Acute care pediatric electromyography.
The recognition of uncommon pediatric motor unit disorders or unusual clinical presentations of common illnesses, such as Guillain-Barré syndrome (GBS), have increased the need for electromyography (EMG) in childhood critical care units. There are two different clinical sets, one appropriate to newborns and infants and the other to older children. Some illnesses that present as an acute floppy infant are not found in the differential diagnosis of motor unit disorders in the older child or adult. These include spinal muscular atrophy, postvaccine poliomyelitis, intrauterine GBS, infantile botulism, and severe myopathies, such as myotonia dystrophy, and some glycogen storage diseases. An appreciation of the neurophysiological maturational norms is essential to an effective pediatric EMG consultation for children ages 0-3 years. Additionally, the neuromuscular complications of extended intubation and sepsis in children are gaining broader recognition. An increased dialogue between clinical neurophysiologists and pediatric neurologists and intensivists in both neonatal and pediatric intensive care units is essential.
Jones
H R
HR
Department of Neurology, Lahey Clinic Medical Center, Burlington, Massachusetts 01805, USA. Royden.Jones@Lahey.org
Darras
B T
BT
D000208:Acute Disease; D002528:Cerebellar Neoplasms / Q000175:diagnosis; D002648:Child; D002675:Child, Preschool; D004576:Electromyography; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D008527:Medulloblastoma / Q000175:diagnosis; D009223:Myotonic Dystrophy / Q000175:diagnosis; D009468:Neuromuscular Diseases / Q000175:diagnosis*; D020511:Neuromuscular Junction Diseases / Q000175:diagnosis; D011051:Poliomyelitis / Q000175:diagnosis; D011115:Polyneuropathies / Q000175:diagnosis