypertension is discussed, together with the contribution of genetic and other risk factors to plexogenic pulmonary arteriopathy.
Langleben
D
D
Departments of Cardiology, Pathology, Cardiovascular Surgery, and Intensive Care, Sir Mortimer B. Davis Jewish General Hospital, McGill University, Montreal, Quebec, Canada.
Lamoureux
E
E
Marcotte
F
F
Schlesinger
R
R
Dragatakis
L
L
Crowe
M J
MJ
Langlois
Y
Y
Lemire
F
F
White
M
M
D000328:Adult; D017809:Fatal Outcome; D005260:Female; D020022:Genetic Predisposition to Disease; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications*; D008875:Middle Aged; D008946:Mitral Valve Stenosis / Q000150:complications* / Q000601:surgery; D012307:Risk Factors