[Leiomyosarcoma of the right ventricle].
A 58-year-old woman has dyspnea and palpitations which reveal a leiomyosarcoma of the right ventricle. The medical imaging shows a lobulated sessile tumor attached to the ventricular septum and the tricuspid valve extending into the pulmonary artery trunk. The resection is performed with a tricuspid valvoplasty. In spite of chemotherapy (epirubicin-cyclophosphamide), relapse is observed with pulmonary metastases 17 months after the surgery. The death becomes on 18 months in congestive heart failure. From this case, the authors make a review of the literature about this exceptional tumour, and talk over the low possibilities of treatment, despite the capacities of the new ways of diagnosis.
Ceccaldi
B
B
Service de médecine interne et pathologie cardiovasculaire, Hôpital d'instruction des armées Bégin, 69, avenue de Paris, 94160 Saint-Mandé.
Dourthe
L M
LM
Garcin
J M
JM
Vergeau
B
B
Chanudet
X
X
Larroque
P
P
D004417:Dyspnea / Q000209:etiology; D017809:Fatal Outcome; D005260:Female; D006338:Heart Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D007890:Leiomyosarcoma / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008875:Middle Aged