Isolated congenital absence of a single pulmonary valve cusp.
Isolated absence of a single pulmonary valve is extremely unusual. We present a 16-year-old male with the absence of one cusp resulting in significant pulmonary regurgitation, right ventricular enlargement, and dilatation of the main pulmonary artery and its branches. Surgery consisted of creating a valve cusp from the posterior wall of the pulmonary artery at the base of the pulmonary trunk. Follow-up at 3.5 years revealed good results with only mild pulmonary stenosis and regurgitation.
Sayger
P
P
Pediatric Cardiology Division, The Heart Institute for Children, Hope Children's Hospital, Oak Lawn, IL 60453, USA.
Lewis
M
M
Arcilla
R
R
Ilbawi
M
M
D000293:Adolescent; D006348:Cardiac Surgical Procedures / Q000379:methods; D004452:Echocardiography; D006439:Hemodynamics; D006801:Humans; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D011665:Pulmonary Valve Insufficiency / Q000151:congenital / Q000000981:diagnostic imaging / Q000601:surgery*