title: Absence of the aortic valve associated with hypoplastic left-sided heart syndrome.
abstract: In this report we describe the twelfth case in the literature of absence of the aortic valve cusps, associated with hypoplastic left-sided heart syndrome in a neonate. Clinical and hemodynamic conditions in our patient resemble the classical features of this syndrome except for a greater development of the ascending aorta and the left ventricular cavity, due to aortic insufficiency. A patch was unsuccessfully inserted at the aortic annulus to exclude the left ventricle from the circulation. In addition the Norwood operation was performed.
authors.affiliation: Instituto do Coração do Hospital das Clínicas-FMUSP, Brazil.
authors.forename: E
authors.initials: E
authors.lastname: Atik
authors.forename: L A
authors.initials: LA
authors.lastname: Benvenuti
authors.forename: T C
authors.initials: TC
authors.lastname: Martins
authors.forename: M
authors.initials: M
authors.lastname: Barbero-Marcial
mesh_terms: D001021:Aortic Valve / Q000002:abnormalities*; D017809:Fatal Outcome; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000175:diagnosis* / Q000601:surgery; D007231:Infant, Newborn; D008297:Male