Massive hematuria in adults with Klippel-Trenaunay syndrome associated with vascular malformation of the bladder.
Although hematuria has been reported in children with Klippel-Trenaunay syndrome, it is a rare presentation in the adult population. Two cases of massive hematuria in adults with Klippel-Trenaunay syndrome are reported here. A unique feature was venous malformations of the bladder which were responsible for massive recurrent bleeding in 1 patient. The clinical presentation and management are discussed. Conservative endoscopic and arteriographic control seems to be appropriate as initial management in these patients.
Shekarriz
B
B
Department of Urology, Wayne State University and School of Medicine, Detroit, MI 48201, USA. aa3542@wayne.edu
Upadhyay
J
J
Smith
C
C
Kazmers
A
A
Frontera
R
R
D000328:Adult; D001165:Arteriovenous Malformations / Q000150:complications*; D006417:Hematuria / Q000209:etiology*; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008297:Male; D001743:Urinary Bladder / Q000098:blood supply*