Fechtner's syndrome: considerations of anesthetic management.
Fechtner's syndrome is a rare form of macrothrombocytopenia (potentially associated with other hemostatic deficiencies, e.g., von Willebrand's disease and protein Z deficiency), which can exacerbate the risk of uncontrollable bleeding during surgery. We describe the management of a patient with Fechtner's syndrome involving desmopressin, prednisone, and platelets, which produced safe and effective results during cochlear implant surgery.
Mertzlufft
F
F
Department of Anesthesiology and Intensive Care, Universitaetskliniken des Saarlandes, Homburg/Saar, Germany. mertzlufft@t-online.de
Koster
A
A
Steinhart
H
H
Schenk
J F
JF
Crystal
G J
GJ
D000758:Anesthesia; D001794:Blood Pressure / Q000187:drug effects; D019929:Cochlear Implantation; D005260:Female; D006339:Heart Rate / Q000187:drug effects; D006801:Humans; D020315:Latex Hypersensitivity / Q000150:complications; D008875:Middle Aged; D010979:Platelet Function Tests; D012828:Silicones; D013577:Syndrome; D013921:Thrombocytopenia / Q000150:complications* / Q000235:genetics
D012828:Silicones