Hypothalamic hamartoma associated with an arachnoid cyst.
A hypothalamic hamartoma associated with an arachnoid cyst in an 8-year-old boy is reported herein. He presented with precocious puberty, and neuroimaging studies demonstrated a solid mass in the prepontine cistern and a huge arachnoid cyst in the left cranial fossa. The mass appeared isointense to the surrounding cerebral cortex on T1-weighted magnetic resonance images, hyperintense on T2-weighted images, and was not enhanced after administration of Gd-DTPA. The patient underwent a left frontotemporal craniotomy and a cyst-peritoneal shunt was inserted. Histological features of the cyst wall and the mass were characteristic of an arachnoid cyst and hamartoma, respectively. While a hypothalamic hamartoma associated with an arachnoid cyst is rare, such a case may help clarify the geneses of both anomalous lesions.
Nishio
S
S
Department of Neurosurgery, Graduate School of Medical Sciences, Kyushu University, Japan.shunji@ns.med.kyushu-u.ac.jp
Morioka
T
T
Hamada
Y
Y
Kuromaru
R
R
Fukui
M
M
D001099:Arachnoid / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D016080:Arachnoid Cysts / Q000150:complications* / Q000473:pathology / Q000601:surgery; D002557:Cerebrospinal Fluid Shunts / Q000379:methods; D002648:Child; D006222:Hamartoma / Q000150:complications* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007027:Hypothalamic Diseases / Q000150:complications* / Q000473:pathology / Q000601:surgery; D007031:Hypothalamus / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D008279:Magnetic Resonance Imaging; D008297:Male; D011629:Puberty, Precocious / Q000209:etiology / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome