Non-confluent pulmonary arteries in a patient with pulmonary atresia and intact ventricular septum: ? A 5th aortic arch with a systemic-to-pulmonary arterial connection.
Major abnormalities of pulmonary circulation are uncommon in the patient with pulmonary atresia and intact ventricular septum. Non-confluent pulmonary arteries have only rarely been described in this setting. In this case report, we describe a patient in whom the pulmonary arteries are non-confluent, with the right pulmonary artery supplied through a right-sided arterial duct, and the left pulmonary artery most likely through a fifth aortic arch, thus providing a systemic-to-pulmonary arterial connection. We discuss the various forms of non-confluent pulmonary arteries in the setting of pulmonary atresia and intact ventricular septum.
Serra
A
A
Department of Pediatric Cardiology, Instituto Estadual de Cardiologia Aloysio de Castro, Rio de Janeiro Brasil.
Chamie
F
F
Freedom
R M
RM
D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology; D001027:Aortography; D006328:Cardiac Catheterization; D017023:Coronary Angiography; D003490:Cyanosis / Q000209:etiology; D004452:Echocardiography; D005183:Failure to Thrive / Q000209:etiology; D017809:Fatal Outcome; D006439:Hemodynamics; D006801:Humans; D007223:Infant; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology; D018633:Pulmonary Atresia / Q000150:complications* / Q000000981:diagnostic imaging / Q000503:physiopathology; D011652:Pulmonary Circulation