Congenitally corrected transposition with pulmonary atresia and intact ventricular septum.
We describe a patient with the rare association of the heart in the left chest, congenitally corrected transposition, pulmonary atresia and an intact ventricular septum. There were associated fistulous communications between the morphologically left ventricle and the coronary arteries. Diagnosis was made by echocardiography, and subsequently confirmed by cardiac catheterization.
Patel
C R
CR
Department of Pediatrics, Rainbow Babies and Childrens Hospital, Case Western Reserve University School of Medicine, Cleveland, OH 44106, USA. cxp24@po.cwru.edu
Spector
M L
ML
Zahka
K G
KG
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D006328:Cardiac Catheterization; D004452:Echocardiography; D017809:Fatal Outcome; D006346:Heart Septum / Q000033:anatomy & histology*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D018633:Pulmonary Atresia / Q000175:diagnosis*; D014188:Transposition of Great Vessels / Q000175:diagnosis*