title: Caroli syndrome.
abstract: We describe a case of Caroli syndrome (Caroli's disease and congenital hepatic fibrosis) in a 10-year-old boy with bilobar involvement and numerous renal cysts. Liver transplantation offers the only hope for such patients.
authors.affiliation: Department of Surgery, Armed Forces Medical College, Pune, India.
authors.forename: M M
authors.initials: MM
authors.lastname: Harjai
authors.forename: R K
authors.initials: RK
authors.lastname: Bal
mesh_terms: D015746:Abdominal Pain / Q000209:etiology; D001707:Biopsy, Needle; D016767:Caroli Disease / Q000097:blood / Q000150:complications / Q000175:diagnosis* / Q000235:genetics / Q000628:therapy*; D002648:Child; D002760:Cholangiopancreatography, Endoscopic Retrograde; D002761:Cholangitis / Q000209:etiology; D003937:Diagnosis, Differential; D004322:Drainage; D005334:Fever / Q000209:etiology; D006801:Humans; D016031:Liver Transplantation; D008297:Male; D011379:Prognosis; D016717:Sphincterotomy, Endoscopic; D015607:Stents; D014057:Tomography, X-Ray Computed; D014839:Vomiting / Q000209:etiology