[Ileal invaginations caused by Peutz-Jeghers polyposis].
The Peutz-Jeghers syndrome is considered a familial polyposis syndrome. The polyps are of hamartomatous type. The symptomatology is due to the more voluminous polyps which can necrotize, ulcerate, bleed and cause intussusception and intestinal obstruction. A case of ileum-ileal intussusception due to Peutz-Jeghers syndrome is reported. The utility of a genealogic research is underlined and the recent results of the genetic research are evaluated. The surgical therapy of Peutz-Jeghers syndrome can have many aims: 1) to remove all big polyps, 2) to avoid the danger of canceration, 3) to prevent the hemorrhagic or occlusive risks and complications.
Mirone
I
I
Cattedra e Unità Operativa di Chirurgia dell'Apparato Digerente, Università degli Studi, Catania.
Consoli
A
A
Bonaccorso
R
R
Cimbali
P
P
Lizzio
A
A
Cavallaro
A
A
D000328:Adult; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007077:Ileal Diseases / Q000209:etiology* / Q000601:surgery; D007443:Intussusception / Q000209:etiology* / Q000601:surgery; D008297:Male; D010375:Pedigree; D010580:Peutz-Jeghers Syndrome / Q000150:complications* / Q000235:genetics / Q000601:surgery; D013997:Time Factors