Kearns-Sayre syndromes an absolute indication for prophylactic implantation of definitive pacemaker?
Kearns-Sayre syndrome is a mitochondrial cytopathy characterized by chronic progressive external ophthalmoplegia, retinitis pigmentosa and heart block, the last of which determines the survival of these patients. The case of a 23 year old man with Kearns-Sayre syndrome, conduction disturbances and mitral valve prolapse is presented. The characteristics of this syndrome are described and the criteria for prophylactic installation of a pacemaker discussed.
Barragán-Campos
H M
HM
Department of Internal Medicine, Instituto Nacional de la Nutrición Salvador Zubirán, México, D.F.
Barrera-Ramírez
C F
CF
Iturralde Torres
P
P
Ilarraza-Lomelí
H
H
Avila-Casado
M C
MC
Estañol
B
B
Dorantes
J
J
Oseguera
J
J
D000328:Adult; D002037:Bundle-Branch Block / Q000517:prevention & control; D006801:Humans; D007625:Kearns-Sayre Syndrome / Q000628:therapy*; D008297:Male; D010138:Pacemaker, Artificial