Intracranial adenoid cystic carcinoma--a case report.
Adenoid cystic carcinoma (ACC) is a relatively common malignant neoplasm which occurs in the head and neck region, particularly in the salivary glands. It is a slow growing, locally aggressive neoplasm with a unique feature of perineural spread. Intracranial extension can occur by direct extension, hematogenous metastases or by perineural spread. However, the occurrence of primary intracranial ACC with no evidence of a primary, is rare, with only ten cases reported in reviewed English literature until now. One such case is presented here with brief review of literature. This patient showed a good response to treatment with surgery followed by post-operative radiotherapy and has remained disease free, 32 months after the completion of treatment.
Jayalakshmi
S
S
Department of Radiotherapy, All India Institute of Medical Sciences, New Delhi, India.
Agarwal
S
S
Nachiappan
P L
PL
Prasad
R R
RR
Bhuthra
S
S
Sharma
M C
MC
Julka
P K
PK
D000328:Adult; D001706:Biopsy; D003528:Carcinoma, Adenoid Cystic / Q000473:pathology* / Q000532:radiotherapy / Q000601:surgery; D003390:Cranial Nerve Neoplasms / Q000473:pathology* / Q000532:radiotherapy / Q000601:surgery; D004388:Dura Mater / Q000473:pathology; D006801:Humans; D008297:Male; D010525:Peripheral Nerves / Q000473:pathology; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014276:Trigeminal Nerve / Q000473:pathology