title: [Ventricular septal aneurysm in a patient with Marfan syndrome].
abstract: This is the first description of a patient with Marfan syndrome and an aneurysm of the ventricular septum. Apart from a borderline dilatation of the ascending aorta, there were no cardiovascular manifestations of Marfan syndrome. A transesophageal echocardiographic examination showed a large aneurysm of the ventricular septum. To prevent the imminent rupture and the acute occurrence of a significant left-to-right-shunt on the ventricular level, as well as increasing irritation of tricuspid valve, an elective operation was performed. Besides the routine cardiological diagnostics, the search for intracardial defects is also necessary in patients with Marfan syndrome.
authors.affiliation: Klinik für Herz-, Thorax- und Gefässchirurgie Deutsches Herzzentrum Berlin. mbauer@dhzb.de
authors.forename: M
authors.initials: M
authors.lastname: Bauer
authors.forename: H
authors.initials: H
authors.lastname: Siniawski
authors.forename: U
authors.initials: U
authors.lastname: Bauer
authors.forename: H
authors.initials: H
authors.lastname: Gülmez
authors.forename: F
authors.initials: F
authors.lastname: Knollmann
authors.forename: P E
authors.initials: PE
authors.lastname: Lange
authors.forename: R
authors.initials: R
authors.lastname: Hetzer
mesh_terms: D000328:Adult; D000792:Angiography; D017548:Echocardiography, Transesophageal; D005260:Female; D006322:Heart Aneurysm / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000150:complications* / Q000175:diagnosis; D006346:Heart Septum; D006352:Heart Ventricles; D006801:Humans; D008382:Marfan Syndrome / Q000150:complications*; D014057:Tomography, X-Ray Computed