Hereditary sensory and autonomic neuropathy: review and a case report with dental implications.
Hereditary sensory and autonomic neuropathy (HSAN) is a rare syndrome which is seen in early childhood. Five different types are described. Absence of pain and self-mutilation are characteristic findings of this syndrome. Teeth in the oral cavity can cause damage to the oral tissues and tongue. When it is diagnosed, there should be co-operation between dentist and neurologist. Using an oral shield prevents the biting and, thus, traumatization of the tissues can be prevented. A case report which is diagnosed as HSAN type 4 is presented and information submitted about its treatment.
Erdem
T L
TL
Faculty of Dentistry, Department of Oral Diagnosis and Radiology, University of Istanbul, Istanbul, Turkey. tlerdem@instanbul.edu.tr
Ozcan
I
I
Ilgüy
D
D
Sirin
S
S
D002648:Child; D005500:Follow-Up Studies; D009477:Hereditary Sensory and Autonomic Neuropathies / Q000503:physiopathology*; D006801:Humans; D008035:Lingual Frenum / Q000002:abnormalities; D008046:Lip / Q000293:injuries*; D008297:Male; D009064:Mouth Protectors; D000699:Pain Insensitivity, Congenital / Q000503:physiopathology; D012652:Self Mutilation / Q000517:prevention & control*; D014059:Tongue / Q000293:injuries*; D014095:Tooth, Impacted / Q000601:surgery