Rapid recurrence of an inflammatory myofibroblastic tumor in the right ventricular outflow tract.
We describe an unusual case of rapid recurrence of a previously excised inflammatory myofibroblastic tumor of the right ventricular outflow tract in a 5-month-old infant. The infant is asymptomatic 18 months after the second surgery. The very rare cardiac involvement, and the early relapse of the inflammatory pseudotumor, to the best of our knowledge, is a unique combination. The inflammatory myofibroblastic tumor, as known as a pseudotumor or plasma cell granuloma is an uncommon reactive lesion with unknown aetiology. It is found most commonly in the lung and a number of visceral organs, such as the spleen, liver, ileum, salivary glands, urinary bladder, larynx or brain or in the retroperitoneum and lymph nodes. To our knowledge only 9 cases have been published of such tumor arising within the heart.
Hartyánszky
I L
IL
Hungarian Institute of Cardiology, Paediatric Cardiac Surgery Department, Budapest. hartyanszky@hotmail.com
Kádár
K
K
Hubay
M
M
D002315:Cardiopulmonary Bypass; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D006104:Granuloma, Plasma Cell / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery*; D006331:Heart Diseases / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery*; D006801:Humans; D007150:Immunohistochemistry; D007223:Infant; D011651:Pulmonary Artery / Q000473:pathology* / Q000601:surgery; D012008:Recurrence; D012086:Reoperation; D016896:Treatment Outcome; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery*