title: [Electrocardiography and echocardiography aspects of hypertrophic myocardiopathy in pediatrics].
abstract: Hypertrophic cardiomyopathy (HCM) is a heterogeneous disease, characterized by asymmetric hypertrophy of the left and/or right ventricle with disarray of myocardial fibers. In order to know its clinical and electrocardiographic manifestation in the pediatric age group, we made a retrospective study of 24 cases from 1986 to 1995. There were: 15 girls and 9 boys, with a mean age of 6 years (age range: 1 month to 17 years). Clinical manifestations were dyspnea (71%), syncope (42%) and palpitations (42%). Physical examination disclosed an aortic systolic murmur in all patients, a mitral regurgitation in 42% and physical signs of congestive heart failure in 54% of patients. Chest X rays showed cardiac enlargement in 71% and pulmonary capillary hypertension in 42%. The most frequent ECG abnormalities were: a prolonged time in the intrinsecoid deflection onset on leads corresponding to the affected region, more or less deep and clean Q waves on leads aVF, aVL, V5 and V6, as well as supraventricular and ventricular rhythm disturbances in 11 patients (46%) with and without congestive heart failure. Bidimensional echocardiography confirmed antero-septal hypertrophy in all patients. The mortality rate was 17%. HCM is rare disease in the pediatric age group. Mortality increases when congestive heart failure and arrhythmias are present. Treatment must be individualized in all cases.
authors.affiliation: Servicio de Cardiología Pediátrica, Instituto Nacional de Cardiología Ignacio Chávez (INCICH), México, D.F.
authors.forename: B
authors.initials: B
authors.lastname: Maldonado Tapia
authors.forename: J
authors.initials: J
authors.lastname: Calderón Colmenero
authors.forename: A
authors.initials: A
authors.lastname: de Micheli
authors.forename: M
authors.initials: M
authors.lastname: Rijlaarsdam
authors.forename: J M
authors.initials: JM
authors.lastname: Casanova Garcés
authors.forename: F
authors.initials: F
authors.lastname: Attie
authors.forename: A
authors.initials: A
authors.lastname: Buendia
mesh_terms: D000293:Adolescent; D002312:Cardiomyopathy, Hypertrophic / Q000150:complications / Q000000981:diagnostic imaging* / Q000503:physiopathology*; D002648:Child; D002675:Child, Preschool; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006801:Humans; D017379:Hypertrophy, Left Ventricular / Q000150:complications / Q000000981:diagnostic imaging / Q000503:physiopathology; D007223:Infant; D008297:Male; D012189:Retrospective Studies