Extra-adrenal pheochromocytoma (paraganglioma).
The authors describe the case of a 19-year-old female patient with an abdominal paraaortic extra-adrenal pheochromocytoma (paraganglioma), presenting arterial hypertension. The predominant catecholamine produced by the tumor was norepinephrine (4110 pg/ml; normal < 450 pg/ml). 131I metaiodobenzylguanidine (131I-MIBG), computed tomography and magnetic resonance imaging allowed location and characterization of the tumor. Histologically the tumor (weight = 34.2 g; 5.8 x 4 x 3 cm) was a typical pheochromocytoma.
Correia
M J
MJ
UTIC-Arsénio Cordeiro, Hospital de Santa Maria, Lisboa.
Mascarenhas
M
M
Madureira
R
R
Neves
L S
LS
Ferreira
J A
JA
Gonçalves
M D
MD
D000008:Abdominal Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D000328:Adult; D001012:Aorta, Abdominal; D005260:Female; D006801:Humans; D006973:Hypertension / Q000209:etiology; D007668:Kidney; D010236:Paraganglioma, Extra-Adrenal / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery