[Acute bulbar palsy due to myelomeningocele and Chiari II malformation].
We describe a case of a 10-year-old girl with myelomeningocele and type II Chiari malformation. She presented with an acute bulbar palsy requiring mechanical ventilation. Surgical decompression of the brainstem was performed and, because of a phrenic nerve palsy, surgical plication of the right diaphragm was also required. The patient s evolution was favourable. We discuss the various forms of clinical presentation of this pathology as well as its management. The importance of early diagnosis and surgical correction are also stressed as a key factor for favourable evolution.
Ulloa Santamaría
E
E
Servicio de Críticos y Urgencias Pediátricas, Departamento de Pediatría, Hospital Universitario Reina Sofía, Córdoba. ucip@arrakis.ed
Cifuentes Sabio
V
V
Ibarra de la Rosa
I
I
Velasco Jabalquinto
M J
MJ
Frías Pérez
M
M
Montero Schiemann
C
C
Pérez Navero
J L
JL
D000208:Acute Disease; D001139:Arnold-Chiari Malformation / Q000150:complications*; D010244:Bulbar Palsy, Progressive / Q000209:etiology*; D002648:Child; D005260:Female; D006801:Humans; D008591:Meningomyelocele / Q000150:complications*