title: [Leiomyosarcoma of the right ventricle].
abstract: A 58-year-old woman has dyspnea and palpitations which reveal a leiomyosarcoma of the right ventricle. The medical imaging shows a lobulated sessile tumor attached to the ventricular septum and the tricuspid valve extending into the pulmonary artery trunk. The resection is performed with a tricuspid valvoplasty. In spite of chemotherapy (epirubicin-cyclophosphamide), relapse is observed with pulmonary metastases 17 months after the surgery. The death becomes on 18 months in congestive heart failure. From this case, the authors make a review of the literature about this exceptional tumour, and talk over the low possibilities of treatment, despite the capacities of the new ways of diagnosis.
authors.affiliation: Service de médecine interne et pathologie cardiovasculaire, Hôpital d'instruction des armées Bégin, 69, avenue de Paris, 94160 Saint-Mandé.
authors.forename: B
authors.initials: B
authors.lastname: Ceccaldi
authors.forename: L M
authors.initials: LM
authors.lastname: Dourthe
authors.forename: J M
authors.initials: JM
authors.lastname: Garcin
authors.forename: B
authors.initials: B
authors.lastname: Vergeau
authors.forename: X
authors.initials: X
authors.lastname: Chanudet
authors.forename: P
authors.initials: P
authors.lastname: Larroque
mesh_terms: D004417:Dyspnea / Q000209:etiology; D017809:Fatal Outcome; D005260:Female; D006338:Heart Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D007890:Leiomyosarcoma / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008875:Middle Aged