title: Intestinal involvement and vasculopathy in von Recklinghausen's neurofibromatosis.
abstract: Involvement of the gastrointestinal system and vascular lesions are well-known features of von Recklinghausen's disease, but they are rarely detected in childhood. We report a case of von Recklinghausen's disease with intestinal involvement. The excised right hemicolectomy material of a 16-year-old girl was examined, and diffuse neurofibromatous proliferation with ganglioneuromatous features were observed. Vasculopathy was also seen in some arteries throughout the intestinal segment.
authors.affiliation: Department of Pediatrics, Hacettepe University Faculty of Medicine, Ankara.
authors.forename: S
authors.initials: S
authors.lastname: Göğüş
authors.forename: F
authors.initials: F
authors.lastname: Sarikayalar
authors.forename: Z
authors.initials: Z
authors.lastname: Akçören
authors.forename: D
authors.initials: D
authors.lastname: Yalnizoğlu
authors.forename: A
authors.initials: A
authors.lastname: Hiçsönmez
mesh_terms: D000293:Adolescent; D001158:Arteries / Q000473:pathology; D003082:Colectomy; D005260:Female; D006801:Humans; D007410:Intestinal Diseases / Q000209:etiology* / Q000473:pathology* / Q000601:surgery; D007422:Intestines / Q000098:blood supply* / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000473:pathology