[Primitive leiomyosarcoma of the right atrium presenting with a pulmonary embolism].
Primary Cardiac leiomyosarcoma is a very rare condition. The authors report the case of a 64 year old woman admitted to hospital for suspected pulmonary embolism, confirmed by thoracic angio-CT scan. Despite thrombolytic therapy, a persistent poor haemodynamic condition associated with a superior vena cava syndrome led to a transoesophageal echocardiographic examination which demonstrated an abnormal intra-right atrial mass obstructing the tricuspid valve. At surgery, a leio-myosarcoma was successfully resected under good conditions. During systematic three-monthly clinical and echocardiographic follow-up, transoesophageal echocardiography detected an asymptomatic local recurrence at 15 months, for which surgery was repeated with adjuvant chemotherapy.
Imbert
S
S
Service de soins intensifs cardiologiques, hôpital cardiologique du Haut-Lévêque, CHU de Bordeaux, Pessac.
Laffort
P
P
Deville
C
C
Bonnel
C
C
De Mascarel
A
A
Roudaut
R
R
D003937:Diagnosis, Differential; D017548:Echocardiography, Transesophageal; D005260:Female; D006325:Heart Atria; D006338:Heart Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D006439:Hemodynamics; D006801:Humans; D007890:Leiomyosarcoma / Q000150:complications / Q000473:pathology* / Q000601:surgery; D008875:Middle Aged; D009364:Neoplasm Recurrence, Local; D011655:Pulmonary Embolism / Q000209:etiology*; D013479:Superior Vena Cava Syndrome / Q000209:etiology; D016896:Treatment Outcome