Management of tracheal agenesis.
Complete tracheal agenesis is a very rare congenital anomaly that is only compatible with life in some cases with associated tracheo-oesophageal or broncho-oesophageal fistula. In most cases, concomitant congenital anomalies of the heart, digestive tract or genitourinary tract are present. It should be suspected in any neonate with a history of hydramnios, absent crying, respiratory distress and difficulty in intubation. The possibility for surgical correction or palliation rests on the extent of atresia present. We present a case of complete tracheal agenesis without tracheo nor broncho-oesophageal fistula (type II by Floyd's classification) - the diagnosis of which was prenatally suspected - and discuss the important features of the airway management of this condition.
De José María
B
B
Department of Paediatric Anaesthesia Universitat de Barcelona, Barcelona, Spain.
Drudis
R
R
Monclús
E
E
Silva
A
A
Santander
S
S
Cusí
V
V
D000015:Abnormalities, Multiple; D000328:Adult; D000649:Amniocentesis; D000653:Amniotic Fluid / Q000737:chemistry; D003448:Crying / Q000502:physiology; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007442:Intubation, Intratracheal; D007828:Laryngoscopy; D008297:Male; D010166:Palliative Care; D010743:Phospholipids / Q000032:analysis; D006831:Polyhydramnios / Q000150:complications; D011247:Pregnancy; D012127:Respiratory Distress Syndrome, Newborn / Q000209:etiology; D014132:Trachea / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000196:embryology / Q000601:surgery; D016216:Ultrasonography, Prenatal
D010743:Phospholipids