title: [Primary extranodal malignant lymphoma].
abstract: Primary extranodal lymphoma with high frequency and/or unique feature in Japan is discussed. Waldeyer ring lymphoma is most frequent(30%). Most tumors consist of diffuse, large cell type of B cell. CHOP followed by radiation achieved 94.1% of 5 years survival. Gastrointestinal lymphoma is another frequent lymphoma. Surgical rejection followed by chemotherapy and radiation therapy achieved high response. Pyothorax-associated lymphoma is a unique entity reported in Japan. EB-virus and artificial pneumothorax are related to its occurrence. In intravascular lymphomas, lymphoma cells regionally exist in small vessel and are diffuse, large cell type of B cells. Brain is frequently involved. Bone lymphoma is found in 4-8%. The prognosis depend on the site and 5 year relapse-free survival is 70%.
authors.affiliation: First Department of Medicine, Fukui Medical University.
authors.forename: T
authors.initials: T
authors.lastname: Ueda
authors.forename: H
authors.initials: H
authors.lastname: Tsutani
mesh_terms: D001859:Bone Neoplasms / Q000628:therapy; D003131:Combined Modality Therapy; D016724:Empyema, Pleural / Q000150:complications; D005770:Gastrointestinal Neoplasms / Q000628:therapy; D006801:Humans; D016393:Lymphoma, B-Cell / Q000209:etiology / Q000628:therapy; D016403:Lymphoma, Large B-Cell, Diffuse / Q000209:etiology / Q000628:therapy; D011379:Prognosis; D015996:Survival Rate; D014067:Tonsillar Neoplasms / Q000628:therapy; D019043:Vascular Neoplasms / Q000628:therapy