Anaesthesia for liver transplantation in a patient with methylmalonic acidaemia.
Liver transplantation is an accepted modality of treatment in some patients with inborn errors of metabolism. We present a child with methylmalonic acidaemia who had successful liver transplantation. The pathophysiology, medical and anaesthetic managements are discussed.
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Department of Anaesthesia, New Children's Hospital, Hawkesbury Road, Westmead, NSW 2145, Australia.
Harrison
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Street
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N
D000136:Acid-Base Equilibrium / Q000502:physiology; D000769:Anesthesia, Inhalation; D018685:Anesthetics, Inhalation / Q000008:administration & dosage; D006801:Humans; D007223:Infant; D007530:Isoflurane / Q000008:administration & dosage; D016031:Liver Transplantation; D008297:Male; D008661:Metabolism, Inborn Errors / Q000601:surgery* / Q000628:therapy; D008764:Methylmalonic Acid / Q000097:blood*; D011229:Preanesthetic Medication; D006435:Renal Dialysis
D018685:Anesthetics, Inhalation; D008764:Methylmalonic Acid; D007530:Isoflurane