Scimitar syndrome with absence of the right pulmonary artery: a case report.
We report a two-year-old female child with scimitar syndrome associated with absent pulmonary artery but with normal pulmonary artery pressure although several collaterals originated from the abdominal aorta to the right lung. To our knowledge, this is the fifth case with an absent pulmonary artery. Our case also had microphthalmia, an association not previously described in scimitar syndrome.
Saltik
I L
IL
Division of Pediatric Cardiology, Istanbul University Institute of Cardiology.
Eroğlu
A G
AG
Oztunç
F
F
Sarioğlu
A
A
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D001794:Blood Pressure; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008168:Lung / Q000098:blood supply*; D008850:Microphthalmos; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000502:physiology; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D014682:Vena Cava, Inferior / Q000002:abnormalities*