title: Fechtner's syndrome: considerations of anesthetic management.
abstract: Fechtner's syndrome is a rare form of macrothrombocytopenia (potentially associated with other hemostatic deficiencies, e.g., von Willebrand's disease and protein Z deficiency), which can exacerbate the risk of uncontrollable bleeding during surgery. We describe the management of a patient with Fechtner's syndrome involving desmopressin, prednisone, and platelets, which produced safe and effective results during cochlear implant surgery.
authors.affiliation: Department of Anesthesiology and Intensive Care, Universitaetskliniken des Saarlandes, Homburg/Saar, Germany. mertzlufft@t-online.de
authors.forename: F
authors.initials: F
authors.lastname: Mertzlufft
authors.forename: A
authors.initials: A
authors.lastname: Koster
authors.forename: H
authors.initials: H
authors.lastname: Steinhart
authors.forename: J F
authors.initials: JF
authors.lastname: Schenk
authors.forename: G J
authors.initials: GJ
authors.lastname: Crystal
mesh_terms: D000758:Anesthesia; D001794:Blood Pressure / Q000187:drug effects; D019929:Cochlear Implantation; D005260:Female; D006339:Heart Rate / Q000187:drug effects; D006801:Humans; D020315:Latex Hypersensitivity / Q000150:complications; D008875:Middle Aged; D010979:Platelet Function Tests; D012828:Silicones; D013577:Syndrome; D013921:Thrombocytopenia / Q000150:complications* / Q000235:genetics
chemical_list: D012828:Silicones