Absence of the aortic valve associated with hypoplastic left-sided heart syndrome.
In this report we describe the twelfth case in the literature of absence of the aortic valve cusps, associated with hypoplastic left-sided heart syndrome in a neonate. Clinical and hemodynamic conditions in our patient resemble the classical features of this syndrome except for a greater development of the ascending aorta and the left ventricular cavity, due to aortic insufficiency. A patch was unsuccessfully inserted at the aortic annulus to exclude the left ventricle from the circulation. In addition the Norwood operation was performed.
Atik
E
E
Instituto do Coração do Hospital das Clínicas-FMUSP, Brazil.
Benvenuti
L A
LA
Martins
T C
TC
Barbero-Marcial
M
M
D001021:Aortic Valve / Q000002:abnormalities*; D017809:Fatal Outcome; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000175:diagnosis* / Q000601:surgery; D007231:Infant, Newborn; D008297:Male