[Tracheobronchomegaly: an exceptional predisposing factor for pulmonary aspergillomas and massive hemoptysis].
Mounier-Kuhn syndrome--or tracheobronchomegaly--is a rare congenital disorder characterized by significant dilation of the trachea and main bronchi. It is accompanied by ineffective cough and is often complicated by recurrent lung infections and bronchiectasis. Clinical presentation varies widely, ranging from forms with scarce involvement of functional capacity to others that progress to respiratory failure that can prove fatal. We report an exceptional case of massive hemoptysis secondary to the presence of pulmonary aspergillomas and bilateral bronchiectasis in which bronchial arteriography with embolization and surgical resection were insufficient for resolving the complications.
Haro
M
M
Sección de Neumología, Hospital General de Albacete.
Vizcaya
M
M
Jiménez López
J
J
Núñez
A
A
Loeches
N
N
Mansilla
F
F
D000208:Acute Disease; D000328:Adult; D001228:Aspergillosis / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D001234:Aspergillus niger; D001987:Bronchiectasis / Q000175:diagnosis / Q000209:etiology / Q000601:surgery; D003131:Combined Modality Therapy; D004198:Disease Susceptibility; D017809:Fatal Outcome; D006469:Hemoptysis / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D008172:Lung Diseases, Fungal / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D008297:Male; D011013:Pneumonectomy; D014137:Tracheobronchomegaly / Q000150:complications* / Q000175:diagnosis / Q000601:surgery