[Aortic dissection at 6 months gestation in a women with Marfan's syndrome. Simultaneous Bentall intervention and cesarean section].
A 31 year old woman with Marfan's syndrome had a dilatation of the aortic root (55-60 mm at the beginning of pregnancy). Pregnancy was continued with beta-blocker therapy and with regular echocardiographic follow-up. The aortic dilatation increased (62-65 mm) at the last control and, at the 34th week of pregnancy, the patient suffered a dissection of the ascending aorta. A caesarean section was performed with a Bentall procedure during the same operative session. The mother and baby girl are well two years later. The problems of pregnancy in patients with Marfan's syndrome are discussed.
Jondeau
G
G
Service de cardiologie, hôpital Ambroise-Paré, Boulogne.
Nataf
P
P
Belarbi
A
A
Farcot
J C
JC
Iung
B
B
Delorme
G
G
Gandjbakhch
I
I
Bourdarias
J P
JP
D000319:Adrenergic beta-Antagonists / Q000627:therapeutic use; D000328:Adult; D000784:Aortic Dissection / Q000473:pathology / Q000601:surgery*; D001014:Aortic Aneurysm / Q000473:pathology / Q000601:surgery*; D002585:Cesarean Section; D005260:Female; D006801:Humans; D008382:Marfan Syndrome / Q000150:complications*; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000601:surgery*; D011256:Pregnancy Outcome; D016896:Treatment Outcome
D000319:Adrenergic beta-Antagonists