Subclavian steal syndrome in anomalous connection of the left subclavian artery to the pulmonary artery in d-transposition of the great arteries.
Several reports have documented the occurrence of an isolated left subclavian artery in association with both tetralogy of Fallot and double-outlet right ventricle. In certain cases a congenital subclavian or pulmonary artery steal syndrome exists in which the left subclavian artery is connected to the main pulmonary artery via a ductus arteriosus. We describe a subclavian steal syndrome secondary to anomalous origin of the left subclavian artery from the pulmonary artery in d-transposition of the great arteries in a patient with Spondylocostal dysostosis (SCD). Cardiac anomalies are rare in SCD and this constellation of findings have not previously been described.
McMahon
C J
CJ
Division of Pediatric Cardiology, Texas Children's Hospital and Baylor College of Medicine, Houston, TX 77030, USA.
Thompson
K S
KS
Kearney
D L
DL
Nihill
M R
MR
D003330:Coronary Vessel Anomalies / Q000473:pathology*; D004374:Ductus Arteriosus, Patent / Q000150:complications; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D013348:Subclavian Artery / Q000002:abnormalities* / Q000601:surgery; D013349:Subclavian Steal Syndrome / Q000150:complications / Q000151:congenital* / Q000175:diagnosis; D014188:Transposition of Great Vessels / Q000473:pathology*