Could attacks of abdominal pain in cases of acute intermittent porphyria be due to intestinal angina?
Abdominal pain is by far the most serious symptom in attacks of acute intermittent porphyria. Its cause is unknown. This case study suggests visceral ischaemia as a possible cause of the abdominal pain. A 31-year-old woman with recurrent bouts died during an attack; the autopsy revealed a 20-cm necrotic gangrene in the ileum. A protracted intestinal vasospasm could have been the immediate cause of death. It is discussed whether intestinal angina could be the cause of the abdominal pain in acute intermittent porphyria.
Lithner
F
F
Department of Medicine, University Hospital, Umeå, Sweden. Folke.Lithner@medicin.umu.se
D015746:Abdominal Pain / Q000209:etiology*; D000208:Acute Disease; D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007422:Intestines / Q000098:blood supply*; D007511:Ischemia / Q000150:complications* / Q000175:diagnosis*; D017118:Porphyria, Acute Intermittent / Q000150:complications*