title: Bronchiolitis obliterans organizing pneumonia: a distinct pulmonary complication in cystic fibrosis.
abstract: Organizing pneumonia in cystic fibrosis has hitherto been considered a nonspecific reparative process. We report on an adult patient with cystic fibrosis and histologically proven bronchiolitis obliterans organizing pneumonia, who experienced sustained clinical improvement under corticosteroid therapy. This case suggests that bronchiolitis obliterans organizing pneumonia may be a distinct pulmonary complication in cystic fibrosis and improve with specific therapy.
authors.affiliation: Department of Pediatrics, University Hospital, RWTH Aachen, Germany. Haeusler@RWTH-Aachen.de
authors.forename: M
authors.initials: M
authors.lastname: Häusler
authors.forename: R
authors.initials: R
authors.lastname: Meilicke
authors.forename: S
authors.initials: S
authors.lastname: Biesterfeld
authors.forename: H
authors.initials: H
authors.lastname: Kentrup
authors.forename: F
authors.initials: F
authors.lastname: Friedrichs
authors.forename: G
authors.initials: G
authors.lastname: Kusenbach
mesh_terms: D000328:Adult; D001707:Biopsy, Needle; D018549:Cryptogenic Organizing Pneumonia / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology; D003550:Cystic Fibrosis / Q000150:complications*; D004305:Dose-Response Relationship, Drug; D004334:Drug Administration Schedule; D005500:Follow-Up Studies; D005938:Glucocorticoids / Q000008:administration & dosage*; D006801:Humans; D008297:Male; D011239:Prednisolone / Q000008:administration & dosage*; D016896:Treatment Outcome
chemical_list: D005938:Glucocorticoids; D011239:Prednisolone