title: Anesthetic management for patients with arthrogryposis multiplex congenita and severe micrognathia: case reports.
abstract: Arthrogryposis multiplex congenita (AMC) is a spectrum syndrome of multiple persistent limb contractures often accompanied by associated anomalies, including cleft palate, genitourinary defects, gastroschisis, and cardiac defects. Pediatric patients with AMC frequently present for multiple surgeries requiring general endotracheal anesthesia. We describe our anesthetic experience with the laryngeal mask airway and endotracheal tube in two neonates with AMC and severe micrognathia. We discuss AMC and outline the problems encountered in difficult airway management.
authors.affiliation: Department of Anesthesiology, The University of Texas Medical Branch at Galveston, Galveston, TX 77555-0591, USA. nhnguyen@utmb.edu
authors.forename: N H
authors.initials: NH
authors.lastname: Nguyen
authors.forename: E M
authors.initials: EM
authors.lastname: Morvant
authors.forename: J F
authors.initials: JF
authors.lastname: Mayhew
mesh_terms: D000758:Anesthesia / Q000379:methods*; D001176:Arthrogryposis / Q000601:surgery*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D007442:Intubation, Intratracheal; D017214:Laryngeal Masks; D008297:Male; D008844:Micrognathism / Q000601:surgery*