Extra-abdominal desmoid tumor of the hand: a case report and review of the literature.
Extra-abdominal desmoid tumor of the hand is rare and only 10 cases have been described in the literature. We present a 14-year-old boy with a recurrent extra-abdominal desmoid tumor in the dorsal site of the right hand. MR image demonstrated the tumor in the third dorsal interosseous muscle, and adhered to the radial side of the forth metacarpal bone. The lesion revealed iso-signal intensity on T1-weighted images and high intensity on T2. We performed a marginal excision. Histological examination of the tumor showed proliferation of the fibroblastic cells with abundant collagen bundles. He developed local recurrence for the third time. The size of the third recurrent tumor has not been changed for 2 years and 3 months. Therefore, we have not performed any additional surgery. Since extensive resection markedly diminishes the function of the hand, we consider that a marginal surgical margin is acceptable for the quality of daily life of patients with a desmoid tumor of the hand.
Kasukawa
Y
Y
Department of Orthopaedics, Akita University School of Medicine, Japan.
Okada
K
K
Hashimoto
M
M
Sageshima
M
M
D002648:Child; D003094:Collagen / Q000032:analysis; D003286:Contracture / Q000209:etiology; D005347:Fibroblasts / Q000473:pathology; D018222:Desmoid Tumors / Q000473:pathology* / Q000601:surgery; D006225:Hand; D006227:Hand Deformities, Acquired / Q000209:etiology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008663:Metacarpus / Q000473:pathology; D019042:Muscle Neoplasms / Q000473:pathology* / Q000601:surgery; D009361:Neoplasm Invasiveness; D009363:Neoplasm Proteins / Q000032:analysis; D009364:Neoplasm Recurrence, Local; D011183:Postoperative Complications / Q000209:etiology
D009363:Neoplasm Proteins; D003094:Collagen