Cutaneous oozing of lymphatic fluid after interventional cardiac catheterization in a patient with Noonan syndrome.
A 15-year-old girl with Noonan syndrome, intestinal lymphangiectasia and severe valvar pulmonary stenosis had an abnormal lymphangioscintigram that showed intense activity in the inguinal regions bilaterally. Cutaneous oozing of lymphatic fluid from the groin wound complicated percutaneous balloon pulmonary valvoplasty. This previously unreported complication highlights the risk of damage to abnormal lymphatic channels in patients with Noonan syndrome who undergo interventional catheterization.
Tsang
H Y
HY
Division of Pediatric Cardiology, Department of Pediatrics, Grantham Hospital, University of Hong Kong, Hong Kong.
Cheung
Y F
YF
Leung
M P
MP
Chau
K T
KT
D000293:Adolescent; D006328:Cardiac Catheterization / Q000009:adverse effects*; D005260:Female; D006801:Humans; D008196:Lymph; D008209:Lymphedema / Q000209:etiology*; D009634:Noonan Syndrome / Q000150:complications*