Survival of an aortic trauma patient with Ehlers-Danlos syndrome type IV: a case report.
Ehlers-Danlos syndrome type IV is the most lethal variant of that illness and is associated with fatal large vessel arterial hemorrhages. The literature reports only two survivors of elective aortic surgery and two survivors of spontaneous aortic hemorrhage. This article presents a 14-year-old boy who had aortic and vena cava blunt trauma and survived.
Levine
M P
MP
Danville Vascular Surgery, Danville, VA 24541, USA.
D000293:Adolescent; D001012:Aorta, Abdominal / Q000293:injuries* / Q000601:surgery; D001265:Athletic Injuries / Q000601:surgery*; D001490:Basketball / Q000293:injuries*; D004535:Ehlers-Danlos Syndrome / Q000145:classification / Q000150:complications* / Q000235:genetics; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007083:Iliac Artery / Q000293:injuries* / Q000601:surgery; D008297:Male; D009104:Multiple Trauma / Q000601:surgery*; D013997:Time Factors; D014682:Vena Cava, Inferior / Q000293:injuries* / Q000601:surgery