Encephalopathy, hearing loss and retinal occlusions (Susac's syndrome): a new case.
We describe a young woman with retinal arteriolar occlusions, encephalopathy, and hearing loss. At present this disorder is known as Susac's syndrome, a microangiopathy of the brain and retina whose pathogenesis is, however, unknown. The article reviews the clinical features of this rare, but not unusual, syndrome that can easily be misdiagnosed as multiple sclerosis.
Department of Neurological Sciences, Civilian Hospital S. Maria, Terni, Italy.
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M
Maddestra
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S
Sabatini
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A
Paci
D000328:Adult; D001301:Audiometry, Pure-Tone; D002533:Cerebral Angiography; D002560:Cerebrovascular Circulation; D004660:Encephalitis / Q000175:diagnosis*; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008833:Microcirculation; D015356:Retinal Artery Occlusion / Q000175:diagnosis*