title: Phytanic acid alpha-oxidation in man: identification of 2-hydroxyphytanoyl-CoA lyase, a peroxisomal enzyme with normal activity in Zellweger syndrome.
authors.affiliation: University of Amsterdam, Academic Medical Centre, Department of Clinical Chemistry, Emma Children's Hospital, The Netherlands.
authors.forename: G A
authors.initials: GA
authors.lastname: Jansen
authors.forename: S
authors.initials: S
authors.lastname: Denis
authors.forename: N M
authors.initials: NM
authors.lastname: Verhoeven
authors.forename: C
authors.initials: C
authors.lastname: Jakobs
authors.forename: R J
authors.initials: RJ
authors.lastname: Wanders
mesh_terms: D019755:Carbon-Carbon Lyases / Q000378:metabolism*; D006801:Humans; D008099:Liver / Q000201:enzymology; D008297:Male; D010084:Oxidation-Reduction; D020675:Peroxisomes / Q000201:enzymology; D010831:Phytanic Acid / Q000378:metabolism*; D015211:Zellweger Syndrome / Q000201:enzymology*
chemical_list: D010831:Phytanic Acid; D019755:Carbon-Carbon Lyases; C121516:2-hydroxyphytanoyl-coenzyme A lyase