[Familial Waldmann's disease].
We report the observation of a mother and her daughter who presented edema, hypoprotidemia and lymphopenia due to protein-losing enteropathy. Radiological, endoscopic and histological investigations revealed the diagnosis of primary intestinal lymphangiectasis or Waldmann's disease. Dietary treatment with middle chained triglycerides was effective. Familial cases are rarely described.
Le Bougeant
P
P
Fédération de Médecine Interne, Maladies Infectieuses et Pathologies Tropicales, Hôpital Saint-André, 1, rue Jean Burguet, 33075 Bordeaux Cedex.
Delbrel
X
X
Grenouillet
M
M
Leou
S
S
Djossou
F
F
Beylot
J
J
Lebras
M
M
Longy-Boursier
M
M
D000328:Adult; D004041:Dietary Fats / Q000008:administration & dosage; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008201:Lymphangiectasis, Intestinal / Q000175:diagnosis / Q000178:diet therapy / Q000235:genetics*; D008875:Middle Aged; D013577:Syndrome; D013997:Time Factors; D014280:Triglycerides / Q000008:administration & dosage
D004041:Dietary Fats; D014280:Triglycerides