[Malignant mediastinal schwannoma in Recklinghausen's disease presenting as cardiac tamponade. Report of two cases].
The authors report two cases of Recklinghausen's disease admitted for cardiac tamponade. Two-dimensional echocardiography showed a pericardial tumour in addition to a compressive pericardial effusion. After pericardial drainage, the outcome was rapidly fatal. Histological examination confirmed the diagnosis of a malignant intrapericardial schwannoma. A review of the literature revealed the scarcity of mediastinal malignant schwannoma. Associated with Von Reckinghausen's disease in 2 to 13% of cases, the prognosis is poor. The presentation of malignant mediastinal schwannoma with cardiac tamponade remains very rare.
Bennis
A
A
Centre de cardiologie, CHU Ibn Rochd, Casablanca, Maroc.
Ridai
M
M
Nafidi
S
S
Soulami
S
S
Tahiri
A
A
Chraibi
N
N
D000328:Adult; D002305:Cardiac Tamponade / Q000209:etiology* / Q000473:pathology; D003937:Diagnosis, Differential; D004452:Echocardiography; D006338:Heart Neoplasms / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D008297:Male; D009442:Neurilemmoma / Q000150:complications* / Q000175:diagnosis; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis; D010490:Pericardial Effusion / Q000150:complications