title: [Anesthetic management of a patient with Freeman-Sheldon syndrome].
abstract: We describe a case of Freeman-Sheldon syndrome that presented some problems for anesthetic management. A 2-yr-old girl required orthopedic surgery for the bilateral lower extremities. Anesthesia was induced via a mask with oxygen (2 l.min-1), nitrous oxide (4 l.min-1) and sevoflurane (approximately 5%). Tracheal intubation by direct laryngoscopy was successfully achieved. Combined caudal epidural block was, however, avoided because spina bifida occulta was suspected. Spina bifida occulta was revealed postoperatively by X-ray. For anesthetic management of a patient with Freeman-Sheldon syndrome, the spine should be evaluated preoperatively when performing epidural/spinal anesthesia.
authors.affiliation: Department of Anesthesiology, Sapporo Medical University School of Medicine.
authors.forename: M
authors.initials: M
authors.lastname: Namiki
authors.forename: T
authors.initials: T
authors.lastname: Kawamata
authors.forename: M
authors.initials: M
authors.lastname: Yamakage
authors.forename: A
authors.initials: A
authors.lastname: Matsuno
authors.forename: A
authors.initials: A
authors.lastname: Namiki
mesh_terms: D000015:Abnormalities, Multiple; D000767:Anesthesia, Epidural; D000769:Anesthesia, Inhalation; D000775:Anesthesia, Spinal; D002675:Child, Preschool; D000075202:Contraindications; D019465:Craniofacial Abnormalities; D005260:Female; D005530:Foot Deformities / Q000601:surgery*; D006226:Hand Deformities; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods; D009135:Muscular Diseases; D019637:Orthopedic Procedures; D016135:Spinal Dysraphism / Q000150:complications; D013577:Syndrome