[Leiomyosarcoma of Meckel's diverticulum in cystic form].
BACKGROUND
Leiomyosarcoma is an uncommon small bowel tumor. About 60 cases of a Meckel's diverticulum localization have been reported. We present a very rare form of leiomyosarcoma arising in a Meckel's diverticulum, mimicking a very large abdominal cyst.


METHODS
Abdominal ultrasound evidenced a voluminous cystic mass in the abdomen of a 37-year-old man consulting for abdominal discomfort. Computed tomography visualized a tissular component with contrast uptake. Laparotomy was performed with resection of a 4 liter cyst on the Meckel's diverticulum. Histology reported leiomyosarcoma.


CONCLUSIONS
Leiomyosarcoma of the small bowel mainly develops in an extraluminal localization. Necrotic remodeling explains the cyst formation. Computed tomography with contrast injection can be most helpful for diagnosis. Surgery provides the only possible cure in still localized forms. Other treatments have failed to demonstrate any benefit. Prognosis is mainly related to the histological grading according to the mitotic index.
Cazaban-Mazerolles
D
D
Service de Chirurgie viscérale, Centre Hospitalier, Cahors.
Baylet-Vincent
F
F
D000328:Adult; D003560:Cysts / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007078:Ileal Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D007890:Leiomyosarcoma / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D008297:Male; D008467:Meckel Diverticulum / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed