[Congenital bladder diverticulum and Ehlers-Danlos syndrome: an unusual association].
The existence of a vesical diverticulum in the context of a congenital connective tissue disorder such as Ehlers-Danlos syndrome led us to consider the possibility of a relationship. Four types of diverticula can be found in the literature: congenital, acquired, iatrogenic and syndrome-associated. Within the later, Ehlers-Danlos syndromes type IV and IX, even type V, are associated to the existence of vesical diverticula. The potential spontaneous rupture of the diverticulum is a typical feature, as well as post-surgery relapse. The attitude towards such diverticula should be one of watchful waiting, and simple, plasty-free diverticulectomy on the bladder's neck is indicated when performing a surgical procedure.
Bachiller Burgos
J
J
Servicio de Urología, H.C.U. Puerto Real, Cádiz.
Varo Solís
C
C
Báez
J M
JM
Estudillo
F
F
Juárez Soto
A
A
Soto Delgado
M
M
Beltrán Aguilar
V
V
González Moreno
D
D
Sánchez Bernal
C
C
Rodríguez-Rubio
F
F
D000328:Adult; D004240:Diverticulum / Q000150:complications* / Q000151:congenital*; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D006801:Humans; D001745:Urinary Bladder Diseases / Q000150:complications* / Q000151:congenital*