Duplicated exstrophy in one of identical twins.
The characteristic of duplicated exstrophy is the presence of a patch of exstrophic bladder mucosa in the infraumbilical region with a low-set umbilicus, in addition to the normal bladder. Musculoskeletal defects, diastasis pubis, and rectus abdominis can also be found in these patients. We report the first case of a female twin baby with appearance of a low-set umbilicus and diastasis pubis associated with a pubic sinus. The external genitalia and urinary continence were normal. Duplicated exstrophic mucosal remnant was excised, and the histopathologic study of the specimen confirmed urothelium.
Cerrah Celayir
A
A
Department of Pediatric Surgery, Zeynep Kamil Hospital, Istanbul, Turkey.
Celayir
S
S
Oner
N
N
Vural
G
G
Danişmend
N
N
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000235:genetics / Q000601:surgery; D001746:Bladder Exstrophy / Q000175:diagnosis* / Q000235:genetics / Q000601:surgery; D004200:Diseases in Twins / Q000175:diagnosis* / Q000235:genetics; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011379:Prognosis; D011631:Pubic Symphysis / Q000002:abnormalities / Q000601:surgery; D014430:Twins, Monozygotic