title: Pulmonary involvement in tuberous sclerosis complex: presentation of a case.
abstract: A clinical case of a pulmonary involvement in Tuberous Sclerosis Complex is reported. This rare involvement (1%) is characterized by either interstitial disease or bullae; therefore, pneumothorax is likely to happen in lung parenchyma. Furthermore this complication induces a progressive serious respiratory failure until the death of the patient.
authors.affiliation: Department of Cardiovascular and Respiratory Sciences, University La Sapienza, Rome, Italy.
authors.forename: M
authors.initials: M
authors.lastname: Vitto
authors.forename: F
authors.initials: F
authors.lastname: Fabiani
authors.forename: P
authors.initials: P
authors.lastname: Capuzi
authors.forename: A L
authors.initials: AL
authors.lastname: D'Angeli
authors.forename: A B
authors.initials: AB
authors.lastname: Mariotti
authors.forename: E L
authors.initials: EL
authors.lastname: Bianchi
authors.forename: C
authors.initials: C
authors.lastname: Fiorucci
authors.forename: G
authors.initials: G
authors.lastname: Schmid
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008171:Lung Diseases / Q000209:etiology* / Q000473:pathology; D011030:Pneumothorax / Q000209:etiology; D014402:Tuberous Sclerosis / Q000150:complications* / Q000473:pathology