title: Management of tracheal agenesis.
abstract: Complete tracheal agenesis is a very rare congenital anomaly that is only compatible with life in some cases with associated tracheo-oesophageal or broncho-oesophageal fistula. In most cases, concomitant congenital anomalies of the heart, digestive tract or genitourinary tract are present. It should be suspected in any neonate with a history of hydramnios, absent crying, respiratory distress and difficulty in intubation. The possibility for surgical correction or palliation rests on the extent of atresia present. We present a case of complete tracheal agenesis without tracheo nor broncho-oesophageal fistula (type II by Floyd's classification) - the diagnosis of which was prenatally suspected - and discuss the important features of the airway management of this condition.
authors.affiliation: Department of Paediatric Anaesthesia Universitat de Barcelona, Barcelona, Spain.
authors.forename: B
authors.initials: B
authors.lastname: De José María
authors.forename: R
authors.initials: R
authors.lastname: Drudis
authors.forename: E
authors.initials: E
authors.lastname: Monclús
authors.forename: A
authors.initials: A
authors.lastname: Silva
authors.forename: S
authors.initials: S
authors.lastname: Santander
authors.forename: V
authors.initials: V
authors.lastname: Cusí
mesh_terms: D000015:Abnormalities, Multiple; D000328:Adult; D000649:Amniocentesis; D000653:Amniotic Fluid / Q000737:chemistry; D003448:Crying / Q000502:physiology; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007442:Intubation, Intratracheal; D007828:Laryngoscopy; D008297:Male; D010166:Palliative Care; D010743:Phospholipids / Q000032:analysis; D006831:Polyhydramnios / Q000150:complications; D011247:Pregnancy; D012127:Respiratory Distress Syndrome, Newborn / Q000209:etiology; D014132:Trachea / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000196:embryology / Q000601:surgery; D016216:Ultrasonography, Prenatal
chemical_list: D010743:Phospholipids