Bilateral sequential lung transplant for ectodermal dysplasia.
A case of bilateral sequential lung transplantation for anhidrotic ectodermal dysplasia is presented. The patient was a 16-year-old male with end-stage lung disease secondary to chronic severe respiratory infection. Although a relatively rare disease, the common association of fatal pulmonary compromise in those affected with this disorder warrants consideration of lung transplantation as a viable therapeutic option.
Smythe
W R
WR
Department of Anesthesiology, The Children's Hospital of Philadelphia, Pennsylvania 19104, USA.
Bridges
N D
ND
Gaynor
J W
JW
Nicolson
S
S
Clark
B J
BJ
Spray
T L
TL
D000293:Adolescent; D004476:Ectodermal Dysplasia / Q000150:complications*; D017809:Fatal Outcome; D006801:Humans; D016040:Lung Transplantation / Q000379:methods*; D008297:Male; D012131:Respiratory Insufficiency / Q000209:etiology* / Q000601:surgery*