title: Anaesthesia for liver transplantation in a patient with methylmalonic acidaemia.
abstract: Liver transplantation is an accepted modality of treatment in some patients with inborn errors of metabolism. We present a child with methylmalonic acidaemia who had successful liver transplantation. The pathophysiology, medical and anaesthetic managements are discussed.
authors.affiliation: Department of Anaesthesia, New Children's Hospital, Hawkesbury Road, Westmead, NSW 2145, Australia.
authors.forename: D
authors.initials: D
authors.lastname: Ho
authors.forename: V
authors.initials: V
authors.lastname: Harrison
authors.forename: N
authors.initials: N
authors.lastname: Street
mesh_terms: D000136:Acid-Base Equilibrium / Q000502:physiology; D000769:Anesthesia, Inhalation; D018685:Anesthetics, Inhalation / Q000008:administration & dosage; D006801:Humans; D007223:Infant; D007530:Isoflurane / Q000008:administration & dosage; D016031:Liver Transplantation; D008297:Male; D008661:Metabolism, Inborn Errors / Q000601:surgery* / Q000628:therapy; D008764:Methylmalonic Acid / Q000097:blood*; D011229:Preanesthetic Medication; D006435:Renal Dialysis
chemical_list: D018685:Anesthetics, Inhalation; D008764:Methylmalonic Acid; D007530:Isoflurane