title: Mitral stenosis obscuring the diagnosis of plexogenic pulmonary arteriopathy and familial pulmonary hypertension.
abstract: A patient who died after surgery for critical mitral stenosis was found to have underlying unrecognised plexogenic pulmonary arteriopathy and familial pulmonary hypertension. The importance of recognising familial pulmonary hypertension is discussed, together with the contribution of genetic and other risk factors to plexogenic pulmonary arteriopathy.
authors.affiliation: Departments of Cardiology, Pathology, Cardiovascular Surgery, and Intensive Care, Sir Mortimer B. Davis Jewish General Hospital, McGill University, Montreal, Quebec, Canada.
authors.forename: D
authors.initials: D
authors.lastname: Langleben
authors.forename: E
authors.initials: E
authors.lastname: Lamoureux
authors.forename: F
authors.initials: F
authors.lastname: Marcotte
authors.forename: R
authors.initials: R
authors.lastname: Schlesinger
authors.forename: L
authors.initials: L
authors.lastname: Dragatakis
authors.forename: M J
authors.initials: MJ
authors.lastname: Crowe
authors.forename: Y
authors.initials: Y
authors.lastname: Langlois
authors.forename: F
authors.initials: F
authors.lastname: Lemire
authors.forename: M
authors.initials: M
authors.lastname: White
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D005260:Female; D020022:Genetic Predisposition to Disease; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications*; D008875:Middle Aged; D008946:Mitral Valve Stenosis / Q000150:complications* / Q000601:surgery; D012307:Risk Factors