Duplicated exstrophy in one of identical twins.
The characteristic of duplicated exstrophy is the presence of a patch of exstrophic bladder mucosa in the infraumbilical region with a low-set umbilicus, in addition to the normal bladder. Musculoskeletal defects, diastasis pubis, and rectus abdominis can also be found in these patients. We report the first case of a female twin baby with appearance of a low-set umbilicus and diastasis pubis associated with a pubic sinus. The external genitalia and urinary continence were normal. Duplicated exstrophic mucosal remnant was excised, and the histopathologic study of the specimen confirmed urothelium.
Department of Pediatric Surgery, Zeynep Kamil Hospital, Istanbul, Turkey.
A
A
Cerrah Celayir
S
S
Celayir
N
N
Oner
G
G
Vural
N
N
Danişmend
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000235:genetics / Q000601:surgery; D001746:Bladder Exstrophy / Q000175:diagnosis* / Q000235:genetics / Q000601:surgery; D004200:Diseases in Twins / Q000175:diagnosis* / Q000235:genetics; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011379:Prognosis; D011631:Pubic Symphysis / Q000002:abnormalities / Q000601:surgery; D014430:Twins, Monozygotic