Management and care of the newly diagnosed patient with cystic fibrosis.
Cystic fibrosis is the most common autosomal recessive fatal disease among whites. Life expectancy is now at 31 years of age. The major cause of morbidity and mortality is chronic progressive lung disease. Lung disease occurs early in cystic fibrosis, suggesting the need for early and aggressive treatment of any pulmonary symptoms and malnutrition. This treatment is ideally performed within a cystic fibrosis center, and new therapies are being sought for management of the early stages of disease.
Varlotta
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St. Christopher's Hospital for Children, Allegheny University of the Health Sciences, Medical College of Pennsylvania, Hahnemann School of Medicine, Philadelphia 19134-1095, USA.
D000293:Adolescent; D000328:Adult; D000900:Anti-Bacterial Agents; D002648:Child; D002675:Child, Preschool; D003550:Cystic Fibrosis / Q000150:complications / Q000175:diagnosis / Q000401:mortality / Q000628:therapy*; D004359:Drug Therapy, Combination / Q000008:administration & dosage*; D005260:Female; D006801:Humans; D007223:Infant; D008017:Life Expectancy / Q000639:trends*; D008168:Lung / Q000382:microbiology / Q000473:pathology; D008297:Male; D018410:Pneumonia, Bacterial / Q000175:diagnosis / Q000209:etiology / Q000401:mortality / Q000628:therapy*; D011379:Prognosis; D012129:Respiratory Function Tests; D012138:Respiratory Therapy / Q000379:methods*; D016019:Survival Analysis; D016896:Treatment Outcome
D000900:Anti-Bacterial Agents