Pulmonary hypertension as a result of asymptomatic portosystemic shunt.
This report describes a patient with severe pulmonary hypertension accompanied by a congenital intrahepatic portosystemic shunt. Primary pulmonary hypertension was suspected initially because none of the classic symptoms of a portosystemic shunt were present. Physicians should note that disorders of the portal system may cause pulmonary hypertension even in the absence of symptoms suggesting liver disease.
Imamura
H
H
The First Department of Internal Medicine, Shinshu University School of Medicine, Matsumoto, Japan. imamura@hsp.md.shinshu-u.ac.jp
Momose
T
T
Kitabayashi
H
H
Takahashi
W
W
Yazaki
Y
Y
Takenaka
H
H
Isobe
M
M
Sekiguchi
M
M
Kubo
K
K
D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology* / Q000503:physiopathology*; D008107:Liver Diseases / Q000150:complications*; D008875:Middle Aged; D011168:Portal System / Q000002:abnormalities*