title: Kearns-Sayre syndromes an absolute indication for prophylactic implantation of definitive pacemaker?
abstract: Kearns-Sayre syndrome is a mitochondrial cytopathy characterized by chronic progressive external ophthalmoplegia, retinitis pigmentosa and heart block, the last of which determines the survival of these patients. The case of a 23 year old man with Kearns-Sayre syndrome, conduction disturbances and mitral valve prolapse is presented. The characteristics of this syndrome are described and the criteria for prophylactic installation of a pacemaker discussed.
authors.affiliation: Department of Internal Medicine, Instituto Nacional de la Nutrición Salvador Zubirán, México, D.F.
authors.forename: H M
authors.initials: HM
authors.lastname: Barragán-Campos
authors.forename: C F
authors.initials: CF
authors.lastname: Barrera-Ramírez
authors.forename: P
authors.initials: P
authors.lastname: Iturralde Torres
authors.forename: H
authors.initials: H
authors.lastname: Ilarraza-Lomelí
authors.forename: M C
authors.initials: MC
authors.lastname: Avila-Casado
authors.forename: B
authors.initials: B
authors.lastname: Estañol
authors.forename: J
authors.initials: J
authors.lastname: Dorantes
authors.forename: J
authors.initials: J
authors.lastname: Oseguera
mesh_terms: D000328:Adult; D002037:Bundle-Branch Block / Q000517:prevention & control; D006801:Humans; D007625:Kearns-Sayre Syndrome / Q000628:therapy*; D008297:Male; D010138:Pacemaker, Artificial