title: Right ventricular cardiomyopathy showing right bundle branch block and right precordial ST segment elevation.
abstract: A 73-year-old man who had a family history of sudden death, experienced syncope. His electrocardiogram (ECG) presented right bundle branch block and right precordial ST segment elevation which are findings identical with those in Brugada syndrome. The cardiac MRI showed right ventricular mild dilatation, and endomyocardial biopsy revealed fatty replacement of myocardial fibers. Though no ventricular tachyarrhythmias were induced during an electrophysiologic test, the effects on ECG of antiarrhythmic agents and autonomic modulations were similar to those in Brugada syndrome. This case may suggest the relationship between Brugada syndrome and right ventricular cardiomyopathy.
authors.affiliation: Division of Cardiology, Kanto Central Hospital, Tokyo.
authors.forename: T
authors.initials: T
authors.lastname: Izumi
authors.forename: K
authors.initials: K
authors.lastname: Ajiki
authors.forename: A
authors.initials: A
authors.lastname: Nozaki
authors.forename: S
authors.initials: S
authors.lastname: Takahashi
authors.forename: F
authors.initials: F
authors.lastname: Tabei
authors.forename: H
authors.initials: H
authors.lastname: Hayakawa
authors.forename: T
authors.initials: T
authors.lastname: Sugimoto
mesh_terms: D018674:Adrenergic Antagonists / Q000494:pharmacology; D000368:Aged; D000889:Anti-Arrhythmia Agents / Q000494:pharmacology; D002037:Bundle-Branch Block / Q000150:complications* / Q000503:physiopathology; D002311:Cardiomyopathy, Dilated / Q000150:complications* / Q000473:pathology; D003937:Diagnosis, Differential; D004562:Electrocardiography / Q000187:drug effects*; D006352:Heart Ventricles / Q000473:pathology; D006801:Humans; D008297:Male; D013575:Syncope / Q000209:etiology; D013577:Syndrome
chemical_list: D018674:Adrenergic Antagonists; D000889:Anti-Arrhythmia Agents