Delayed cure of an omphalocele requiring abdominosternoplasty, right hepatectomy and partial splenectomy.
A large ventral hernia resulting from the primary treatment of an omphalocele according to the Gross technique was repaired at age 16. The girl presented with extra-abdominal development of the liver and the spleen along with hypotrophy of the abdominal and thoracic cavities. The operation included enlargement sternoplasty, liver and spleen-size reduction and prosthetic abdominal closure. The cosmetic and functional results are good and stable on 7-year follow-up. Surgical issues and blood transfusion policy are discussed. A multi-disciplinary pediatric surgical approach is advocated.
Delarue
A
A
Department of Pediatric Surgery, Hôpital d'Enfants de la Timone, Marseille, France.
Camboulives
J
J
Bollini
G
G
Bardot
J
J
Guys
J M
JM
D005260:Female; D006498:Hepatectomy; D006554:Hernia, Umbilical / Q000601:surgery*; D006555:Hernia, Ventral / Q000209:etiology* / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D011138:Polytetrafluoroethylene / Q000627:therapeutic use; D011183:Postoperative Complications; D019736:Prostheses and Implants; D013156:Splenectomy; D013249:Sternum / Q000601:surgery; D013997:Time Factors
D011138:Polytetrafluoroethylene