title: [A surgical case of atrial septal defect with myotonic dystrophy].
abstract: A case report is presented of a 16-year-old woman with myotonic dystrophy, who required open-heart surgery for an atrial septal defect. We successfully repaired an atrial septal defect using normothermic cardiopulmonary bypass and electrically maintained ventricular fibrillation. Anesthesia using fentanyl, vecronium and isoflurane was uneventful and there were no postoperative complications. Anesthetic agents must be selected with care, and ventilation requires meticulous attention.
authors.affiliation: Department of Surgery, University of Tsukuba, Japan.
authors.forename: T
authors.initials: T
authors.lastname: Jikuya
authors.forename: T
authors.initials: T
authors.lastname: Shimada
authors.forename: Y
authors.initials: Y
authors.lastname: Hiramatsu
authors.forename: Y
authors.initials: Y
authors.lastname: Sakakibara
authors.forename: T
authors.initials: T
authors.lastname: Mitsui
mesh_terms: D000293:Adolescent; D000758:Anesthesia; D002315:Cardiopulmonary Bypass; D005260:Female; D005283:Fentanyl; D006344:Heart Septal Defects, Atrial / Q000150:complications / Q000601:surgery*; D006801:Humans; D007530:Isoflurane; D009223:Myotonic Dystrophy / Q000150:complications*; D019990:Perioperative Care; D012121:Respiration, Artificial; D016896:Treatment Outcome; D014673:Vecuronium Bromide
chemical_list: D014673:Vecuronium Bromide; D007530:Isoflurane; D005283:Fentanyl