Idiopathic ocular neuromyotonia: a neurovascular compression syndrome?
Ocular neuromyotonia in the muscles innervated by the right oculomotor nerve was diagnosed in a patient without a history of radiation therapy. Electromyography of the levator palpebrae showed continuous motor unit activity. Brain MRI disclosed a close contact between the right third cranial nerve and a basilar artery dolichoectasia. The patient partly benefited from carbamazepine therapy. This unique finding suggests that neurovascular compression syndrome could be an hitherto unrecognised cause of ocular neuromyotonia.
Tilikete
C
C
Neuro-ophthalmology Unit, Hôpital Neurologique et Neurochirurgical P Wertheimer, 59 Bd Pinel, 69003 Lyon, France. caroline.tilikete@free.fr
Vial
C
C
Niederlaender
M
M
Bonnier
P L
PL
Vighetto
A
A
D000368:Aged; D006801:Humans; D020386:Isaacs Syndrome / Q000473:pathology* / Q000503:physiopathology; D008279:Magnetic Resonance Imaging; D008297:Male; D009408:Nerve Compression Syndromes / Q000473:pathology* / Q000503:physiopathology; D009801:Oculomotor Muscles / Q000473:pathology* / Q000503:physiopathology; D009802:Oculomotor Nerve / Q000473:pathology* / Q000503:physiopathology