title: Chordoma periphericum: a case report.
abstract: The authors describe a tumor that had the histologic and ultrastructural features and immunohistochemical profile of an axial chordoma, but arose in the distal ulna. A skeletal survey failed to show any other site of involvement. The tumor was resected, and the patient remains free of disease 2 1/2 years later. Rare tumors with the histologic features of chordoma have been reported in appendicular locations. Chordoma periphericum, a tumor that has the potential to metastasize, needs to be distinguished from parachordoma because no classic parachordoma has been reported to disseminate.
authors.affiliation: James Homer Wright Pathology Laboratories, Massachusetts General Hospital, Harvard Medical School, Boston 02114, USA.
authors.forename: G P
authors.initials: GP
authors.lastname: Nielsen
authors.forename: D C
authors.initials: DC
authors.lastname: Mangham
authors.forename: R J
authors.initials: RJ
authors.lastname: Grimer
authors.forename: A E
authors.initials: AE
authors.lastname: Rosenberg
mesh_terms: D000328:Adult; D014408:Biomarkers, Tumor / Q000032:analysis; D001859:Bone Neoplasms / Q000737:chemistry / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D002817:Chordoma / Q000737:chemistry / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D018572:Disease-Free Survival; D006801:Humans; D007124:Immunoenzyme Techniques; D007365:Intercellular Junctions / Q000648:ultrastructure; D007633:Keratins / Q000032:analysis; D008279:Magnetic Resonance Imaging; D008297:Male; D009363:Neoplasm Proteins / Q000032:analysis; D015388:Organelles / Q000648:ultrastructure; D011859:Radiography; D009418:S100 Proteins / Q000032:analysis; D014457:Ulna / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery
chemical_list: D014408:Biomarkers, Tumor; D009363:Neoplasm Proteins; D009418:S100 Proteins; D007633:Keratins