Bilateral hip arthroplasty for ochronotic arthropathy.
Ochronosis is a musculoskeletal manifestation of alkaptonuria, a rare hereditary metabolic disorder characterised by the absence of the enzyme homogentisic acid oxidase and associated with various systemic abnormalities related to the deposition of homogentisic acid pigment (ochronotic pigment). In this report, we describe a 53-year-old, HLA-B27(+) woman with ochronotic arthropathy. In addition to the typical clinical features of the disorder, she had bilateral hip involvement, which was improved by cementless total hip prosthesis.
Aynaci
O
O
Department of Orthopedic Surgery, Faculty of Medicine, Karadeniz Technical University, Trabzon, Turkey.
Onder
C
C
Turhan
A U
AU
D019644:Arthroplasty, Replacement, Hip; D005260:Female; D006622:Hip Prosthesis; D006713:Homogentisic Acid / Q000652:urine; D006801:Humans; D007738:Kyphosis / Q000000981:diagnostic imaging / Q000652:urine; D008141:Lordosis / Q000000981:diagnostic imaging / Q000652:urine; D008161:Lumbosacral Region / Q000000981:diagnostic imaging; D008875:Middle Aged; D009794:Ochronosis / Q000000981:diagnostic imaging / Q000601:surgery* / Q000652:urine; D015207:Osteoarthritis, Hip / Q000000981:diagnostic imaging / Q000601:surgery* / Q000652:urine; D011859:Radiography; D013167:Spondylitis, Ankylosing / Q000000981:diagnostic imaging / Q000601:surgery* / Q000652:urine
D006713:Homogentisic Acid