Hypoplastic left heart syndrome with restrictive atrial septal defect and congenital pulmonary lymphangiectasis.
The presence of a restrictive atrial septal defect in hypoplastic left heart syndrome represents a surgical emergency and may negatively affect survival after operation. A neonate with such a disease association, requiring septectomy upon birth developed intractable respiratory failure due to congenital pulmonary lymphangiectasis. The therapeutic implications of this rare pathologic condition are discussed.
Luciani
G B
GB
Division of Cardiac Surgery, University of Verona, Italy.
Pessotto
R
R
Mombello
A
A
Mazzucco
A
A
D017809:Fatal Outcome; D006344:Heart Septal Defects, Atrial / Q000150:complications* / Q000473:pathology / Q000628:therapy; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000150:complications* / Q000473:pathology / Q000628:therapy; D007231:Infant, Newborn; D008168:Lung / Q000002:abnormalities*; D008171:Lung Diseases / Q000150:complications* / Q000151:congenital / Q000473:pathology / Q000628:therapy; D008200:Lymphangiectasis / Q000150:complications* / Q000151:congenital / Q000473:pathology / Q000628:therapy; D008297:Male