title: Bilateral sequential lung transplant for ectodermal dysplasia.
abstract: A case of bilateral sequential lung transplantation for anhidrotic ectodermal dysplasia is presented. The patient was a 16-year-old male with end-stage lung disease secondary to chronic severe respiratory infection. Although a relatively rare disease, the common association of fatal pulmonary compromise in those affected with this disorder warrants consideration of lung transplantation as a viable therapeutic option.
authors.affiliation: Department of Anesthesiology, The Children's Hospital of Philadelphia, Pennsylvania 19104, USA.
authors.forename: W R
authors.initials: WR
authors.lastname: Smythe
authors.forename: N D
authors.initials: ND
authors.lastname: Bridges
authors.forename: J W
authors.initials: JW
authors.lastname: Gaynor
authors.forename: S
authors.initials: S
authors.lastname: Nicolson
authors.forename: B J
authors.initials: BJ
authors.lastname: Clark
authors.forename: T L
authors.initials: TL
authors.lastname: Spray
mesh_terms: D000293:Adolescent; D004476:Ectodermal Dysplasia / Q000150:complications*; D017809:Fatal Outcome; D006801:Humans; D016040:Lung Transplantation / Q000379:methods*; D008297:Male; D012131:Respiratory Insufficiency / Q000209:etiology* / Q000601:surgery*