title: [Respiratory failure during the course of congenital myopathy effectively treated with nocturnal noninvasive nasal positive pressure ventilation].
abstract: Respiratory muscle weakness in myopathy may result in respiratory failure. 41 year old male with congenital myopathy was successfully treated with nocturnal noninvasive nasal positive pressure ventilation. NPPV resulted in improvement of arterial blood gases and allowed to close tracheostomy. Patient was able to return to full time employment.
authors.affiliation: Kliniki Chorób Płuc Instytutu Gruźlicy i Chorób Płuc w Warszawie.
authors.forename: P
authors.initials: P
authors.lastname: Bieleń
authors.forename: P
authors.initials: P
authors.lastname: Sliwiński
authors.forename: D
authors.initials: D
authors.lastname: Kamiński
authors.forename: J
authors.initials: J
authors.lastname: Zieliński
mesh_terms: D000328:Adult; D001784:Blood Gas Analysis; D006801:Humans; D008297:Male; D018908:Muscle Weakness / Q000150:complications* / Q000151:congenital*; D011175:Positive-Pressure Respiration; D012131:Respiratory Insufficiency / Q000209:etiology* / Q000628:therapy*; D014139:Tracheostomy