Congenital nasal pyriform aperture stenosis.
Congenital nasal pyriform aperture stenosis is a rare cause of pediatric nasal airway obstruction. As infants are obligate nasal breathers, nasal obstruction and even severe nasal congestion can lead to apnea and respiratory distress. Congenital nasal pyriform aperture stenosis was first described by Brown et al in 1989. The narrowing of the nasal pyriform aperture is thought to be due to bony overgrowth of the nasal process of the maxilla during fetal development. Because of the association this anomaly has with other midline defects, such as holoprosencephaly, it is important to recognize it and pursue a thorough workup. We present a case of a patient with pyriform aperture stenosis and solitary central megaincisor. This patient initially presented to our clinic with a history of nasal airway obstruction, poor feeding, and failure to thrive.
Lacey
J P
JP
Department of Otolaryngology-Head and Neck Surgery, Tulane University School of Medicine, New Orleans, Louisiana, USA.
Brown
K
K
D003937:Diagnosis, Differential; D004200:Diseases in Twins / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D015508:Nasal Obstruction / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery; D009666:Nose / Q000002:abnormalities; D013517:Otorhinolaryngologic Surgical Procedures / Q000379:methods; D014057:Tomography, X-Ray Computed