title: [Caroli's syndrome. Report of a case beginning in childhood with favorable course].
abstract: Caroli's disease is a rare entity that is included in the fibropolycystic abnormalities of the bile ducts. Ultrasonographic patterns consist of evident dilatation of the bile ducts. Although it is thought to be a congenital disease, it usually presents in young adults and few cases have been reported in children. We present the case of a 10-year-old boy with Caroli's syndrome (Caroli's disease, congenital hepatic fibrosis and polycystic renal disease). Evolution was favorable.
authors.affiliation: Servicio de Pediatría , Hospital Severo Ochoa, Leganés, Madrid.
authors.forename: M J
authors.initials: MJ
authors.lastname: Rivero
authors.forename: E
authors.initials: E
authors.lastname: Román
authors.forename: M L
authors.initials: ML
authors.lastname: Cilleruelo
authors.forename: F
authors.initials: F
authors.lastname: Sánchez
authors.forename: J
authors.initials: J
authors.lastname: Barrio
mesh_terms: D017668:Age of Onset; D016767:Caroli Disease / Q000150:complications / Q000628:therapy*; D002648:Child; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D012074:Remission Induction