title: [Evaluation of a new amino acid mixture for the treatment of phenylketonuria].
abstract: BACKGROUND
  To assess the acceptability and nutritional adequacy of a new phenylalanine-free amino acid mixture (Phenylade-Dietetic Metabolic Food).
  
  
  METHODS
  Twenty PKU patients (aged 2.6-10 years) diagnosed and followed by our Department. The children were given this product for a minimum of 4 and a maximum of 12 months. The clinical control has been carried out before treatment and then every 3 months. The biochemical parameters included: quantitative plasma amino acids, hematologic measurements of nutritional adequacy folic acid and vitamin B12.
  
  
  RESULTS
  All patients (except one) found this new product to be an acceptable alternatives as to taste and convenience to the previous low phenylalanine protein substitutes.
  
  
  CONCLUSIONS
  Normal growth was maintained.
authors.affiliation: Dipartimento di Pediatria, Istituto G. Gaslini, Genova.
authors.forename: R
authors.initials: R
authors.lastname: Cerone
authors.forename: C
authors.initials: C
authors.lastname: Barella
authors.forename: A R
authors.initials: AR
authors.lastname: Fantasia
authors.forename: M C
authors.initials: MC
authors.lastname: Schiaffino
mesh_terms: D000596:Amino Acids / Q000627:therapeutic use*; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D010649:Phenylalanine / Q000378:metabolism; D010661:Phenylketonurias / Q000178:diet therapy*
chemical_list: D000596:Amino Acids; D010649:Phenylalanine