Phytanic acid alpha-oxidation in man: identification of 2-hydroxyphytanoyl-CoA lyase, a peroxisomal enzyme with normal activity in Zellweger syndrome.
Jansen
G A
GA
University of Amsterdam, Academic Medical Centre, Department of Clinical Chemistry, Emma Children's Hospital, The Netherlands.
Denis
S
S
Verhoeven
N M
NM
Jakobs
C
C
Wanders
R J
RJ
D019755:Carbon-Carbon Lyases / Q000378:metabolism*; D006801:Humans; D008099:Liver / Q000201:enzymology; D008297:Male; D010084:Oxidation-Reduction; D020675:Peroxisomes / Q000201:enzymology; D010831:Phytanic Acid / Q000378:metabolism*; D015211:Zellweger Syndrome / Q000201:enzymology*
D010831:Phytanic Acid; D019755:Carbon-Carbon Lyases; C121516:2-hydroxyphytanoyl-coenzyme A lyase