Bilateral optic neuropathy associated with diffuse cerebral angiomatosis in Sturge-Weber syndrome.
Visual loss in patients with encephalotrigeminal angiomatosis or Sturge-Weber syndrome usually results from secondary glaucoma or from damage to the retrogeniculate pathways by the angiomatous lesions. Optic neuropathy has not been reported as a component of this syndrome. This report describes a patient who developed bilateral optic neuropathy with progressive visual loss associated with diffuse cerebral angiomatosis in the setting of Sturge-Weber syndrome.
Sadda
S R
SR
Wilmer Ophthalmological Institute, Department of Neurosurgery, The Johns Hopkins Medical Institutions, Baltimore, Maryland, USA.
Miller
N R
NR
Tamargo
R
R
Wityk
R
R
D000328:Adult; D000798:Angiomatosis / Q000150:complications; D001706:Biopsy; D001766:Blindness / Q000209:etiology*; D001927:Brain Diseases / Q000150:complications* / Q000473:pathology; D005260:Female; D005625:Frontal Lobe / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D009898:Optic Disk / Q000473:pathology; D009901:Optic Nerve Diseases / Q000209:etiology*; D013341:Sturge-Weber Syndrome / Q000150:complications* / Q000473:pathology; D014792:Visual Acuity; D014794:Visual Fields