Tongue reduction in Beckwith-Weidemann syndrome.
OBJECTIVE
To review our experience with patients with macroglossia as a component of Beckwith-Weidemann Syndrome (BWS).


METHODS
Chart review of six patients treated with BWS.


METHODS
Tertiary care teaching hospital.


METHODS
Six patients diagnosed with BWS and macroglossia.


METHODS
Four patients underwent at least one surgical procedure to address their macroglossia. The surgical options and potential complications are discussed.


RESULTS
Three patients who have undergone tongue reduction have a functioning tongue with normal mobility. Two patients have required tracheotomy as apart of their management and still have significant tongue enlargement.


CONCLUSIONS
Macroglossia as a part of BWS may present a difficult management problem. Various methods of tongue reductions have been reported with mixed results.
Kacker
A
A
Lenox Hill Hospital and Manhattan Eye, Ear and Throat Hospital, 2nd Floor, 186 East 76th Street, New York, NY 10021, USA.
Honrado
C
C
Martin
D
D
Ward
R
R
D001506:Beckwith-Wiedemann Syndrome / Q000175:diagnosis; D002675:Child, Preschool; D004954:Esthetics; D005069:Evaluation Studies as Topic; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008260:Macroglossia / Q000175:diagnosis / Q000601:surgery*; D008297:Male; D019647:Oral Surgical Procedures / Q000379:methods*; D014059:Tongue / Q000601:surgery; D016896:Treatment Outcome