title: Beckwith-Wiedemann syndrome and virilizing cortical adrenal tumor in a child.
abstract: The authors report a case of a virilizing adrenal tumor that developed in a 2-year-old child with Beckwith-Wiedemann syndrome (BWS). He had a fetal diagnosis of omphalocele and a history of neonatal adrenal cysts. The importance of prenatal diagnosis of BWS and postnatal follow-up of tumors is discussed. The differential diagnosis of adrenal pathologies occurring in BWS also is reviewed.
authors.affiliation: Department of Pathology, Faculty of Medical Science, State University of Campinas, São Paulo, Brazil.
authors.forename: L
authors.initials: L
authors.lastname: Sbragia-Neto
authors.forename: A A
authors.initials: AA
authors.lastname: Melo-Filho
authors.forename: G
authors.initials: G
authors.lastname: Guerra-Júnior
authors.forename: S H
authors.initials: SH
authors.lastname: Valente de Lemos Marini
authors.forename: M T
authors.initials: MT
authors.lastname: Baptista
authors.forename: P S
authors.initials: PS
authors.lastname: Sabino de Matos
authors.forename: A
authors.initials: A
authors.lastname: Gonçalves de Oliveira-Filho
authors.forename: J M
authors.initials: JM
authors.lastname: Bustorff-Silva
mesh_terms: D000306:Adrenal Cortex Neoplasms / Q000150:complications* / Q000175:diagnosis; D001506:Beckwith-Wiedemann Syndrome / Q000150:complications* / Q000175:diagnosis; D002675:Child, Preschool; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D011296:Prenatal Diagnosis; D013997:Time Factors; D014770:Virilism / Q000209:etiology