Ewing's sarcoma/primitive neuroectodermal tumor of the ureter: a case report and review of the literature.
Extraosseous Ewing's sarcoma/primitive neuroectodermal tumor (ES/PNET) is a rare soft tissue tumor of childhood usually found in the extremities. The authors present the case of a 17-year-old girl who presented with right flank pain and hematuria and during operation was found to have a right ureteral mass. The histopathologic, immunohistochemical, ultrastructural, and cytogenetic characteristics of the excised mass were consistent with extraosseous ES/PNET. This is the first known reported case of extraosseous ES/ PNET of the ureter. The pathologic features and clinical management of this case, as well as a review of the literature, are presented.
Charny
C K
CK
Department of Surgery, Memorial Sloan-Kettering Cancer Center, New York, NY 10021, USA.
Glick
R D
RD
Genega
E M
EM
Meyers
P A
PA
Reuter
V E
VE
La Quaglia
M P
MP
D000293:Adolescent; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002880:Chromosomes, Human, Pair 11; D002892:Chromosomes, Human, Pair 22; D003131:Combined Modality Therapy; D005260:Female; D006801:Humans; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000235:genetics / Q000473:pathology / Q000601:surgery; D012512:Sarcoma, Ewing / Q000235:genetics / Q000473:pathology / Q000601:surgery; D014178:Translocation, Genetic; D014516:Ureteral Neoplasms / Q000235:genetics / Q000473:pathology / Q000601:surgery