Progressive systemic sclerosis and the lung.
Pulmonary manifestations of systemic sclerosis (scleroderma) are many. The mean survival in these patients is 78 +/- 17 months. Improved diagnostic techniques and better therapeutic options are essential to stem the tide of overwhelming mortality in patients with scleroderma lung disease.
Veeraraghavan
S
S
Division of Pulmonary and Critical Care Medicine, Los Angeles, CA 90033, USA.
Sharma
O P
OP
D003952:Diagnostic Imaging; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology; D017563:Lung Diseases, Interstitial / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology*; D011658:Pulmonary Fibrosis / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology; D012129:Respiratory Function Tests; D012595:Scleroderma, Systemic / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology*; D015996:Survival Rate