Outcome in infants with pulmonary atresia, intact ventricular septum, and right ventricle-dependent coronary circulation.
Management of all patients with pulmonary atresia, intact ventricular septum, and right ventricle-dependent coronary circulation (n = 12) with staged surgery directed toward a Fontan palliation resulted in an 83% 5-year actuarial survival. Both deaths in the study were presumably related to coronary ischemia and occurred in the first 4 months of life.
Powell
A J
AJ
Department of Cardiology, Children's Hospital, Harvard Medical School, Boston, Massachusetts 02115, USA. powell@cardio.tch.harvard.edu
Mayer
J E
JE
Lang
P
P
Lock
J E
JE
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D000792:Angiography; D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures / Q000379:methods; D002648:Child; D002675:Child, Preschool; D003330:Coronary Vessel Anomalies / Q000175:diagnosis / Q000601:surgery*; D004452:Echocardiography; D006345:Heart Septal Defects, Ventricular / Q000175:diagnosis / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D018633:Pulmonary Atresia / Q000175:diagnosis / Q000601:surgery*; D012189:Retrospective Studies; D016896:Treatment Outcome; D016157:Vascular Fistula / Q000175:diagnosis / Q000601:surgery*