title: Sjögren's syndrome with primary biliary cirrhosis, complicated by transverse myelitis and malignant lymphoma.
abstract: A 53-year-old woman with Sjögren's syndrome (SS) and primary biliary cirrhosis (PBC) complicated by transverse myelitis (TM) and malignant lymphoma (ML) is reported. TM has been described only in seven cases of primary SS, including three with PBC and four without PBC. The features of SS associated with PBC and complicated by TM were less typical compared with those seen in SS without PBC complicated by TM. This case is the first report of a case with SS, PBC, TM and ML. SS in association with PBC is, in general, overlooked, but such cases must be investigated with great caution for extraglandular complications.
authors.affiliation: Department of Internal Medicine II, Fukushima Medical University School of Medicine.
authors.forename: T
authors.initials: T
authors.lastname: Wakatsuki
authors.forename: M
authors.initials: M
authors.lastname: Miyata
authors.forename: S
authors.initials: S
authors.lastname: Shishido
authors.forename: T
authors.initials: T
authors.lastname: Suzuki
authors.forename: H
authors.initials: H
authors.lastname: Ohira
authors.forename: M
authors.initials: M
authors.lastname: Kokubun
authors.forename: Y
authors.initials: Y
authors.lastname: Sato
authors.forename: T
authors.initials: T
authors.lastname: Yamamoto
authors.forename: R
authors.initials: R
authors.lastname: Kasukawa
mesh_terms: D000005:Abdomen; D001706:Biopsy; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008105:Liver Cirrhosis, Biliary / Q000150:complications* / Q000175:diagnosis; D008198:Lymph Nodes / Q000000981:diagnostic imaging / Q000473:pathology; D016403:Lymphoma, Large B-Cell, Diffuse / Q000150:complications* / Q000175:diagnosis; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D009188:Myelitis, Transverse / Q000150:complications* / Q000175:diagnosis; D009333:Neck; D011877:Radionuclide Imaging; D012859:Sjogren's Syndrome / Q000150:complications* / Q000175:diagnosis; D014057:Tomography, X-Ray Computed