Bilateral diffuse choroidal hemangiomas with unilateral facial nevus flammeus in Sturge-Weber syndrome.
OBJECTIVE
To report bilateral choroidal hemangiomas associated with unilateral facial nevus flammeus in Sturge-Weber syndrome.


METHODS
Case report.


RESULTS
A 6-year-old male with a left facial nevus flammeus and a history of a left cerebral angioma had been followed 2 years for increasing esotropia. Examination demonstrated bilateral diffuse choroidal hemangiomas with overlying exudative retinal detachments. After bilateral external beam radiotherapy, the retinal detachments resolved and vision improved.


CONCLUSIONS
Patients with Sturge-Weber syndrome and unilateral facial nevus flammeus may harbor bilateral choroidal hemangiomas. Clinical manifestations of the Sturge-Weber syndrome are characteristically unilateral and ipsilateral to the facial nevus flammeus. Bilateral choroidal hemangiomas associated with bilateral facial nevus flammeus are rare. 1,2 We report bilateral diffuse choroidal hemangiomas associated with unilateral facial nevus flammeus in Sturge-Weber syndrome.
Amirikia
A
A
Department of Ophthalmology, Bascom Palmer Eye Institute, University of Miami School of Medicine, Miami, Florida 33101, USA.
Scott
I U
IU
Murray
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TG
D002648:Child; D002830:Choroid Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000532:radiotherapy; D005145:Face; D006391:Hemangioma / Q000150:complications* / Q000175:diagnosis / Q000532:radiotherapy; D006801:Humans; D008297:Male; D019339:Port-Wine Stain / Q000150:complications* / Q000175:diagnosis / Q000532:radiotherapy; D012163:Retinal Detachment / Q000150:complications / Q000000981:diagnostic imaging / Q000532:radiotherapy; D013341:Sturge-Weber Syndrome / Q000150:complications* / Q000175:diagnosis / Q000532:radiotherapy; D014463:Ultrasonography; D014792:Visual Acuity