title: Treatment of otitis media with effusion in children with mucopolysaccharidoses.
abstract: Otitis media with effusion (OME) is a constant finding in children with mucopolysaccharidoses (MPS). Affected children may also present the anaesthetist with a difficult airway. A 7-year retrospective review of the management of OME in individuals with MPS was carried out. Nine patients were identified. All had a number of short-term ventilation tube insertions (one to four, mean two) before a diagnosis of MPS was made. Following diagnosis three required repeated short-term ventilation tubes insertions (two to four, mean three), four had long-term ventilation tube insertions once only. Five children who had residual hearing loss were provided with hearing aids but compliance was poor in two. Once a diagnosis of MPS has been made, a hearing aid, if compliant, or a long-term ventilation tube would be a better option than a short term one in order to minimise the anaesthetic risk. A 'watch and wait' policy is not recommended.
authors.affiliation: Department of Otolaryngology Head and Neck Surgery, Leicester Royal Infirmary, UK.
authors.forename: M
authors.initials: M
authors.lastname: Motamed
authors.forename: S
authors.initials: S
authors.lastname: Thorne
authors.forename: A
authors.initials: A
authors.lastname: Narula
mesh_terms: D002675:Child, Preschool; D005260:Female; D006310:Hearing Aids; D006311:Hearing Disorders / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D006801:Humans; D008297:Male; D008876:Middle Ear Ventilation / Q000379:methods*; D009083:Mucopolysaccharidoses / Q000150:complications*; D010034:Otitis Media with Effusion / Q000150:complications* / Q000601:surgery*; D012189:Retrospective Studies