title: [Gronblad-Strandberg syndrome].
abstract: The Grönblad-Strandberg syndrome, also known as pseudoxanthoma elasticum, is a rare congenital dysplasic disorder of the connective tissue, characterized by a progressive abnormal mineralization and dystrophic calcification of elastic tissues and collagen (1). The mode of inheritance is uncertain, but autosomal recessive inheritance can be assumed. This process affects tissues rich in elastic fibres and multiple systems of the organism, being the most common the cutaneous (pseudoxanthoma elasticum), ocular (angioid streaks), vascular (occlusive vascular disease) and gastrointestinal manifestations. These findings progress through the life of the affected person, with variable pattern clinic and evolution.
authors.affiliation: Servicio de Medicina Interna B, Hospital Clínico Universitario, Zaragoza.
authors.forename: M A
authors.initials: MA
authors.lastname: Iglesia Puig
authors.forename: J
authors.initials: J
authors.lastname: Puig Galy
authors.forename: J
authors.initials: J
authors.lastname: Bueno Gómez
authors.forename: A
authors.initials: A
authors.lastname: Arellano Cabornero
authors.forename: B
authors.initials: B
authors.lastname: López-Areal García
mesh_terms: D006801:Humans; D011561:Pseudoxanthoma Elasticum / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology / Q000628:therapy