Pre-excitation syndrome secondary to cardiac rhabdomyomas in tuberous sclerosis.
Rhabdomyomas are not uncommon in infants with tuberous sclerosis. We describe a neonate who presented with hydrops fetalis arising from a tachyarrhythmia during fetal life related to rhabdomyomas. After reversion of the arrhythmia, pre-excitation was noted on an interval electrocardiogram. Following regression of the tumours, the delta wave disappeared with no further arrhythmias noted.
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Monash University Centre for Heart and Chest Research, Monash Medical Centre, Clayton, Victoria, Australia.
Penny
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DJ
Menahem
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D002585:Cesarean Section; D004562:Electrocardiography; D005260:Female; D005315:Fetal Diseases / Q000175:diagnosis; D006338:Heart Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging; D006801:Humans; D015160:Hydrops Fetalis / Q000000981:diagnostic imaging; D007231:Infant, Newborn; D011226:Pre-Excitation Syndromes / Q000209:etiology*; D011247:Pregnancy; D012207:Rhabdomyoma / Q000150:complications* / Q000000981:diagnostic imaging; D013610:Tachycardia / Q000209:etiology; D014402:Tuberous Sclerosis / Q000150:complications* / Q000175:diagnosis; D016216:Ultrasonography, Prenatal