[Treatment of desmoid tumors of the mesenteric root].
OBJECTIVE
To elaborate a therapeutic scheme for desmoid tumors developing within the mesenteric root. These uncommon and often unrecognized tumors are difficult to treat as they lie very close to the superior mesenteric vessels.


METHODS
Retrospective analysis of 14 cases treated in our center over the last 20 years and a review of the literature.


RESULTS
The analysis led to the development of a therapeutic scheme. Patients are placed under regular surveillance to detect any progression of the mesenteric root desmoid tumor. In case of progression, surgery should be proposed as often as possible in spite of the real difficulty of this surgery. When the tumor is unresectable, hormone therapy, sulindac, chemotherapy and radiotherapy can be proposed as appropriate.


CONCLUSIONS
Based on the available literature, the proposed decisional tree is a helpful management tool. This scheme should be validated with the help of a National Observatory focusing on this rare disease.
Elias
D
D
Service de Chirurgie digestive carcinologique, Institut Gustave Roussy, Villejuif. elias@igr.fr
Prezioso
G P
GP
Goharin
A
A
Cavalcanti
A
A
Lasser
P
P
D000328:Adult; D000368:Aged; D001706:Biopsy; D003131:Combined Modality Therapy; D005260:Female; D018222:Desmoid Tumors / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008297:Male; D008643:Mesentery / Q000473:pathology / Q000601:surgery*; D008875:Middle Aged; D009367:Neoplasm Staging; D010166:Palliative Care; D010534:Peritoneal Neoplasms / Q000473:pathology / Q000601:surgery*