[Caroli's syndrome. Report of a case beginning in childhood with favorable course].
Caroli's disease is a rare entity that is included in the fibropolycystic abnormalities of the bile ducts. Ultrasonographic patterns consist of evident dilatation of the bile ducts. Although it is thought to be a congenital disease, it usually presents in young adults and few cases have been reported in children. We present the case of a 10-year-old boy with Caroli's syndrome (Caroli's disease, congenital hepatic fibrosis and polycystic renal disease). Evolution was favorable.
Rivero
M J
MJ
Servicio de Pediatría , Hospital Severo Ochoa, Leganés, Madrid.
Román
E
E
Cilleruelo
M L
ML
Sánchez
F
F
Barrio
J
J
D017668:Age of Onset; D016767:Caroli Disease / Q000150:complications / Q000628:therapy*; D002648:Child; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D012074:Remission Induction