Recurrent lower respiratory tract infections in a 14-year-old boy with tracheobronchomegaly (Mounier-Kuhn syndrome).
Tracheobronchomegaly (Mounier-Kuhn syndrome) is characterized by dilatation of the central airways, tracheobronchial outpouchings, and chronic tracheobronchitis. Most cases are diagnosed in adulthood. We report the clinical, radiographic, and bronchoscopic findings in a 14-year-old boy with tracheobronchomegaly, ptosis of the right eyelid, and redundant skin and mucosa of the upper lip, who presented with a 2-year history of recurrent lower respiratory tract infections. Pediatricians should be aware of the possibility that tracheobronchomegaly may cause clinical symptoms in childhood and adolescence. Pediatr Pulmonol. 2000; 29: 476-479.
Benesch
M
M
Respiratory and Allergic Disease Division, Department of Pediatrics, University of Graz, Graz, Austria. maximilian.zach@kfunigraz.ac.at
Eber
E
E
Pfleger
A
A
Zach
M S
MS
D000293:Adolescent; D001763:Blepharoptosis; D006801:Humans; D008046:Lip / Q000002:abnormalities; D008297:Male; D012008:Recurrence; D012141:Respiratory Tract Infections / Q000209:etiology* / Q000473:pathology; D014137:Tracheobronchomegaly / Q000150:complications* / Q000382:microbiology